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RGC-ADOA/ref/mitocarta3.0/Mouse_MitoCarta3.0_genes.csv
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1MouseGeneIDSymbolHumanOrthologGeneIDDescriptionEvidenceSubMitoLocalizationMitoPathways
266445Cyc11537.0cytochrome c-1literature, APEX_IMS, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits | Metabolism > Metals and cofactors > Heme-containing proteins | Metabolism > Electron carriers > Cytochromes | OXPHOS > OXPHOS subunits
318597Pdha15160.0pyruvate dehydrogenase E1 alpha 1literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolism
466043Atp5d513.0ATP synthase, H+ transporting, mitochondrial F1 complex, delta subunitliterature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
574316Isca2122961.0iron-sulfur cluster assembly 2APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Metals and cofactors > Fe-S-containing proteins
668263Pdhb5162.0pyruvate dehydrogenase (lipoamide) betaliterature, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolism
722273Uqcrc17384.0ubiquinol-cytochrome c reductase core protein 1literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage | OXPHOS > Complex III > CIII subunits | OXPHOS > OXPHOS subunits
867914Coq957017.0coenzyme Q9APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolism
956282Mrpl126182.0mitochondrial ribosomal protein L12literature, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > Transcription | Mitochondrial central dogma > Translation > Mitochondrial ribosome
10232536Mrps3560488.0mitochondrial ribosomal protein S35literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
1112858Cox5a9377.0cytochrome c oxidase subunit 5Aliterature, APEX_IMS, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
1266694Uqcrfs17386.0ubiquinol-cytochrome c reductase, Rieske iron-sulfur polypeptide 1literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits | Metabolism > Metals and cofactors > Fe-S-containing proteins | OXPHOS > OXPHOS subunits
1312850Coq710229.0demethyl-Q 7literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression++, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolism
1466945Sdha6389.0succinate dehydrogenase complex, subunit A, flavoprotein (Fp)literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex II > CII subunits | Metabolism > Carbohydrate metabolism > TCA cycle | OXPHOS > OXPHOS subunits
1567680Sdhb6390.0succinate dehydrogenase complex, subunit B, iron sulfur (Ip)literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex II > CII subunits | Metabolism > Carbohydrate metabolism > TCA cycle | Metabolism > Metals and cofactors > Fe-S-containing proteins | OXPHOS > OXPHOS subunits
1611946Atp5a1498.0ATP synthase, H+ transporting, mitochondrial F1 complex, alpha subunit 1literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
1768002Sdhaf4135154.0succinate dehydrogenase complex assembly factor 4targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MSMatrixOXPHOS > Complex II > CII assembly factors | OXPHOS > OXPHOS assembly factors
1873078Pmpcb9512.0peptidase (mitochondrial processing) betaliterature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage | Protein import, sorting and homeostasis > Protein homeostasis > Proteases
1966925Sdhd6392.0succinate dehydrogenase complex, subunit D, integral membrane proteinliterature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+MIMOXPHOS > Complex II > CII subunits | Metabolism > Carbohydrate metabolism > TCA cycle | Metabolism > Metals and cofactors > Heme-containing proteins | OXPHOS > OXPHOS subunits
2067003Uqcrc27385.0ubiquinol cytochrome c reductase core protein 2literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage | OXPHOS > Complex III > CIII subunits | OXPHOS > OXPHOS subunits
2152064Coq584274.0coenzyme Q5 methyltransferaseAPEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolism
2218293Ogdh4967.0oxoglutarate (alpha-ketoglutarate) dehydrogenase (lipoamide)literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle
2322272Uqcrq27089.0ubiquinol-cytochrome c reductase, complex III subunit VIIliterature, APEX_IMS, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits | OXPHOS > OXPHOS subunits
2417448Mdh24191.0malate dehydrogenase 2, NAD (mitochondrial)literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Gluconeogenesis | Metabolism > Carbohydrate metabolism > Malate-aspartate shuttle | Metabolism > Carbohydrate metabolism > TCA cycle
2513171Dbt1629.0dihydrolipoamide branched chain transacylase E2literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > Branched-chain amino acid metabolism | Metabolism > Amino acid metabolism > Branched-chain amino acid dehydrogenase complex
26235339Dlat1737.0dihydrolipoamide S-acetyltransferase (E2 component of pyruvate dehydrogenase complex)literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolism
2772416Lrpprc10128.0leucine-rich PPR-motif containingliterature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay | Mitochondrial central dogma > Translation
2868499Mrpl53116540.0mitochondrial ribosomal protein L53literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
2978920Dlst1743.0dihydrolipoamide S-succinyltransferase (E2 component of 2-oxo-glutarate complex)literature, APEX_IMS, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+MatrixMetabolism > Carbohydrate metabolism > TCA cycle | Metabolism > Amino acid metabolism > Lysine metabolism
3027402Pdhx8050.0pyruvate dehydrogenase complex, component Xliterature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS+MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolism
3128030Gfm185476.0G elongation factor, mitochondrial 1literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factors
3217713Grpel180273.0GrpE-like 1, mitochondrialliterature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MatrixProtein import, sorting and homeostasis > Protein import and sorting > Import motor | Metabolism > Metals and cofactors > Fe-S cluster biosynthesis
3370456Mpc225874.0mitochondrial pyruvate carrier 2literature, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis | Metabolism > Carbohydrate metabolism > Pyruvate metabolism | Metabolism > Carbohydrate metabolism > TCA-associated | Small molecule transport
3466152Uqcr1029796.0ubiquinol-cytochrome c reductase, complex III subunit Xliterature, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits | OXPHOS > OXPHOS subunits
35230027Coq351805.0coenzyme Q3 methyltransferaseAPEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression+, MS/MS+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolism
3667126Atp5e514.0ATP synthase, H+ transporting, mitochondrial F1 complex, epsilon subunitliterature, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
3718674Slc25a35250.0solute carrier family 25 (mitochondrial carrier, phosphate carrier), member 3literature, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMMetabolism > Metals and cofactors > Copper metabolism | Signaling > Calcium homeostasis > Calcium cycle | Small molecule transport > SLC25A family
3894065Mrpl3464981.0mitochondrial ribosomal protein L34literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
3966407Mrps1564960.0mitochondrial ribosomal protein S15literature, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
4066052Sdhc6391.0succinate dehydrogenase complex, subunit C, integral membrane proteinliterature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS+MIMOXPHOS > Complex II > CII subunits | Metabolism > Carbohydrate metabolism > TCA cycle | Metabolism > Metals and cofactors > Heme-containing proteins | OXPHOS > OXPHOS subunits
4111947Atp5b506.0ATP synthase, H+ transporting mitochondrial F1 complex, beta subunitliterature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
4264656Mrps2351649.0mitochondrial ribosomal protein S23literature, APEX_matrix, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
43110842Etfa2108.0electron transferring flavoprotein, alpha polypeptideliterature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Amino acid metabolism > Branched-chain amino acid metabolism | Metabolism > Amino acid metabolism > Lysine metabolism | Metabolism > Amino acid metabolism > Glycine metabolism | Metabolism > Vitamin metabolism > Choline and betaine metabolism | Metabolism > Electron carriers > Q-linked reactions, other
4414194Fh12271.0fumarate hydratase 1literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle
45218506Mrps2723107.0mitochondrial ribosomal protein S27literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, induction, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
4669046Isca181689.0iron-sulfur cluster assembly 1APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Metals and cofactors > Fe-S-containing proteins
4767834Idh3a3419.0isocitrate dehydrogenase 3 (NAD+) alphaAPEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle
48227197Ndufs14719.0NADH:ubiquinone oxidoreductase core subunit S1literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | Metabolism > Metals and cofactors > Fe-S-containing proteins | OXPHOS > OXPHOS subunits
4911992Auh549.0AU RNA binding protein/enoyl-coenzyme A hydrataseliterature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Itaconate metabolism | Metabolism > Amino acid metabolism > Branched-chain amino acid metabolism
5069597Afg3l210939.0AFG3-like AAA ATPase 2literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteases
5166865Pmpca23203.0peptidase (mitochondrial processing) alphaliterature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage | Protein import, sorting and homeostasis > Protein homeostasis > Proteases
5269802Cox111353.0cytochrome c oxidase assembly protein 11, copper chaperoneliterature, APEX_IMS, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors | Metabolism > Metals and cofactors > Copper metabolism | OXPHOS > OXPHOS assembly factors
5320916Sucla28803.0succinate-Coenzyme A ligase, ADP-forming, beta subunitliterature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle | Metabolism > Carbohydrate metabolism > Itaconate metabolism | Metabolism > Nucleotide metabolism > Nucleotide synthesis and processing
54102436Lars223395.0leucyl-tRNA synthetase, mitochondrialliterature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
5528080Atp5o539.0ATP synthase, H+ transporting, mitochondrial F1 complex, O subunitliterature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, MS/MS++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
5667308Mrpl4626589.0mitochondrial ribosomal protein L46literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
57226139Cox151355.0cytochrome c oxidase assembly protein 15literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression++, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors | Metabolism > Metals and cofactors > Heme synthesis and processing | OXPHOS > OXPHOS assembly factors
5867044Higd2a192286.0HIG1 domain family, member 2AAPEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > OXPHOS assembly factors | OXPHOS > Respirasome assembly
5966576Uqcrh7388.0ubiquinol-cytochrome c reductase hinge proteinliterature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII subunits | OXPHOS > OXPHOS subunits
6066841Etfdh2110.0electron transferring flavoprotein, dehydrogenaseliterature, APEX_matrix, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Amino acid metabolism > Branched-chain amino acid metabolism | Metabolism > Amino acid metabolism > Lysine metabolism | Metabolism > Amino acid metabolism > Glycine metabolism | Metabolism > Metals and cofactors > Fe-S-containing proteins | Metabolism > Vitamin metabolism > Choline and betaine metabolism | Metabolism > Electron carriers > Q-linked reactions, other
6130059Timm1026519.0translocase of inner mitochondrial membrane 10literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones | Protein import, sorting and homeostasis > Protein import and sorting
6293747Echs11892.0enoyl Coenzyme A hydratase, short chain, 1, mitochondrialliterature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Amino acid metabolism > Branched-chain amino acid metabolism | Metabolism > Amino acid metabolism > Lysine metabolism
6397212Hadha3030.0hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit alphaliterature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Lipid metabolism > Cardiolipin synthesis | Metabolism > Amino acid metabolism > Branched-chain amino acid metabolism
6412039Bckdha593.0branched chain ketoacid dehydrogenase E1, alpha polypeptideliterature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS++MIMMetabolism > Amino acid metabolism > Branched-chain amino acid metabolism | Metabolism > Amino acid metabolism > Branched-chain amino acid dehydrogenase complex
6556451Suclg18802.0succinate-CoA ligase, GDP-forming, alpha subunittargetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle | Metabolism > Carbohydrate metabolism > Itaconate metabolism | Metabolism > Nucleotide metabolism > Nucleotide synthesis and processing
6612974Cs1431.0citrate synthaseliterature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle
6712861Cox6a11337.0cytochrome c oxidase subunit 6A1literature, targetP signal+, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
6811409Acads35.0acyl-Coenzyme A dehydrogenase, short chainliterature, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation
6972900Ndufv24729.0NADH:ubiquinone oxidoreductase core subunit V2literature, APEX_matrix, targetP signal+, Rickettsial homolog, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | Metabolism > Metals and cofactors > Fe-S-containing proteins | OXPHOS > OXPHOS subunits
70381314Iars255699.0isoleucine-tRNA synthetase 2, mitochondrialAPEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
71217707Coq651004.0coenzyme Q6 monooxygenaseliterature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolism
7211958Atp5k521.0ATP synthase, H+ transporting, mitochondrial F1F0 complex, subunit Eliterature, APEX_IMS, yeast mito homolog++, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits | Mitochondrial dynamics and surveillance > Cristae formation
73170718Idh3b3420.0isocitrate dehydrogenase 3 (NAD+) betaliterature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle
7467130Ndufa64700.0NADH:ubiquinone oxidoreductase subunit A6literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
7556384Letm13954.0leucine zipper-EF-hand containing transmembrane protein 1literature, APEX_IMS, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain+, coexpression++, MS/MS++MIMSignaling > Calcium homeostasis > Calcium cycle
76246782Atpaf291647.0ATP synthase mitochondrial F1 complex assembly factor 2literature, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSMatrixOXPHOS > Complex V > CV assembly factors | OXPHOS > OXPHOS assembly factors
77170728Rtn4ip184816.0reticulon 4 interacting protein 1literature, APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain, induction, coexpression++, MS/MS++Matrix0
7894067Mrpl4384545.0mitochondrial ribosomal protein L43literature, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
7968758Abhd1183451.0abhydrolase domain containing 11literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA-associated
8066525Timm5092609.0translocase of inner mitochondrial membrane 50literature, APEX_IMS, targetP signal+, yeast mito homolog++, mito protein domain, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathway
8168611Mrpl2810573.0mitochondrial ribosomal protein L28literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
8266072Sdhaf254949.0succinate dehydrogenase complex assembly factor 2GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMatrixOXPHOS > Complex II > CII assembly factors | OXPHOS > OXPHOS assembly factors
8367264Ndufb84714.0NADH:ubiquinone oxidoreductase subunit B8literature, APEX_IMS, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
8413382Dld1738.0dihydrolipoamide dehydrogenaseliterature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolism | Metabolism > Carbohydrate metabolism > TCA cycle | Metabolism > Amino acid metabolism > Branched-chain amino acid metabolism | Metabolism > Amino acid metabolism > Branched-chain amino acid dehydrogenase complex | Metabolism > Amino acid metabolism > Lysine metabolism | Metabolism > Amino acid metabolism > Glycine metabolism | Metabolism > Amino acid metabolism > Glycine cleavage system
85226646Ndufs24720.0NADH:ubiquinone oxidoreductase core subunit S2literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | Metabolism > Metals and cofactors > Fe-S-containing proteins | OXPHOS > OXPHOS subunits
8617995Ndufv14723.0NADH:ubiquinone oxidoreductase core subunit V1literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | Metabolism > Metals and cofactors > Fe-S-containing proteins | OXPHOS > OXPHOS subunits
8774143Opa14976.0OPA1, mitochondrial dynamin like GTPaseliterature, APEX_IMS, yeast mito homolog++, mito protein domain, induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Fusion | Mitochondrial dynamics and surveillance > Cristae formation
8876614Immt10989.0inner membrane protein, mitochondrialliterature, targetP signal, yeast mito homolog, mito protein domain+, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complex
8968117Apool139322.0apolipoprotein O-likeliterature, yeast mito homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complex
9074142Lonp19361.0lon peptidase 1, mitochondrialliterature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteases
9168614Letmd125875.0LETM1 domain containing 1GFP, targetP signal, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MembraneSmall molecule transport
9227273Pdk45166.0pyruvate dehydrogenase kinase, isoenzyme 4literature, targetP signal, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Pyruvate metabolism
9376784Mtif24528.0mitochondrial translational initiation factor 2literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > Translation factors
94225887Ndufs84728.0NADH:ubiquinone oxidoreductase core subunit S8literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | Metabolism > Metals and cofactors > Fe-S-containing proteins | OXPHOS > OXPHOS subunits
9575406Ndufs7374291.0NADH:ubiquinone oxidoreductase core subunit S7literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | Metabolism > Metals and cofactors > Fe-S-containing proteins | OXPHOS > OXPHOS subunits
9667871Mrrf92399.0mitochondrial ribosome recycling factorliterature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factors
9727398Mrpl251069.0mitochondrial ribosomal protein L2literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
98320806Gfm284340.0G elongation factor, mitochondrial 2literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factors
9930056Timm926520.0translocase of inner mitochondrial membrane 9literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression+, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones | Protein import, sorting and homeostasis > Protein import and sorting
10069617Pitrm110531.0pitrilysin metallepetidase 1literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteases
10111364Acadm34.0acyl-Coenzyme A dehydrogenase, medium chainliterature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation
102338359Supv3l16832.0suppressor of var1, 3-like 1 (S. cerevisiae)literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression+, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
10394061Mrpl165008.0mitochondrial ribosomal protein L1literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
10411429Aco250.0aconitase 2, mitochondrialliterature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle | Metabolism > Metals and cofactors > Fe-S-containing proteins
105210582Coq10a93058.0coenzyme Q10AtargetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolism
10668653Samm5025813.0SAMM50 sorting and assembly machinery componentliterature, APEX_IMS, APEX_matrix, yeast mito homolog++, Rickettsial homolog, induction, coexpression++, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > SAM | Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
107118451Mrps251116.0mitochondrial ribosomal protein S2literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
10820930Surf16834.0surfeit gene 1literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
10969163Mrpl4465080.0mitochondrial ribosomal protein L44literature, APEX_matrix, targetP signal+, yeast mito homolog++, induction, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
11018673Phb5245.0prohibitinliterature, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones
111231279Guf160558.0GUF1 homolog, GTPaseAPEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation
112216151Polrmt5442.0polymerase (RNA) mitochondrial (DNA directed)literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, coexpression++, MS/MSMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication | Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid | Mitochondrial central dogma > mtRNA metabolism > Transcription
11366092Ghitm27069.0growth hormone inducible transmembrane proteinliterature, APEX_IMS, targetP signal+, Rickettsial homolog, mito protein domain+, induction, coexpression++, MS/MSMIMMitochondrial dynamics and surveillance > Apoptosis
11430055Timm1326517.0translocase of inner mitochondrial membrane 13literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones | Protein import, sorting and homeostasis > Protein import and sorting
11512896Cpt21376.0carnitine palmitoyltransferase 2literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression+, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Metals and cofactors > Carnitine synthesis and transport | Metabolism > Metals and cofactors > Carnitine shuttle
116107732Mrpl10124995.0mitochondrial ribosomal protein L10literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
11768291Mto125821.0mitochondrial tRNA translation optimization 1literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression++MatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications | Metabolism > Vitamin metabolism > Folate and 1-C metabolism
11811757Prdx310935.0peroxiredoxin 3literature, APEX_IMS, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism
11912866Cox7a21347.0cytochrome c oxidase subunit 7A2literature, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
12011957Atp5j522.0ATP synthase, H+ transporting, mitochondrial F0 complex, subunit Fliterature, APEX_IMS, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
121216792Iba57200205.0IBA57 homolog, iron-sulfur cluster assemblyAPEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis
12218100Mrpl4064976.0mitochondrial ribosomal protein L40literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
123227095Hibch26275.03-hydroxyisobutyryl-Coenzyme A hydrolaseliterature, APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Branched-chain amino acid metabolism
124407785Ndufs64726.0NADH:ubiquinone oxidoreductase core subunit S6literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
12567041Oxct15019.03-oxoacid CoA transferase 1literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolism
12628295Gatd3a8209.0glutamine amidotransferase like class 1 domain containing 3AAPEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MS++Matrix0
12766218Ndufb94715.0NADH:ubiquinone oxidoreductase subunit B9literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
12812864Cox6c1345.0cytochrome c oxidase subunit 6Cliterature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
12920656Sod26648.0superoxide dismutase 2, mitochondrialliterature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism
13066046Ndufb54711.0NADH:ubiquinone oxidoreductase subunit B5literature, APEX_IMS, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression++, MS/MS+MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
13115107Hadh3033.0hydroxyacyl-Coenzyme A dehydrogenaseliterature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Amino acid metabolism > Lysine metabolism
13214151Fech2235.0ferrochelataseliterature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > Heme synthesis and processing | Metabolism > Metals and cofactors > Fe-S-containing proteins
13379464Lias11019.0lipoic acid synthetaseliterature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MSMatrixMetabolism > Lipid metabolism > Lipoate insertion | Metabolism > Metals and cofactors > Fe-S-containing proteins
13418041Nfs19054.0nitrogen fixation gene 1 (S. cerevisiae)literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Metals and cofactors > Fe-S-containing proteins
13514148Fdx12230.0ferredoxin 1literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS+MatrixMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis | Metabolism > Metals and cofactors > Heme synthesis and processing | Metabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Metals and cofactors > Fe-S-containing proteins | Metabolism > Vitamin metabolism > Vitamin D metabolism
136217038Mrm179922.0mitochondrial rRNA methyltransferase 1APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain+, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
13768565Mrps18a55168.0mitochondrial ribosomal protein S18Aliterature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
13875593Malsu1115416.0mitochondrial assembly of ribosomal large subunit 1literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assembly
139229487Gatb5188.0glutamyl-tRNA(Gln) amidotransferase, subunit Bliterature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
14070120Yars251067.0tyrosyl-tRNA synthetase 2 (mitochondrial)literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
14114297Fxn2395.0frataxinliterature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis
14215929Idh3g3421.0isocitrate dehydrogenase 3 (NAD+), gammaliterature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle
14366230Mrps2828957.0mitochondrial ribosomal protein S28literature, targetP signal+, mito protein domain+, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
14421856Timm4410469.0translocase of inner mitochondrial membrane 44literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Import motor
145270166Clpx10845.0caseinolytic mitochondrial matrix peptidase chaperone subunitliterature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteases
14694062Mrpl311222.0mitochondrial ribosomal protein L3literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
14726922Mecr51102.0mitochondrial trans-2-enoyl-CoA reductaseliterature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesis
14857279Slc25a20788.0solute carrier family 25 (mitochondrial carnitine/acylcarnitine translocase), member 20literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Metals and cofactors > Carnitine synthesis and transport | Metabolism > Metals and cofactors > Carnitine shuttle | Small molecule transport > SLC25A family
14911739Slc25a4291.0solute carrier family 25 (mitochondrial carrier, adenine nucleotide translocator), member 4literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import | Signaling > Calcium homeostasis > Mitochondrial permeability transition pore | Small molecule transport > SLC25A family
15056428Mtch223788.0mitochondrial carrier 2literature, APEX_IMS, yeast mito homolog+, mito protein domain+, induction, coexpression+, MS/MS++MOMSmall molecule transport > SLC25A family | Mitochondrial dynamics and surveillance > Fusion
15118604Pdk25164.0pyruvate dehydrogenase kinase, isoenzyme 2literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolism
152110323Cox6b11340.0cytochrome c oxidase, subunit 6B1literature, APEX_IMS, yeast mito homolog+, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
15322333Vdac17416.0voltage-dependent anion channel 1literature, APEX_IMS, yeast mito homolog+, mito protein domain+, coexpression++, MS/MS++MOMSignaling > Calcium homeostasis > Mitochondrial permeability transition pore | Mitochondrial dynamics and surveillance > Organelle contact sites | Small molecule transport
15466163Mrpl451073.0mitochondrial ribosomal protein L4literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
15564659Mrps1463931.0mitochondrial ribosomal protein S14literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
15615526Hspa93313.0heat shock protein 9APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis
15766108Ndufa94704.0NADH:ubiquinone oxidoreductase subunit A9literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
15817991Ndufa24695.0NADH:ubiquinone oxidoreductase subunit A2literature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
15966383Iscu23479.0iron-sulfur cluster assembly enzymeliterature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Metals and cofactors > Fe-S-containing proteins
16012261C1qbp708.0complement component 1, q subcomponent binding proteinliterature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS++MatrixSignaling > Immune response
161215951Afg1l246269.0AFG1 like ATPaseAPEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteases
162433771Micos10440574.0mitochondrial contact site and cristae organizing system subunit 10literature, APEX_IMS, yeast mito homolog, mito protein domain+, induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complex
16312856Cox1710063.0cytochrome c oxidase assembly protein 17, copper chaperoneliterature, APEX_IMS, yeast mito homolog, mito protein domain+, induction, coexpression++, MS/MS++IMSOXPHOS > Complex IV > CIV assembly factors | Metabolism > Metals and cofactors > Copper metabolism | OXPHOS > OXPHOS assembly factors
16456046Uqcc155245.0ubiquinol-cytochrome c reductase complex assembly factor 1literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex III > CIII assembly factors | OXPHOS > OXPHOS assembly factors
16566845Mrpl339553.0mitochondrial ribosomal protein L33literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
16611363Acadl33.0acyl-Coenzyme A dehydrogenase, long-chainliterature, targetP signal+, mito protein domain+, induction, coexpression+, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation
16717993Ndufs44724.0NADH:ubiquinone oxidoreductase core subunit S4literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
16812034Phb211331.0prohibitin 2literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones
16912040Bckdhb594.0branched chain ketoacid dehydrogenase E1, beta polypeptideliterature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS++MIMMetabolism > Amino acid metabolism > Branched-chain amino acid metabolism | Metabolism > Amino acid metabolism > Branched-chain amino acid dehydrogenase complex
17024030Mrps126183.0mitochondrial ribosomal protein S12literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
171223722Mcat27349.0malonyl CoA:ACP acyltransferase (mitochondrial)literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesis
17267707Mrpl2479590.0mitochondrial ribosomal protein L24literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
17368537Mrpl1328998.0mitochondrial ribosomal protein L13literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
174110821Pcca5095.0propionyl-Coenzyme A carboxylase, alpha polypeptideliterature, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Propanoate metabolism | Metabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Vitamin metabolism > Biotin utilizing proteins
17527397Mrpl1763875.0mitochondrial ribosomal protein L17literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
17626926Aifm19131.0apoptosis-inducing factor, mitochondrion-associated 1literature, APEX_IMS, targetP signal, yeast mito homolog, mito protein domain, induction, coexpression++, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > MIA40 | OXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors | Mitochondrial dynamics and surveillance > Apoptosis
17712857Cox4i11327.0cytochrome c oxidase subunit 4I1literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
17868493Ndufaf429078.0NADH:ubiquinone oxidoreductase complex assembly factor 4APEX_matrix, GFP, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
17971998Slc25a35399512.0solute carrier family 25, member 35APEX_matrix, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMSmall molecule transport > SLC25A family
18065111Dap37818.0death associated protein 3literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
18111949Atp5c1509.0ATP synthase, H+ transporting, mitochondrial F1 complex, gamma polypeptide 1literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
18267863Slc25a118402.0solute carrier family 25 (mitochondrial carrier oxoglutarate carrier), member 11literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis | Metabolism > Carbohydrate metabolism > Malate-aspartate shuttle | Metabolism > Carbohydrate metabolism > TCA-associated | Small molecule transport > SLC25A family
18330057Timm8b26521.0translocase of inner mitochondrial membrane 8Bliterature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones | Protein import, sorting and homeostasis > Protein import and sorting
18468332Sdhaf1644096.0succinate dehydrogenase complex assembly factor 1literature, targetP signal+, yeast mito homolog, mito protein domain+, induction, coexpression+, MS/MSMatrixOXPHOS > Complex II > CII assembly factors | OXPHOS > OXPHOS assembly factors
18527395Mrpl1529088.0mitochondrial ribosomal protein L15literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
18611655Alas1211.0aminolevulinic acid synthase 1literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > Heme synthesis and processing
18766531Cmc256942.0COX assembly mitochondrial protein 2APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS+IMSOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
188320717Pptc7160760.0PTC7 protein phosphatase homologAPEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, induction, coexpression, MS/MS++MatrixSignaling
18912041Bckdk10295.0branched chain ketoacid dehydrogenase kinaseliterature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++MatrixMetabolism > Amino acid metabolism > Branched-chain amino acid metabolism | Metabolism > Amino acid metabolism > Branched-chain amino acid dehydrogenase complex
19056551Txn225828.0thioredoxin 2literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS+MatrixMetabolism > Vitamin metabolism > Vitamin C metabolism | Metabolism > Detoxification > ROS and glutathione metabolism
19120917Suclg28801.0succinate-Coenzyme A ligase, GDP-forming, beta subunitliterature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle | Metabolism > Carbohydrate metabolism > Itaconate metabolism | Metabolism > Nucleotide metabolism > Nucleotide synthesis and processing
19267414Mfn155669.0mitofusin 1literature, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS+MOMMitochondrial dynamics and surveillance > Fusion | Mitochondrial dynamics and surveillance > Organelle contact sites
193230075Ndufb64712.0NADH:ubiquinone oxidoreductase subunit B6literature, APEX_IMS, APEX_matrix, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
19468202Ndufa54698.0NADH:ubiquinone oxidoreductase subunit A5literature, APEX_matrix, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
19553375Mtx210651.0metaxin 2literature, mito protein domain+, induction, coexpression++, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > SAM | Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
196239017Ogdhl55753.0oxoglutarate dehydrogenase-likeAPEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle
197110446Acat138.0acetyl-Coenzyme A acetyltransferase 1literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolism | Metabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Amino acid metabolism > Branched-chain amino acid metabolism | Metabolism > Amino acid metabolism > Lysine metabolism
19867856Echdc379746.0enoyl Coenzyme A hydratase domain containing 3targetP signal, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++Matrix0
199353242Mrpl21219927.0mitochondrial ribosomal protein L21literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
20056748Nfu127247.0NFU1 iron-sulfur cluster scaffoldAPEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Metals and cofactors > Fe-S-containing proteins
20167212Mrpl55128308.0mitochondrial ribosomal protein L55literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression++, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
20270207Taco151204.0translational activator of mitochondrially encoded cytochrome c oxidase Iliterature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factors | OXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
20371238Sdhaf357001.0succinate dehydrogenase complex assembly factor 3targetP signal, yeast mito homolog++, mito protein domain+, coexpression+, MS/MSMatrixOXPHOS > Complex II > CII assembly factors | OXPHOS > OXPHOS assembly factors
20466419Mrpl1165003.0mitochondrial ribosomal protein L11literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
20552430Echdc255268.0enoyl Coenzyme A hydratase domain containing 2targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++Matrix0
20612859Cox5b1329.0cytochrome c oxidase subunit 5Bliterature, APEX_IMS, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
20766885Acadsb36.0acyl-Coenzyme A dehydrogenase, short/branched chainliterature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Amino acid metabolism > Branched-chain amino acid metabolism
20857837Eral126284.0Era (G-protein)-like 1 (E. coli)APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
20956199Abcb1023456.0ATP-binding cassette, sub-family B (MDR/TAP), member 10literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS+MIMMetabolism > Metals and cofactors > Heme synthesis and processing | Small molecule transport > ABC transporters
21066821Bcs1l617.0BCS1-like (yeast)literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain+, coexpression+, MS/MS+MIMOXPHOS > Complex III > CIII assembly factors | OXPHOS > OXPHOS assembly factors
21172479Hsdl284263.0hydroxysteroid dehydrogenase like 2APEX_matrix, GFP, Rickettsial homolog, mito protein domain+, induction, coexpression+, MS/MS++Matrix0
21267899Cmc1152100.0COX assembly mitochondrial protein 1APEX_IMS, GFP, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MS+IMSOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
213109264Me310873.0malic enzyme 3, NADP(+)-dependent, mitochondrialliterature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA-associated
21415510Hspd13329.0heat shock protein 1 (chaperonin)literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperones
21575530Lyrm790624.0LYR motif containing 7literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS++MatrixOXPHOS > Complex III > CIII assembly factors | OXPHOS > OXPHOS assembly factors
21666399Tsfm10102.0Ts translation elongation factor, mitochondrialliterature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factors
21766071Ethe123474.0ethylmalonic encephalopathy 1literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, MS/MS++MatrixMetabolism > Sulfur metabolism
218212647Aldh4a18659.0aldehyde dehydrogenase 4 family, member A1literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Proline metabolism | Metabolism > Amino acid metabolism > Glyoxylate metabolism
21922334Vdac27417.0voltage-dependent anion channel 2literature, APEX_IMS, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MOMSmall molecule transport
22067892Coa6388753.0cytochrome c oxidase assembly factor 6APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression+, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
221227683Coq451117.0coenzyme Q4literature, targetP signal+, yeast mito homolog++, mito protein domain+, coexpression, MS/MSMIMMetabolism > Metals and cofactors > Coenzyme Q metabolism
22256357Ivd3712.0isovaleryl coenzyme A dehydrogenaseliterature, APEX_matrix, targetP signal+, mito protein domain+, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > Branched-chain amino acid metabolism
22311370Acadvl37.0acyl-Coenzyme A dehydrogenase, very long chainliterature, APEX_matrix, targetP signal+, mito protein domain+, coexpression+, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation
22413358Slc25a16576.0solute carrier family 25 (mitochondrial carrier, citrate transporter), member 1literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis | Metabolism > Carbohydrate metabolism > TCA-associated | Metabolism > Lipid metabolism | Small molecule transport > SLC25A family
22573095Slc25a42284439.0solute carrier family 25, member 42literature, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme A metabolism | Small molecule transport > SLC25A family
22674610Abcb811194.0ATP-binding cassette, sub-family B (MDR/TAP), member 8literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression++, MS/MS++MIMSmall molecule transport > ABC transporters
227595136Ndufs54725.0NADH:ubiquinone oxidoreductase core subunit S5literature, APEX_IMS, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
22850529Mrps751081.0mitchondrial ribosomal protein S7literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > Translation > Mitochondrial ribosome
22972039Mccc156922.0methylcrotonoyl-Coenzyme A carboxylase 1 (alpha)literature, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > Branched-chain amino acid metabolism | Metabolism > Vitamin metabolism > Biotin utilizing proteins
23018120Mrpl49740.0mitochondrial ribosomal protein L49literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
23169487Ndufaf579133.0NADH:ubiquinone oxidoreductase complex assembly factor 5literature, APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
23269527Mrps964965.0mitochondrial ribosomal protein S9literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > Translation > Mitochondrial ribosome
23368342Ndufb104716.0NADH:ubiquinone oxidoreductase subunit B10literature, APEX_matrix, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
23483945Dnaja39093.0DnaJ heat shock protein family (Hsp40) member A3literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++, MS/MS+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperones
23556284Mrpl199801.0mitochondrial ribosomal protein L19literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
23670478Mipep4285.0mitochondrial intermediate peptidaseliterature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, induction, MS/MS++MatrixProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage | Protein import, sorting and homeostasis > Protein homeostasis > Proteases
237641376Tomm40l84134.0translocase of outer mitochondrial membrane 40-liketargetP signal, yeast mito homolog+, mito protein domain+, induction, coexpression+, MS/MSMOMProtein import, sorting and homeostasis > Protein import and sorting > TOM
23876187Adhfe1137872.0alcohol dehydrogenase, iron containing, 1targetP signal, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolism
23967426Coq8a56997.0coenzyme Q8Aliterature, APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MIMMetabolism > Metals and cofactors > Coenzyme Q metabolism
24071911Bdh1622.03-hydroxybutyrate dehydrogenase, type 1literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Ketone metabolism
24166169Tomm754543.0translocase of outer mitochondrial membrane 7literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > TOM | Mitochondrial dynamics and surveillance > Mitophagy | Mitochondrial dynamics and surveillance > Autophagy
24215159Hccs3052.0holocytochrome c synthetaseliterature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSIMSMetabolism > Metals and cofactors > Heme synthesis and processing | OXPHOS > OXPHOS subunits | OXPHOS > Cytochrome C
24394063Mrpl1654948.0mitochondrial ribosomal protein L16literature, targetP signal, yeast mito homolog++, mito protein domain, coexpression++, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
24419125Prodh5625.0proline dehydrogenaseliterature, targetP signal, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > Proline metabolism | Metabolism > Electron carriers > Q-linked reactions, other
245107734Mrpl3051263.0mitochondrial ribosomal protein L30literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
24667273Ndufa104705.0NADH:ubiquinone oxidoreductase subunit A10literature, targetP signal+, mito protein domain, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
247212679Mars292935.0methionine-tRNA synthetase 2 (mitochondrial)literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
24853895Clpp8192.0caseinolytic mitochondrial matrix peptidase proteolytic subunitliterature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteases
24956248Ak350808.0adenylate kinase 3literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
250234847Spg76687.0SPG7, paraplegin matrix AAA peptidase subunitliterature, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression+, MS/MSMIMProtein import, sorting and homeostasis > Protein homeostasis > Proteases
25152892Sco16341.0SCO1 cytochrome c oxidase assembly proteinliterature, APEX_IMS, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MIMOXPHOS > Complex IV > CIV assembly factors | Metabolism > Metals and cofactors > Copper metabolism | OXPHOS > OXPHOS assembly factors
25211983Atpif193974.0ATPase inhibitory factor 1literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS++MatrixOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
25366075Chchd354927.0coiled-coil-helix-coiled-coil-helix domain containing 3literature, APEX_IMS, APEX_matrix, GFP, Rickettsial homolog, induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complex | Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
254338350Acad12acyl-Coenzyme A dehydrogenase family, member 12targetP signal+, mito protein domain+, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation
25558875Hibadh11112.03-hydroxyisobutyrate dehydrogenaseliterature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > Branched-chain amino acid metabolism
256384281Gatc283459.0glutamyl-tRNA(Gln) amidotransferase, subunit Cliterature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
25712869Cox8bcytochrome c oxidase subunit 8Bliterature, targetP signal, mito protein domain+, induction, coexpression+, MS/MS++MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
25820480Clpb81570.0ClpB caseinolytic peptidase BAPEX_IMS, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++IMSProtein import, sorting and homeostasis > Protein homeostasis > Proteases
25966271Tmem126a84233.0transmembrane protein 126Aliterature, mito protein domain+, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
260104776Aldh6a14329.0aldehyde dehydrogenase family 6, subfamily A1literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > Branched-chain amino acid metabolism
26168735Mrps18c51023.0mitochondrial ribosomal protein S18Cliterature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
262228026Pdk15163.0pyruvate dehydrogenase kinase, isoenzyme 1literature, APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolism
263105675Ppif10105.0peptidylprolyl isomerase F (cyclophilin F)literature, APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain, induction, coexpression, MS/MS++MatrixSignaling > Calcium homeostasis > Mitochondrial permeability transition pore
264380840Lyrm457128.0LYR motif containing 4literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis
26551798Ech11891.0enoyl coenzyme A hydratase 1, peroxisomalAPEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism
26652538Acaa210449.0acetyl-Coenzyme A acyltransferase 2 (mitochondrial 3-oxoacyl-Coenzyme A thiolase)literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolism | Metabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Amino acid metabolism > Lysine metabolism
26766416Ndufa74701.0NADH:ubiquinone oxidoreductase subunit A7literature, APEX_matrix, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
26866223Mrpl3551318.0mitochondrial ribosomal protein L35literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
26966904Pccb5096.0propionyl Coenzyme A carboxylase, beta polypeptideliterature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Propanoate metabolism | Metabolism > Lipid metabolism > Fatty acid oxidation
27071883Coq227235.0coenzyme Q2 4-hydroxybenzoate polyprenyltransferaseliterature, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolism
27166448Mrpl2055052.0mitochondrial ribosomal protein L20literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
27221854Timm17a10440.0translocase of inner mitochondrial membrane 17aliterature, APEX_IMS, yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathway
27356322Timm2229928.0translocase of inner mitochondrial membrane 22literature, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > TIM22 carrier pathway
27466047Mrpl54116541.0mitochondrial ribosomal protein L54literature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
275223696Tomm2256993.0translocase of outer mitochondrial membrane 22literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > TOM
27612908Crat1384.0carnitine acetyltransferaseliterature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation
27777721Mrps564969.0mitochondrial ribosomal protein S5literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
278209692Dhtkd155526.0dehydrogenase E1 and transketolase domain containing 1APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MSMatrixMetabolism > Amino acid metabolism > Lysine metabolism
27970397Tmem7054968.0transmembrane protein 70literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression++, MS/MSMIMOXPHOS > Complex I > CI assembly factors | OXPHOS > Complex V > CV assembly factors | OXPHOS > OXPHOS assembly factors
28066400Alkbh784266.0alkB homolog 7APEX_matrix, targetP signal+, mito protein domain, induction, coexpression++, MS/MSMatrix0
28164655Mrps2256945.0mitochondrial ribosomal protein S22literature, APEX_matrix, targetP signal+, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
28267530Uqcrb7381.0ubiquinol-cytochrome c reductase binding proteinliterature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex III > CIII subunits | OXPHOS > OXPHOS subunits
28312867Cox7c1350.0cytochrome c oxidase subunit 7Cliterature, APEX_IMS, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
28469702Ndufaf151103.0NADH:ubiquinone oxidoreductase complex assembly factor 1literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
28566948Acad827034.0acyl-Coenzyme A dehydrogenase family, member 8literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Branched-chain amino acid metabolism
28670560Wars210352.0tryptophanyl tRNA synthetase 2 (mitochondrial)literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
28779044Mrps3465993.0mitochondrial ribosomal protein S34literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
28878330Ndufv34731.0NADH:ubiquinone oxidoreductase core subunit V3literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
28968198Ndufb24708.0NADH:ubiquinone oxidoreductase subunit B2literature, targetP signal, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
29078830Slc25a128604.0solute carrier family 25 (mitochondrial carrier, Aralar), member 12literature, yeast mito homolog+, mito protein domain+, induction, MS/MS++MIMMetabolism > Carbohydrate metabolism > Malate-aspartate shuttle | Metabolism > Amino acid metabolism > Glutamate metabolism | Signaling > Calcium homeostasis > EF hand proteins | Small molecule transport > SLC25A family
29111740Slc25a5292.0solute carrier family 25 (mitochondrial carrier, adenine nucleotide translocator), member 5literature, yeast mito homolog+, mito protein domain+, induction, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import | Signaling > Calcium homeostasis > Mitochondrial permeability transition pore | Small molecule transport > SLC25A family
29266292Mrps2154460.0mitochondrial ribosomal protein S21literature, yeast mito homolog++, Rickettsial homolog, mito protein domain, induction, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
29376467Msrb222921.0methionine sulfoxide reductase B2APEX_matrix, targetP signal+, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism | Metabolism > Sulfur metabolism
29473046Glrx551218.0glutaredoxin 5literature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Metals and cofactors > Fe-S-containing proteins
295103172Chchd10400916.0coiled-coil-helix-coiled-coil-helix domain containing 10literature, targetP signal, yeast mito homolog+, mito protein domain, induction, coexpression++IMS0
29667876Coq10b80219.0coenzyme Q10BGFP, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolism
29767554Slc25a30253512.0solute carrier family 25, member 30literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Sulfur metabolism | Small molecule transport > SLC25A family
29850799Slc25a1310165.0solute carrier family 25 (mitochondrial carrier, adenine nucleotide translocator), member 13literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Malate-aspartate shuttle | Metabolism > Amino acid metabolism > Urea cycle | Signaling > Calcium homeostasis > EF hand proteins | Small molecule transport > SLC25A family
29927376Slc25a101468.0solute carrier family 25 (mitochondrial carrier, dicarboxylate transporter), member 10literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis | Metabolism > Carbohydrate metabolism > Malate-aspartate shuttle | Small molecule transport > SLC25A family
30012865Cox7a11346.0cytochrome c oxidase subunit 7A1literature, targetP signal, mito protein domain+, induction, coexpression, MS/MS+MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
30167283Slc25a1960386.0solute carrier family 25 (mitochondrial thiamine pyrophosphate carrier), member 19literature, yeast mito homolog++, mito protein domain+, induction, coexpression, MS/MSMIMMetabolism > Vitamin metabolism > Vitamin B1 metabolism | Small molecule transport > SLC25A family
30269029Smdt191689.0single-pass membrane protein with aspartate rich tail 1literature, targetP signal, mito protein domain+, induction, coexpression+, MS/MSMIMSignaling > Calcium homeostasis > Calcium cycle | Small molecule transport > Calcium uniporter
303216767Mrpl2229093.0mitochondrial ribosomal protein L22literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
30464657Mrps1055173.0mitochondrial ribosomal protein S10literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
305114896Afg3l1AFG3-like AAA ATPase 1literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteases
30614149Fdxr2232.0ferredoxin reductaseliterature, APEX_matrix, targetP signal, yeast mito homolog++, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis | Metabolism > Metals and cofactors > Heme synthesis and processing | Metabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Vitamin metabolism > Vitamin D metabolism
307380773Slirp81892.0SRA stem-loop interacting RNA binding proteinliterature, APEX_matrix, GFP, targetP signal+, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay | Mitochondrial central dogma > Translation
30867811Poldip226073.0polymerase (DNA-directed), delta interacting protein 2literature, APEX_matrix, targetP signal+, induction, coexpression++, MS/MS++MatrixMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid
309257633Acsf3197322.0acyl-CoA synthetase family member 3APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesis
31069089Oxa1l5018.0oxidase assembly 1-likeliterature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMIMProtein import, sorting and homeostasis > Protein import and sorting > OXA | Mitochondrial central dogma > Translation
311269951Idh23418.0isocitrate dehydrogenase 2 (NADP+), mitochondrialliterature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA cycle
31227425Atp5l10632.0ATP synthase, H+ transporting, mitochondrial F0 complex, subunit Gliterature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits | Mitochondrial dynamics and surveillance > Cristae formation
31369168Bola151027.0bolA-like 1 (E. coli)GFP, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Metals and cofactors > Fe-S-containing proteins
31468126Fahd2a51011.0fumarylacetoacetate hydrolase domain containing 2AAPEX_matrix, targetP signal, yeast mito homolog, mito protein domain, induction, coexpression, MS/MS++Matrix0
31567636Etfrf1144363.0electron transfer flavoprotein regulatory factor 1mito protein domain+, induction, coexpression, MS/MS++MatrixMetabolism > Electron carriers > Q-linked reactions, other
31668197Ndufc24718.0NADH:ubiquinone oxidoreductase subunit C2literature, APEX_IMS, mito protein domain+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
31768375Ndufa84702.0NADH:ubiquinone oxidoreductase subunit A8literature, APEX_IMS, mito protein domain, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
318270685Mthfd1l25902.0methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 1-likeliterature, APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolism
319236900Pdk35165.0pyruvate dehydrogenase kinase, isoenzyme 3literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolism
32066379Cox1484987.0cytochrome c oxidase assembly protein 14literature, GFP, mito protein domain+, induction, coexpression++, MS/MS+MIMMitochondrial central dogma > Translation > Translation factors | OXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
321270076Gcdh2639.0glutaryl-Coenzyme A dehydrogenaseliterature, APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Lysine metabolism
32266493Mrpl5151258.0mitochondrial ribosomal protein L51literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
32314651Hagh3029.0hydroxyacyl glutathione hydrolaseliterature, APEX_matrix, targetP signal+, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism
32417827Mtx14580.0metaxin 1literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > SAM | Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
32569955Fars210667.0phenylalanine-tRNA synthetase 2 (mitochondrial)literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
326234309Cbr484869.0carbonyl reductase 4literature, APEX_matrix, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesis
32775398Mrpl3264983.0mitochondrial ribosomal protein L32literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
328696622310061I04Rik221545.0RIKEN cDNA 2310061I04 genetargetP signal, induction, coexpression++, MS/MS+Matrix0
32968165Fdx2112812.0ferredoxin 2APEX_matrix, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > Heme synthesis and processing | Metabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Metals and cofactors > Fe-S-containing proteins
33017709mt-Co24513.0cytochrome c oxidase subunit IIliterature, APEX_IMS, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
33117705mt-Atp64508.0ATP synthase F0 subunit 6literature, yeast mito homolog++, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
33268015Trap110131.0TNF receptor-associated protein 1APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpression++, MS/MS+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperones
33314571Gpd22820.0glycerol phosphate dehydrogenase 2, mitochondrialliterature, APEX_IMS, yeast mito homolog++, mito protein domain, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > Glycerol phosphate shuttle | Metabolism > Electron carriers > Q-linked reactions, other
33411306Abcb722.0ATP-binding cassette, sub-family B (MDR/TAP), member 7literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression+, MS/MS+MIMMetabolism > Metals and cofactors > Heme synthesis and processing | Metabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteins | Small molecule transport > ABC transporters
33515108Hsd17b103028.0hydroxysteroid (17-beta) dehydrogenase 10literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing | Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications | Metabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis | Metabolism > Amino acid metabolism > Branched-chain amino acid metabolism
33614661Glud12746.0glutamate dehydrogenase 1literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Glutamate metabolism | Metabolism > Amino acid metabolism > GABA metabolism
33711669Aldh2217.0aldehyde dehydrogenase 2, mitochondrialliterature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolism
338233870Tufm7284.0Tu translation elongation factor, mitochondrialliterature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Translation factors
33966592Stoml230968.0stomatin (Epb7.2)-like 2literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis
34028200Dhrs410901.0dehydrogenase/reductase (SDR family) member 4targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Vitamin metabolism > Vitamin A metabolism
34156752Aldh9a1223.0aldehyde dehydrogenase 9, subfamily A1APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolism | Metabolism > Detoxification > ROS and glutathione metabolism
342244141Nars279731.0asparaginyl-tRNA synthetase 2 (mitochondrial)(putative)GFP, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
343219189Vwa823078.0von Willebrand factor A domain containing 8APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression+, MS/MS++Matrix0
34499045Mrps2664949.0mitochondrial ribosomal protein S26literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
345268822Adck5203054.0aarF domain containing kinase 5targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSunknown0
34671941Cars279587.0cysteinyl-tRNA synthetase 2 (mitochondrial)(putative)APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
34770383Cox101352.0heme A:farnesyltransferase cytochrome c oxidase assembly factor 10literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression++MIMOXPHOS > Complex IV > CIV assembly factors | Metabolism > Metals and cofactors > Heme synthesis and processing | OXPHOS > OXPHOS assembly factors
348104130Ndufb1154539.0NADH:ubiquinone oxidoreductase subunit B11literature, APEX_IMS, APEX_matrix, targetP signal+, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
34918598Pdha2pyruvate dehydrogenase E1 alpha 2literature, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolism
350381760Ssbp16742.0single-stranded DNA binding protein 1literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication | Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid
351100900Hscb150274.0HscB iron-sulfur cluster co-chaperoneAPEX_matrix, GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis
35294064Mrpl2751264.0mitochondrial ribosomal protein L27literature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
35368917Hint284681.0histidine triad nucleotide binding protein 2APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis
354110826Etfb2109.0electron transferring flavoprotein, beta polypeptideliterature, APEX_matrix, yeast mito homolog, mito protein domain, induction, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Amino acid metabolism > Branched-chain amino acid metabolism | Metabolism > Amino acid metabolism > Lysine metabolism | Metabolism > Amino acid metabolism > Glycine metabolism | Metabolism > Vitamin metabolism > Choline and betaine metabolism | Metabolism > Electron carriers > Q-linked reactions, other
35518408Slc25a1510166.0solute carrier family 25 (mitochondrial carrier ornithine transporter), member 15literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > Urea cycle | Small molecule transport > SLC25A family
356218885Oxnad192106.0oxidoreductase NAD-binding domain containing 1APEX_matrix, GFP, targetP signal, yeast mito homolog, mito protein domain, coexpression++, MS/MS++Matrix0
35713067Cyctcytochrome c, testisliterature, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++IMSMetabolism > Electron carriers > Cytochromes | OXPHOS > OXPHOS subunits | OXPHOS > Cytochrome C
35813063Cycs54205.0cytochrome c, somaticliterature, APEX_IMS, yeast mito homolog+, Rickettsial homolog, mito protein domain+, MS/MS++IMSMetabolism > Metals and cofactors > Heme-containing proteins | Metabolism > Electron carriers > Cytochromes | OXPHOS > OXPHOS subunits | OXPHOS > Cytochrome C | Mitochondrial dynamics and surveillance > Apoptosis
35919935Mrpl236150.0mitochondrial ribosomal protein L23literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
36078523Mrpl965005.0mitochondrial ribosomal protein L9literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
36166121Chchd1118487.0coiled-coil-helix-coiled-coil-helix domain containing 1GFP, targetP signal, yeast mito homolog++, mito protein domain, coexpression+, MS/MSMIMMitochondrial central dogma > Translation > Mitochondrial ribosome
362108888Atad3a55210.0ATPase family, AAA domain containing 3AAPEX_IMS, APEX_matrix, GFP, yeast mito homolog, Rickettsial homolog, mito protein domain+, coexpression, MS/MS++MIMMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid | Mitochondrial dynamics and surveillance > Organelle contact sites | Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
36317850Mmut4594.0methylmalonyl-Coenzyme A mutaseliterature, APEX_matrix, targetP signal, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Propanoate metabolism | Metabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Vitamin metabolism > Vitamin B12 metabolism
36452637Cisd155847.0CDGSH iron sulfur domain 1literature, mito protein domain, induction, coexpression++, MS/MS++MOMMetabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Metals and cofactors > Fe-S-containing proteins
365226539Dars255157.0aspartyl-tRNA synthetase 2 (mitochondrial)APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
36656454Aldh18a15832.0aldehyde dehydrogenase 18 family, member A1literature, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Proline metabolism
36728028Mrpl5054534.0mitochondrial ribosomal protein L50literature, APEX_matrix, targetP signal+, mito protein domain+, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
36812868Cox8a1351.0cytochrome c oxidase subunit 8Aliterature, targetP signal+, mito protein domain+, coexpression+, MS/MSMIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
369121022Mrps664968.0mitochondrial ribosomal protein S6literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
37015528Hspe13336.0heat shock protein 1 (chaperonin 10)literature, APEX_IMS, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperones
37174776Ppa227068.0pyrophosphatase (inorganic) 2literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > mtDNA maintenance | Mitochondrial central dogma > mtRNA metabolism | Mitochondrial central dogma > Translation | Metabolism > Nucleotide metabolism
37218563Pcx5091.0pyruvate carboxylaseliterature, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Gluconeogenesis | Metabolism > Carbohydrate metabolism > TCA-associated | Metabolism > Vitamin metabolism > Biotin utilizing proteins
373104174Gldc2731.0glycine decarboxylaseliterature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Glycine metabolism | Metabolism > Amino acid metabolism > Glycine cleavage system
37468971Tamm41132001.0TAM41 mitochondrial translocator assembly and maintenance homologGFP, yeast mito homolog++, mito protein domain+, MS/MS++MIMMetabolism > Lipid metabolism > Cardiolipin synthesis | Metabolism > Lipid metabolism > Phospholipid metabolism
375228033Atp5g3518.0ATP synthase, H+ transporting, mitochondrial F0 complex, subunit C3 (subunit 9)literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
37660441Mrpl3864978.0mitochondrial ribosomal protein L38APEX_matrix, targetP signal+, mito protein domain, coexpression++, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
37766414Ndufa1255967.0NADH:ubiquinone oxidoreductase subunit A12literature, APEX_matrix, Rickettsial homolog, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
37868023Pdf64146.0peptide deformylase (mitochondrial)APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > fMet processing | Protein import, sorting and homeostasis > Protein homeostasis
37971985Acad1080724.0acyl-Coenzyme A dehydrogenase family, member 10APEX_matrix, targetP signal+, mito protein domain+, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation
38096979Ptges280142.0prostaglandin E synthase 2literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain, induction, coexpression+, MS/MS++MIMMetabolism > Lipid metabolism > Eicosanoid metabolism
381381045Ccdc58131076.0coiled-coil domain containing 58APEX_IMS, yeast mito homolog++, mito protein domain+, MS/MS++IMS0
38273333Slc25a3183447.0solute carrier family 25 (mitochondrial carrier; adenine nucleotide translocator), member 31literature, yeast mito homolog++, mito protein domain+, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import | Signaling > Calcium homeostasis > Mitochondrial permeability transition pore | Small molecule transport > SLC25A family
38371679Atp5h10476.0ATP synthase, H+ transporting, mitochondrial F0 complex, subunit Dliterature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
38411950Atp5pb515.0ATP synthase peripheral stalk-membrane subunit bliterature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MS++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
385107733Mrpl4164975.0mitochondrial ribosomal protein L41literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
38626462Txnrd210587.0thioredoxin reductase 2literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism | Metabolism > Detoxification > Selenoproteins
38773724Mcee84693.0methylmalonyl CoA epimerasetargetP signal, induction, coexpression++, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Propanoate metabolism | Metabolism > Lipid metabolism > Fatty acid oxidation
38878038Mccc264087.0methylcrotonoyl-Coenzyme A carboxylase 2 (beta)literature, targetP signal, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Amino acid metabolism > Branched-chain amino acid metabolism
38968927Ptcd279810.0pentatricopeptide repeat domain 2literature, targetP signal, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing
39011639Ak4205.0adenylate kinase 4APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
391227731Slc25a25114789.0solute carrier family 25 (mitochondrial carrier, phosphate carrier), member 25literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import | Signaling > Calcium homeostasis > EF hand proteins | Small molecule transport > SLC25A family
39253333Tomm4010452.0translocase of outer mitochondrial membrane 40literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > TOM
39369634Clybl171425.0citrate lyase beta likeAPEX_matrix, targetP signal+, induction, coexpression+, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Itaconate metabolism
39474238Mterf280298.0mitochondrial transcription termination factor 2literature, APEX_matrix, targetP signal, mito protein domain+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid
395230935Dnajc1155735.0DnaJ heat shock protein family (Hsp40) member C11GFP, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting | Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
39667460Decr11666.02,4-dienoyl CoA reductase 1, mitochondrialliterature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation
39776947Ndufaf6137682.0NADH:ubiquinone oxidoreductase complex assembly factor 6literature, targetP signal, mito protein domain, induction, coexpression++, MS/MSMIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
398329384Ptrh1138428.0peptidyl-tRNA hydrolase 1 homologAPEX_matrix, GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrix0
39966084Rmnd155005.0required for meiotic nuclear division 1 homologliterature, GFP, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMIMMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > Translation
40026912Gcat23464.0glycine C-acetyltransferase (2-amino-3-ketobutyrate-coenzyme A ligase)literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++unknownMetabolism > Amino acid metabolism > Glycine metabolism
40166459Pyurf100996939.0Pigy upstream reading frametargetP signal+, induction, coexpression++, MS/MSunknown0
402117147Acsm1116285.0acyl-CoA synthetase medium-chain family member 1literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation
40367979Atad184896.0ATPase family, AAA domain containing 1yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MOMProtein import, sorting and homeostasis > Protein homeostasis > Proteases
40466154Tmem14c51522.0transmembrane protein 14Cliterature, yeast mito homolog, mito protein domain+, induction, coexpression, MS/MS+MIM0
405223665C030006K11Rik414919.0RIKEN cDNA C030006K11 geneAPEX_matrix, targetP signal+, coexpression+, MS/MS++Matrix0
40652633Nit256954.0nitrilase family, member 2yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++unknownMetabolism > Detoxification
40767582Slc25a26115286.0solute carrier family 25 (mitochondrial carrier, phosphate carrier), member 26literature, yeast mito homolog++, mito protein domain+, coexpression, MS/MSMIMSmall molecule transport > SLC25A family
40867105Timm2129090.0translocase of inner mitochondrial membrane 21APEX_IMS, GFP, yeast mito homolog++, mito protein domain+, coexpression, MS/MSMIMMitochondrial central dogma > Translation > Translation factors | Protein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathway | OXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
40917992Ndufa44697.0Ndufa4, mitochondrial complex associatedliterature, targetP signal, mito protein domain, coexpression++, MS/MS++MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
410104444Rexo225996.0RNA exonuclease 2APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domain, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
411107029Me24200.0malic enzyme 2, NAD(+)-dependent, mitochondrialliterature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA-associated
41271984Sars254938.0seryl-aminoacyl-tRNA synthetase 2literature, APEX_matrix, targetP signal+, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
41352838Dnlz728489.0DNL-type zinc fingerAPEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, MS/MSMatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperones
41476722Ckmt21160.0creatine kinase, mitochondrial 2literature, targetP signal, mito protein domain, induction, coexpression, MS/MS++MIMMetabolism > Nucleotide metabolism > Creatine metabolism
41566701Spryd4283377.0SPRY domain containing 4APEX_matrix, GFP, targetP signal, mito protein domain, coexpression+, MS/MS++Matrix0
41668021Bphl670.0biphenyl hydrolase-like (serine hydrolase, breast epithelial mucin-associated antigen)targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolism
41772170Chchd4131474.0coiled-coil-helix-coiled-coil-helix domain containing 4literature, APEX_IMS, yeast mito homolog++, mito protein domain, induction, coexpression, MS/MS+IMSProtein import, sorting and homeostasis > Protein import and sorting > MIA40
41856280Mrpl3751253.0mitochondrial ribosomal protein L37literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
419230125Slc25a5192014.0solute carrier family 25, member 51GFP, yeast mito homolog+, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > NAD biosynthesis and metabolism | Small molecule transport > SLC25A family
42067247Mtarc254996.0mitochondrial amidoxime reducing component 2literature, targetP signal, mito protein domain+, induction, coexpression, MS/MS++MOMMetabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteins | Metabolism > Detoxification > Xenobiotic metabolism | Metabolism > Detoxification > Amidoxime reducing complex
42166541Immp1l196294.0IMP1 inner mitochondrial membrane peptidase-like (S. cerevisiae)literature, yeast mito homolog++, Rickettsial homolog, mito protein domain+, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage | Protein import, sorting and homeostasis > Protein homeostasis > Proteases
422108654Fam210a125228.0family with sequence similarity 210, member AGFP, targetP signal, induction, coexpression++, MS/MSMIM0
42364660Mrps2464951.0mitochondrial ribosomal protein S24literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
42421855Timm17b10245.0translocase of inner mitochondrial membrane 17bliterature, APEX_IMS, yeast mito homolog+, mito protein domain+, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathway
42570791Hars223438.0histidyl-tRNA synthetase 2literature, APEX_matrix, GFP, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
42666272Cox1651241.0cytochrome c oxidase assembly protein 16APEX_IMS, GFP, targetP signal, yeast mito homolog++, mito protein domain+, MS/MS+MIMOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
42771365Pdss257107.0prenyl (solanesyl) diphosphate synthase, subunit 2literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression+MIMMetabolism > Metals and cofactors > Coenzyme Q metabolism
42813177Eci11632.0enoyl-Coenzyme A delta isomerase 1literature, APEX_matrix, targetP signal+, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation
42968349Ndufs34722.0NADH:ubiquinone oxidoreductase core subunit S3literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
43015360Hmgcs23158.03-hydroxy-3-methylglutaryl-Coenzyme A synthase 2literature, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolism
431217666L2hgdh79944.0L-2-hydroxyglutarate dehydrogenaseliterature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS++MIMMetabolism > Carbohydrate metabolism > TCA-associated
432225791Zadh2284273.0zinc binding alcohol dehydrogenase, domain containing 2targetP signal, mito protein domain, induction, coexpression+, MS/MS++unknownMetabolism > Lipid metabolism > Eicosanoid metabolism
43366077Aurkaip154998.0aurora kinase A interacting protein 1GFP, targetP signal+, yeast mito homolog++, mito protein domain, coexpression+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
43476178Coa5493753.0cytochrome C oxidase assembly factor 5literature, APEX_IMS, yeast mito homolog++, mito protein domain+, induction, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
43514979H2-Ke67923.0H2-K region expressed gene 6APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesis | Metabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis
436224904Micos13125988.0mitochondrial contact site and cristae organizing system subunit 13induction, coexpression++, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complex
43766916Ndufb74713.0NADH:ubiquinone oxidoreductase subunit B7literature, APEX_IMS, APEX_matrix, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
43814467Nipsnap22631.0nipsnap homolog 2literature, APEX_matrix, targetP signal+, induction, coexpression, MS/MS++MatrixMitochondrial dynamics and surveillance > Mitophagy | Mitochondrial dynamics and surveillance > Autophagy
43974600Mrpl4757129.0mitochondrial ribosomal protein L47literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > Translation > Mitochondrial ribosome
44067851Mtres151250.0mitochondrial transcription rescue factor 1GFP, targetP signal, induction, coexpression++, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > Transcription | Mitochondrial central dogma > Translation
44173694Ndufaf755471.0NADH:ubiquinone oxidoreductase complex assembly factor 7APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain+, coexpression, MS/MSMIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
442229211Acad928976.0acyl-Coenzyme A dehydrogenase family, member 9literature, APEX_matrix, targetP signal+, mito protein domain+, MS/MS++MIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
443217214Nags162417.0N-acetylglutamate synthaseliterature, targetP signal, yeast mito homolog++, mito protein domain+, MS/MSMatrixMetabolism > Amino acid metabolism > Urea cycle
44452815Ldhd197257.0lactate dehydrogenase Dliterature, targetP signal+, yeast mito homolog+, mito protein domain, MS/MS++MIMMetabolism > Carbohydrate metabolism
445192166Sardh1757.0sarcosine dehydrogenaseliterature, targetP signal+, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Glycine metabolism | Metabolism > Vitamin metabolism > Choline and betaine metabolism | Metabolism > Vitamin metabolism > Folate and 1-C metabolism
44620751Spr6697.0sepiapterin reductasetargetP signal, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS++unknownMetabolism > Metals and cofactors > Tetrahydrobiopterin synthesis
447246703Naxe128240.0NAD(P)HX epimeraseAPEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolism
44853600Timm23100287932.0translocase of inner mitochondrial membrane 23literature, APEX_IMS, yeast mito homolog++, mito protein domain+, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathway
44917527Mpv174358.0MpV17 mitochondrial inner membrane proteinliterature, targetP signal, yeast mito homolog+, mito protein domain, coexpression, MS/MS++MIMSmall molecule transport
450212508Mtg192170.0mitochondrial ribosome-associated GTPase 1literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assembly
45115925Ide3416.0insulin degrading enzymeliterature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain+, coexpression, MS/MS+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteases
45270047Trnt151095.0tRNA nucleotidyl transferase, CCA-adding, 1literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
45364658Mrps2564432.0mitochondrial ribosomal protein S25literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
45468463Mrpl1464928.0mitochondrial ribosomal protein L14literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression+, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
45559054Mrps3010884.0mitochondrial ribosomal protein S30literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
45666242Mrps1651021.0mitochondrial ribosomal protein S16literature, APEX_matrix, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
45777619Prelid2153768.0PRELI domain containing 2yeast mito homolog+, mito protein domain+, induction, coexpression, MS/MSIMS0
458108037Shmt26472.0serine hydroxymethyltransferase 2 (mitochondrial)literature, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Serine metabolism | Metabolism > Amino acid metabolism > Glycine metabolism | Metabolism > Vitamin metabolism > Folate and 1-C metabolism
459211389Suox6821.0sulfite oxidaseAPEX_IMS, targetP signal, mito protein domain+, coexpression, MS/MS++IMSMetabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteins | Metabolism > Sulfur metabolism
46066365Ccdc90b60492.0coiled-coil domain containing 90Bliterature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain+, MS/MSMIM0
46166302Rmdn151115.0regulator of microtubule dynamics 1APEX_IMS, targetP signal+, mito protein domain, induction, coexpression, MS/MSMOM0
462272428Acsm554988.0acyl-CoA synthetase medium-chain family member 5literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Detoxification > Xenobiotic metabolism
46394066Mrpl3664979.0mitochondrial ribosomal protein L36literature, targetP signal, yeast mito homolog++, mito protein domain, induction, coexpression+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
46476263Gstk1373156.0glutathione S-transferase kappa 1literature, mito protein domain+, coexpression+, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolism
46566117Fmc1154791.0formation of mitochondrial complex V assembly factor 1literature, APEX_matrix, targetP signal, induction, coexpression++, MS/MSMatrixOXPHOS > Complex V > CV assembly factors | OXPHOS > OXPHOS assembly factors
46668572Mrpl583396.0mitochondrial ribosomal protein L58APEX_matrix, GFP, targetP signal+, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome | Mitochondrial central dogma > Translation > Translation factors
46712894Cpt1a1374.0carnitine palmitoyltransferase 1a, liverliterature, yeast mito homolog+, mito protein domain, induction, coexpression, MS/MS++MOMMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Metals and cofactors > Carnitine synthesis and transport | Metabolism > Metals and cofactors > Carnitine shuttle
46811637Ak2204.0adenylate kinase 2literature, APEX_IMS, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression+, MS/MS++IMSMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
469726502810006K23Rik91574.0RIKEN cDNA 2810006K23 geneliterature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > Translation factors
47014660Gls2744.0glutaminaseliterature, APEX_matrix, targetP signal+, mito protein domain+, MS/MS++MIMMetabolism > Amino acid metabolism > Glutamate metabolism
47175778Them4117145.0thioesterase superfamily member 4literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, induction, MS/MS++MIMMetabolism > Lipid metabolism
47256075Pdss123590.0prenyl (solanesyl) diphosphate synthase, subunit 1APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionMIMMetabolism > Metals and cofactors > Coenzyme Q metabolism
47352856Mtg226164.0mitochondrial ribosome associated GTPase 2literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assembly
47467994Mrps1164963.0mitochondrial ribosomal protein S11literature, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
47556690Mlycd23417.0malonyl-CoA decarboxylaseliterature, APEX_matrix, targetP signal, mito protein domain, coexpression++, MS/MSMatrixMetabolism > Lipid metabolism
476382117Tcaim285343.0T cell activation inhibitor, mitochondrialliterature, APEX_matrix, targetP signal+, mito protein domain+, coexpression++Matrix0
47766377Ndufc14717.0NADH:ubiquinone oxidoreductase subunit C1literature, targetP signal+, mito protein domain+, coexpression++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
47814782Gsr2936.0glutathione reductaseliterature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism
479109093Rars257038.0arginyl-tRNA synthetase 2, mitochondrialliterature, APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
480229731Slc25a2429957.0solute carrier family 25 (mitochondrial carrier, phosphate carrier), member 24literature, APEX_IMS, yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide import | Signaling > Calcium homeostasis > EF hand proteins | Small molecule transport > SLC25A family
48171803Slc25a1883733.0solute carrier family 25 (mitochondrial carrier), member 18literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMSmall molecule transport > SLC25A family
48268267Slc25a2279751.0solute carrier family 25 (mitochondrial carrier, glutamate), member 22literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMSmall molecule transport > SLC25A family
48355951Mpc151660.0mitochondrial pyruvate carrier 1GFP, yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis | Metabolism > Carbohydrate metabolism > Pyruvate metabolism | Metabolism > Carbohydrate metabolism > TCA-associated | Small molecule transport
48430058Timm8a11678.0translocase of inner mitochondrial membrane 8A1literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones | Protein import, sorting and homeostasis > Protein import and sorting
48522335Vdac37419.0voltage-dependent anion channel 3literature, yeast mito homolog+, mito protein domain+, MS/MS++MOMSignaling > Calcium homeostasis > Mitochondrial permeability transition pore | Small molecule transport
48611640Akap18165.0A kinase (PRKA) anchor protein 1literature, mito protein domain, induction, coexpression++, MS/MS+MOMSignaling > cAMP-PKA signaling
48723986Eci210455.0enoyl-Coenzyme A delta isomerase 2literature, APEX_matrix, targetP signal, mito protein domain, coexpression+, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation
48868017Mrm229960.0mitochondrial rRNA methyltransferase 2literature, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
48967164Lipt2387787.0lipoyl(octanoyl) transferase 2 (putative)yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Lipid metabolism > Lipoate insertion
49076826Nubpl80224.0nucleotide binding protein-likeliterature, targetP signal, Rickettsial homolog, mito protein domain, coexpression+, MS/MS+MatrixOXPHOS > Complex I > CI assembly factors | Metabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Metals and cofactors > Fe-S-containing proteins | OXPHOS > OXPHOS assembly factors
49114057Sfxn194081.0sideroflexin 1literature, yeast mito homolog, mito protein domain+, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > Serine metabolism | Metabolism > Vitamin metabolism > Folate and 1-C metabolism | Small molecule transport > Sideroflexins
492109108Slc30a910463.0solute carrier family 30 (zinc transporter), member 9APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, induction, MS/MSMIMSmall molecule transport
49367092Gatm2628.0glycine amidinotransferase (L-arginine:glycine amidinotransferase)literature, targetP signal, mito protein domain+, MS/MS++MatrixMetabolism > Nucleotide metabolism > Creatine metabolism
49469076Triap151499.0TP53 regulated inhibitor of apoptosis 1literature, yeast mito homolog++, mito protein domain, induction, MS/MS++IMSMetabolism > Lipid metabolism > Cardiolipin synthesis | Metabolism > Lipid metabolism > Phospholipid metabolism
49512892Cpox1371.0coproporphyrinogen oxidaseliterature, APEX_IMS, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MIMMetabolism > Metals and cofactors > Heme synthesis and processing
496321003Xpnpep363929.0X-prolyl aminopeptidase 3, mitochondrialliterature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression, MS/MS+MatrixProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage | Protein import, sorting and homeostasis > Protein homeostasis > Proteases
49767452Pnpla850640.0patatin-like phospholipase domain containing 8APEX_matrix, Rickettsial homolog, induction, coexpression++, MS/MS+MIMMetabolism > Lipid metabolism > Cardiolipin synthesis | Metabolism > Lipid metabolism > Phospholipid metabolism
498102060Gadd45gip190480.0growth arrest and DNA-damage-inducible, gamma interacting protein 1APEX_matrix, GFP, targetP signal+, coexpression+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
49911692Gfer2671.0growth factor, augmenter of liver regenerationliterature, GFP, targetP signal, yeast mito homolog++, mito protein domain, coexpression, MS/MSIMSProtein import, sorting and homeostasis > Protein import and sorting > MIA40
50083485Ngrn51335.0neugrin, neurite outgrowth associatedAPEX_matrix, targetP signal, yeast mito homolog++, mito protein domain+, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
50167840Mrpl5778988.0mitochondrial ribosomal protein L57literature, APEX_matrix, targetP signal, mito protein domain+, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
50266091Ndufa34696.0NADH:ubiquinone oxidoreductase subunit A3literature, induction, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
50369956Ptcd355037.0pentatricopeptide repeat domain 3literature, APEX_matrix, targetP signal+, mito protein domain+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
50467036Mrpl4584311.0mitochondrial ribosomal protein L45literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
50573132Slc25a168034.0solute carrier family 25 (mitochondrial carrier, Graves disease autoantigen), member 16literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MSMIMSmall molecule transport > SLC25A family
50622227Ucp17350.0uncoupling protein 1 (mitochondrial, proton carrier)literature, yeast mito homolog+, mito protein domain+, coexpression, MS/MSMIMSmall molecule transport > SLC25A family
50771807Tars280222.0threonyl-tRNA synthetase 2, mitochondrial (putative)APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
50866966Trit154802.0tRNA isopentenyltransferase 1literature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications | Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
50970316Ndufab14706.0NADH:ubiquinone oxidoreductase subunit AB1literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS+MIMOXPHOS > Complex I > CI subunits | Metabolism > Lipid metabolism > Type II fatty acid synthesis | Metabolism > Metals and cofactors > Fe-S cluster biosynthesis | OXPHOS > OXPHOS subunits
51071832Cslcitrate synthase liketargetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MS++Matrix0
51168066Slc25a3951629.0solute carrier family 25, member 39literature, yeast mito homolog+, mito protein domain+, induction, coexpressionMIMSmall molecule transport > SLC25A family
51266390Prelid3b51012.0PRELI domain containing 3BGFP, yeast mito homolog+, mito protein domain+, induction, coexpressionIMSMetabolism > Lipid metabolism > Phospholipid metabolism
51356462Mtch123787.0mitochondrial carrier 1literature, yeast mito homolog+, mito protein domain+, MS/MS++MOMSmall molecule transport > SLC25A family
51466839Dele19812.0DAP3 binding cell death enhancer 1targetP signal+, yeast mito homolog, mito protein domain, induction, coexpressionMIMSignaling
515113868Acaa1aacetyl-Coenzyme A acyltransferase 1AtargetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionMatrixMetabolism > Lipid metabolism > Fatty acid oxidation
51666834Acot1355856.0acyl-CoA thioesterase 13mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism
51767184Ndufa1351079.0NADH:ubiquinone oxidoreductase subunit A13literature, APEX_IMS, mito protein domain, coexpression++, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
518268782Agxt264902.0alanine-glyoxylate aminotransferase 2literature, targetP signal, yeast mito homolog++, mito protein domain, MS/MS+MatrixMetabolism > Amino acid metabolism > Glyoxylate metabolism
519223776Selenoo83642.0selenoprotein OtargetP signal+, yeast mito homolog, mito protein domain+, coexpressionMatrixMetabolism > Detoxification > Selenoproteins
52066431Oxld1339229.0oxidoreductase like domain containing 1targetP signal, yeast mito homolog, mito protein domain+, coexpression+unknown0
521170731Mfn29927.0mitofusin 2literature, mito protein domain+, induction, coexpression, MS/MS+MOMMitochondrial dynamics and surveillance > Fusion | Mitochondrial dynamics and surveillance > Organelle contact sites
522218865Chdh55349.0choline dehydrogenaseAPEX_matrix, targetP signal+, mito protein domain, coexpression, MS/MS++MIMMetabolism > Amino acid metabolism > Glycine metabolism | Metabolism > Vitamin metabolism > Choline and betaine metabolism | Metabolism > Vitamin metabolism > Folate and 1-C metabolism | Metabolism > Electron carriers > Q-linked reactions, other
523110265Msra4482.0methionine sulfoxide reductase AtargetP signal+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism | Metabolism > Sulfur metabolism
52427045Nit14817.0nitrilase 1APEX_matrix, targetP signal+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism
52584682Cox4i284701.0cytochrome c oxidase subunit 4I2literature, targetP signal, yeast mito homolog++, mito protein domain+MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
52680907Lactb114294.0lactamase, betaliterature, APEX_IMS, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++IMSProtein import, sorting and homeostasis > Protein homeostasis > Proteases | Metabolism > Lipid metabolism > Phospholipid metabolism
52722117Tst7263.0thiosulfate sulfurtransferase, mitochondrialliterature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolism | Metabolism > Sulfur metabolism
52868020Coa884334.0cytochrome c oxidase assembly factor 8literature, targetP signal+, mito protein domain+, coexpression+MIMOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
52956189Prodh258510.0proline dehydrogenase (oxidase) 2targetP signal, yeast mito homolog+, mito protein domain+, MS/MS+MIMMetabolism > Amino acid metabolism > Glyoxylate metabolism | Metabolism > Electron carriers > Q-linked reactions, other
53066142Cox7b1349.0cytochrome c oxidase subunit 7Bliterature, targetP signal, mito protein domain+, induction, MS/MS+MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
53169367Glrx251022.0glutaredoxin 2 (thioltransferase)literature, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > Fe-S-containing proteins | Metabolism > Vitamin metabolism > Vitamin C metabolism | Metabolism > Detoxification > ROS and glutathione metabolism
53272535Aldh1b1219.0aldehyde dehydrogenase 1 family, member B1literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolism
53366495Ndufb34709.0NADH:ubiquinone oxidoreductase subunit B3literature, APEX_IMS, APEX_matrix, mito protein domain+, coexpression+, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
53474147Ehhadh1962.0enoyl-Coenzyme A, hydratase/3-hydroxyacyl Coenzyme A dehydrogenaseyeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS+unknownMetabolism > Lipid metabolism
53552665Echdc155862.0enoyl Coenzyme A hydratase domain containing 1yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MS+unknownMetabolism > Lipid metabolism
53672026Trmu55687.0tRNA 5-methylaminomethyl-2-thiouridylate methyltransferaseliterature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
53768915Vars257176.0valyl-tRNA synthetase 2, mitochondrialAPEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
53852535Mettl1764745.0methyltransferase like 17GFP, targetP signal+, yeast mito homolog++, mito protein domain+MatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
53930956Aass10157.0aminoadipate-semialdehyde synthaseAPEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Lysine metabolism
54023923Aadat51166.0aminoadipate aminotransferasetargetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Lysine metabolism
54169875Ndufa11126328.0NADH:ubiquinone oxidoreductase subunit A11literature, APEX_IMS, mito protein domain+, induction, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
542245347Gm4984347411.0predicted pseudogene 4984yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Carbohydrate metabolism > Gluconeogenesis | Metabolism > Carbohydrate metabolism > Pyruvate metabolism | Metabolism > Carbohydrate metabolism > TCA-associated | Small molecule transport
543217593Slc25a2189874.0solute carrier family 25 (mitochondrial oxodicarboxylate carrier), member 21literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Amino acid metabolism | Small molecule transport > SLC25A family
544214663Slc25a29123096.0solute carrier family 25 (mitochondrial carrier, palmitoylcarnitine transporter), member 29literature, yeast mito homolog+, mito protein domain+, MS/MS++MIMMetabolism > Amino acid metabolism > Lysine metabolism | Small molecule transport > SLC25A family
54517768Mthfd210797.0methylenetetrahydrofolate dehydrogenase (NAD+ dependent), methenyltetrahydrofolate cyclohydrolaseliterature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolism
54677697Mmab326625.0methylmalonic aciduria (cobalamin deficiency) cblB type homolog (human)APEX_matrix, GFP, targetP signal+, coexpression, MS/MS++MatrixMetabolism > Vitamin metabolism > Vitamin B12 metabolism
54715488Hsd17b43295.0hydroxysteroid (17-beta) dehydrogenase 4Rickettsial homolog, mito protein domain+, induction, coexpressionunknownMetabolism > Lipid metabolism
54818115Nnt23530.0nicotinamide nucleotide transhydrogenaseliterature, APEX_matrix, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MS+MIMMetabolism > Metals and cofactors > NAD biosynthesis and metabolism
549216821Tmem118834.0transmembrane protein 11GFP, targetP signal, mito protein domain+, induction, coexpression, MS/MSMIMMitochondrial dynamics and surveillance
55067390Mrm355178.0mitochondrial rRNA methyltransferase 3APEX_matrix, GFP, targetP signal, mito protein domain+, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
55115473Rida10247.0reactive intermediate imine deaminase A homologAPEX_matrix, yeast mito homolog++, mito protein domain, coexpression, MS/MS+Matrix0
55212862Cox6a21339.0cytochrome c oxidase subunit 6A2literature, yeast mito homolog+, mito protein domain+, induction, coexpressionMIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
553100126824Sco29997.0SCO2 cytochrome c oxidase assembly proteinliterature, APEX_IMS, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors | Metabolism > Metals and cofactors > Copper metabolism | OXPHOS > OXPHOS assembly factors
554231430Cox18285521.0cytochrome c oxidase assembly protein 18literature, targetP signal+, yeast mito homolog++, mito protein domain, coexpressionMIMOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
55568133Gcsh2653.0glycine cleavage system protein H (aminomethyl carrier)literature, APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain+, MS/MSMatrixMetabolism > Lipid metabolism > Lipoate insertion | Metabolism > Amino acid metabolism > Glycine metabolism | Metabolism > Amino acid metabolism > Glycine cleavage system
55674129Dmgdh29958.0dimethylglycine dehydrogenase precursorliterature, targetP signal+, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Glycine metabolism | Metabolism > Vitamin metabolism > Choline and betaine metabolism | Metabolism > Vitamin metabolism > Folate and 1-C metabolism
557108841Rdh13112724.0retinol dehydrogenase 13 (all-trans and 9-cis)yeast mito homolog+, Rickettsial homolog, mito protein domain, induction, MS/MSMIMMetabolism > Vitamin metabolism > Vitamin A metabolism
558108755Lyrm257226.0LYR motif containing 2APEX_matrix, GFP, targetP signal+, mito protein domain+, coexpression, MS/MSMatrixOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
55954683Prdx525824.0peroxiredoxin 5literature, APEX_matrix, targetP signal, mito protein domain, induction, MS/MS++MatrixMetabolism > Detoxification > ROS and glutathione metabolism
56068115Maip179568.0matrix AAA peptidase interacting protein 1GFP, targetP signal, induction, coexpression, MS/MS+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperones
56114874Gstz12954.0glutathione transferase zeta 1 (maleylacetoacetate isomerase)APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolism
562226153Twnk56652.0twinkle mtDNA helicaseliterature, APEX_matrix, targetP signal+, Rickettsial homolog, induction, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication | Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid
56368550Tefm79736.0transcription elongation factor, mitochondrialAPEX_matrix, targetP signal, induction, coexpression++, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > Transcription
56452469Coa328958.0cytochrome C oxidase assembly factor 3APEX_IMS, APEX_matrix, mito protein domain+, coexpression, MS/MS++MIMMitochondrial central dogma > Translation > Translation factors | OXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
56576137Mcur163933.0mitochondrial calcium uniporter regulator 1APEX_matrix, yeast mito homolog+, mito protein domain+, induction, MS/MSMIM0
56674551Pck25106.0phosphoenolpyruvate carboxykinase 2 (mitochondrial)literature, targetP signal+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Gluconeogenesis | Metabolism > Carbohydrate metabolism > TCA-associated
56715356Hmgcl3155.03-hydroxy-3-methylglutaryl-Coenzyme A lyaseliterature, APEX_matrix, targetP signal+, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolism | Metabolism > Amino acid metabolism > Branched-chain amino acid metabolism
568213012Abhd1055347.0abhydrolase domain containing 10literature, APEX_IMS, APEX_matrix, targetP signal+, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Detoxification > Xenobiotic metabolism
569214489BC003965283951.0cDNA sequence BC003965APEX_IMS, targetP signal+, induction, coexpression, MS/MSIMS0
570171210Acot210965.0acyl-CoA thioesterase 2literature, targetP signal, mito protein domain, induction, coexpression, MS/MS++MatrixMetabolism > Lipid metabolism
57111656Alas2212.0aminolevulinic acid synthase 2, erythroidliterature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain+, coexpressionMatrixMetabolism > Metals and cofactors > Heme synthesis and processing
57220216Acsm36296.0acyl-CoA synthetase medium-chain family member 3literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation
57367067Romo1140823.0reactive oxygen species modulator 1literature, APEX_IMS, yeast mito homolog++, mito protein domain+, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathway | Small molecule transport
57427393Mrpl3954148.0mitochondrial ribosomal protein L39literature, APEX_matrix, targetP signal, Rickettsial homolog, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
575214952Rhot289941.0ras homolog family member T2literature, yeast mito homolog, mito protein domain+, induction, coexpressionMOMSignaling > Calcium homeostasis > EF hand proteins | Mitochondrial dynamics and surveillance > Trafficking
57656295Higd1a25994.0HIG1 domain family, member 1Aliterature, APEX_IMS, mito protein domain+, induction, MS/MS++MIMOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors | OXPHOS > Respirasome assembly
57721379Tbrg49238.0transforming growth factor beta regulated gene 4literature, APEX_matrix, targetP signal+, coexpression, MS/MS++MatrixMitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing | Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
57868316Apoo79135.0apolipoprotein Oliterature, APEX_IMS, targetP signal, mito protein domain+, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complex
579381511Pdp154704.0pyruvate dehyrogenase phosphatase catalytic subunit 1literature, APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, MS/MS++MIMMetabolism > Carbohydrate metabolism > Pyruvate metabolism
58066148Dnajc1529103.0DnaJ heat shock protein family (Hsp40) member C15GFP, yeast mito homolog, mito protein domain, induction, coexpression, MS/MS+MIMProtein import, sorting and homeostasis > Protein import and sorting > Import motor
58112036Bcat2587.0branched chain aminotransferase 2, mitochondrialliterature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Branched-chain amino acid metabolism
58219299Abcd35825.0ATP-binding cassette, sub-family D (ALD), member 3GFP, targetP signal, Rickettsial homolog, mito protein domain, induction, coexpressionMembraneSmall molecule transport > ABC transporters
583227231Cps11373.0carbamoyl-phosphate synthetase 1literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Urea cycle
58470257Atp5mpl9556.0ATP synthase membrane subunit 6.8PLinduction, coexpression++, MS/MS+MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
58518242Oat4942.0ornithine aminotransferaseliterature, APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Proline metabolism
58656185Hao251179.0hydroxyacid oxidase 2yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MSunknownMetabolism > Lipid metabolism
58771776Tha1threonine aldolase 1targetP signal+, mito protein domain+, MS/MS+Matrix0
588231086Hadhb3032.0hydroxyacyl-CoA dehydrogenase trifunctional multienzyme complex subunit betaliterature, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++MIMMetabolism > Carbohydrate metabolism > Ketone metabolism | Metabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Amino acid metabolism > Lysine metabolism
589105014Rdh1457665.0retinol dehydrogenase 14 (all-trans and 9-cis)yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MSMembraneMetabolism > Vitamin metabolism > Vitamin A metabolism
590320720Fastkd179675.0FAST kinase domains 1APEX_matrix, targetP signal, induction, coexpression++MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing | Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
59156078Car5b11238.0carbonic anhydrase 5b, mitochondrialliterature, targetP signal, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Urea cycle
59217714Grpel2134266.0GrpE-like 2, mitochondrialliterature, APEX_matrix, targetP signal+, yeast mito homolog, Rickettsial homolog, mito protein domain+MatrixProtein import, sorting and homeostasis > Protein import and sorting > Import motor | Metabolism > Metals and cofactors > Fe-S cluster biosynthesis
59366258Mrps1751373.0mitochondrial ribosomal protein S17literature, targetP signal, mito protein domain, induction, coexpression, MS/MS+MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
594623661Lipt151601.0lipoyltransferase 1GFP, targetP signal, yeast mito homolog++, mito protein domain, coexpressionMatrixMetabolism > Lipid metabolism > Lipoate insertion
595229517Slc25a449673.0solute carrier family 25, member 44yeast mito homolog+, mito protein domain+, induction, MS/MSMIMMetabolism > Amino acid metabolism > Branched-chain amino acid metabolism | Small molecule transport > SLC25A family
596110074Dut1854.0deoxyuridine triphosphataseliterature, targetP signal+, Rickettsial homolog, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
59793757Immp2l83943.0IMP2 inner mitochondrial membrane peptidase-like (S. cerevisiae)literature, yeast mito homolog++, mito protein domain, coexpression, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage | Protein import, sorting and homeostasis > Protein homeostasis > Proteases
59868033Cox1990639.0cytochrome c oxidase assembly protein 19yeast mito homolog, mito protein domain, induction, coexpression+, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors | Metabolism > Metals and cofactors > Copper metabolism | OXPHOS > OXPHOS assembly factors
599216188Aldh1l2160428.0aldehyde dehydrogenase 1 family, member L2literature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolism
60014004Chchd251142.0coiled-coil-helix-coiled-coil-helix domain containing 2APEX_IMS, targetP signal+, yeast mito homolog+, mito protein domain, coexpressionIMSMitochondrial dynamics and surveillance > Apoptosis
601320951Pisd23761.0phosphatidylserine decarboxylasetargetP signal, yeast mito homolog++, mito protein domain, MS/MSMIMMetabolism > Lipid metabolism > Phospholipid metabolism
60274114Crot54677.0carnitine O-octanoyltransferaseyeast mito homolog+, mito protein domain, induction, coexpression, MS/MSunknownMetabolism > Lipid metabolism > Fatty acid oxidation
60356412Noa184273.0nitric oxide associated 1literature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpressionMIMMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
604208501Ndufaf8284184.0NADH:ubiquinone oxidoreductase complex assembly factor 8targetP signal, induction, coexpression+, MS/MSIMSOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
605235674Acaa1b30.0acetyl-Coenzyme A acyltransferase 1BtargetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Lipid metabolism
606108853Mtrf1l54516.0mitochondrial translational release factor 1-likeliterature, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translation > Translation factors
60768876Atp2391419.0ATP23 metallopeptidase and ATP synthase assembly factor homologyeast mito homolog++, mito protein domain+, coexpressionIMSProtein import, sorting and homeostasis > Protein homeostasis > Proteases
60827377Yme1l110730.0YME1-like 1 (S. cerevisiae)literature, APEX_IMS, yeast mito homolog, Rickettsial homolog, mito protein domain+, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteases
609214932Hdhd527440.0haloacid dehalogenase like hydrolase domain containing 5APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, MS/MS++Matrix0
610110695Aldh7a1501.0aldehyde dehydrogenase family 7, member A1literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Lysine metabolism | Metabolism > Amino acid metabolism > Glycine metabolism | Metabolism > Vitamin metabolism > Choline and betaine metabolism | Metabolism > Vitamin metabolism > Folate and 1-C metabolism | Metabolism > Detoxification > ROS and glutathione metabolism
61166433Chchd779145.0coiled-coil-helix-coiled-coil-helix domain containing 7yeast mito homolog, induction, coexpression, MS/MS+IMSMetabolism > Metals and cofactors > Copper metabolism
612319518Pdpr55066.0pyruvate dehydrogenase phosphatase regulatory subunitAPEX_matrix, targetP signal+, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolism
61375805Nln57486.0neurolysin (metallopeptidase M3 family)literature, APEX_matrix, targetP signal+, yeast mito homolog, mito protein domain, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteases
61475597Ndufaf291942.0NADH:ubiquinone oxidoreductase complex assembly factor 2literature, APEX_matrix, targetP signal, induction, coexpression, MS/MS++MIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
61575619Fastkd222868.0FAST kinase domains 2literature, APEX_matrix, targetP signal+, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing | Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
61668087Dcakd79877.0dephospho-CoA kinase domain containingGFP, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMembrane0
617654795Sdr39u156948.0short chain dehydrogenase/reductase family 39U, member 1targetP signal, mito protein domain, coexpression, MS/MS++unknown0
618353172Gars2617.0glycyl-tRNA synthetasetargetP signal+, yeast mito homolog, mito protein domain, inductionMatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
61966594Uqcr1110975.0ubiquinol-cytochrome c reductase, complex III subunit XIliterature, targetP signal, mito protein domain+, MS/MS++MIMOXPHOS > Complex III > CIII subunits | OXPHOS > OXPHOS subunits
62067417Ears2124454.0glutamyl-tRNA synthetase 2, mitochondrialliterature, APEX_matrix, GFP, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
621333182Cox6b2125965.0cytochrome c oxidase subunit 6B2literature, yeast mito homolog+, mito protein domain+, MS/MS+MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
62214356Timm10b26515.0translocase of inner mitochondrial membrane 10Bliterature, APEX_IMS, yeast mito homolog+, mito protein domain+, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Chaperones | Protein import, sorting and homeostasis > Protein import and sorting
623230649Atpaf164756.0ATP synthase mitochondrial F1 complex assembly factor 1literature, APEX_matrix, yeast mito homolog++, mito protein domain+, MS/MSMatrixOXPHOS > Complex V > CV assembly factors | OXPHOS > OXPHOS assembly factors
62494280Sfxn381855.0sideroflexin 3yeast mito homolog, mito protein domain+, MS/MS++MIMMetabolism > Amino acid metabolism > Serine metabolism | Metabolism > Vitamin metabolism > Folate and 1-C metabolism | Small molecule transport > Sideroflexins
62526874Abcd2225.0ATP-binding cassette, sub-family D (ALD), member 2targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MS+MembraneSmall molecule transport > ABC transporters
62659010Sqor58472.0sulfide quinone oxidoreductaseliterature, targetP signal+, mito protein domain, MS/MS++MIMMetabolism > Electron carriers > Q-linked reactions, other | Metabolism > Sulfur metabolism
62768346Sirt523408.0sirtuin 5literature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolism
62867725Nudt1325961.0nudix (nucleoside diphosphate linked moiety X)-type motif 13GFP, targetP signal, mito protein domain, induction, coexpression, MS/MSMatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolism
629102632Acad1184129.0acyl-Coenzyme A dehydrogenase family, member 11mito protein domain+, induction, coexpressionMIMMetabolism > Lipid metabolism > Fatty acid oxidation
63019044Ppox5498.0protoporphyrinogen oxidaseliterature, APEX_matrix, yeast mito homolog++, mito protein domain, coexpression, MS/MSMIMMetabolism > Metals and cofactors > Heme synthesis and processing
63198314D2hgdh728294.0D-2-hydroxyglutarate dehydrogenaseliterature, APEX_matrix, targetP signal+, yeast mito homolog++, mito protein domainMatrixMetabolism > Carbohydrate metabolism > TCA-associated
63266593Diablo56616.0diablo, IAP-binding mitochondrial proteinliterature, APEX_IMS, targetP signal+, mito protein domain+, MS/MSIMSMitochondrial dynamics and surveillance > Apoptosis
633107375Slc25a45283130.0solute carrier family 25, member 45yeast mito homolog, mito protein domain+, MS/MS++MIMSmall molecule transport > SLC25A family
63472795Ttc1954902.0tetratricopeptide repeat domain 19literature, APEX_IMS, targetP signal+, mito protein domain, induction, MS/MS+MIMOXPHOS > Complex III > CIII assembly factors | OXPHOS > OXPHOS assembly factors
63511611Agxt189.0alanine-glyoxylate aminotransferaseliterature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Amino acid metabolism > Serine metabolism | Metabolism > Amino acid metabolism > Glyoxylate metabolism
636217830Dglucy80017.0D-glutamate cyclaseliterature, APEX_matrix, targetP signal+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism
63769606Mtfmt123263.0mitochondrial methionyl-tRNA formyltransferaseliterature, APEX_matrix, targetP signal, yeast mito homolog++, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > fMet processing | Metabolism > Vitamin metabolism > Folate and 1-C metabolism
63817708mt-Co14512.0cytochrome c oxidase subunit Iliterature, APEX_IMS, yeast mito homolog++, Rickettsial homolog, mito protein domain, MS/MSMIMOXPHOS > Complex IV > CIV subunits | Metabolism > Metals and cofactors > Heme-containing proteins | OXPHOS > OXPHOS subunits
63913804Endog2021.0endonuclease Gliterature, APEX_IMS, yeast mito homolog, mito protein domain, coexpression++, MS/MSIMSMitochondrial central dogma > mtDNA maintenance > mtDNA stability and decay | Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay | Mitochondrial dynamics and surveillance > Apoptosis
64070186Fam162a26355.0family with sequence similarity 162, member AAPEX_IMS, APEX_matrix, targetP signal, induction, coexpression, MS/MS++MIM0
64157423Atp5j29551.0ATP synthase, H+ transporting, mitochondrial F0 complex, subunit F2literature, coexpression++, MS/MS++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
642216456Gls227165.0glutaminase 2 (liver, mitochondrial)targetP signal, mito protein domain+, MS/MS++MatrixMetabolism > Amino acid metabolism > Glutamate metabolism
64376916Timmdc151300.0translocase of inner mitochondrial membrane domain containing 1literature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain+, MS/MS++MIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
64414548Mrps3351650.0mitochondrial ribosomal protein S33literature, targetP signal, mito protein domain+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
64521780Tfam7019.0transcription factor A, mitochondrialliterature, APEX_matrix, targetP signal, mito protein domain, induction, MS/MS++MatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication | Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid | Mitochondrial central dogma > mtRNA metabolism > Transcription
64626940Ecsit51295.0ECSIT signalling integratorliterature, APEX_matrix, targetP signal, mito protein domain, induction, coexpression+MIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
647380836Mrs257380.0MRS2 magnesium transporterAPEX_matrix, GFP, targetP signal, yeast mito homolog++, coexpressionMIMSmall molecule transport | Signaling
64874104Abcb610058.0ATP-binding cassette, sub-family B (MDR/TAP), member 6literature, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpression, MS/MSMOMMetabolism > Metals and cofactors > Heme synthesis and processing | Small molecule transport > ABC transporters
64976824Mtfr1l56181.0mitochondrial fission regulator 1-likemito protein domain+, induction, coexpression, MS/MSunknown0
65066988Lap351056.0leucine aminopeptidase 3APEX_matrix, targetP signal, Rickettsial homolog, coexpression, MS/MS++MatrixProtein import, sorting and homeostasis > Protein homeostasis > Proteases
651264895Acsf280221.0acyl-CoA synthetase family member 2APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Lipid metabolism > Fatty acid oxidation
652108682Gpt284706.0glutamic pyruvate transaminase (alanine aminotransferase) 2APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Glutamate metabolism
65376238Grhpr9380.0glyoxylate reductase/hydroxypyruvate reductaseAPEX_matrix, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > Glyoxylate metabolism
65413830Stom2040.0stomatinyeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MSMembrane0
65567201Glod451031.0glyoxalase domain containing 4APEX_matrix, targetP signal, coexpression, MS/MS++Matrix0
65666119Tomm6100188893.0translocase of outer mitochondrial membrane 6GFP, mito protein domain+, coexpression, MS/MS+MOMProtein import, sorting and homeostasis > Protein import and sorting > TOM
65766128Mrps3692259.0mitochondrial ribosomal protein S36literature, APEX_matrix, mito protein domain+, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome | Metabolism > Carbohydrate metabolism > TCA cycle
65874868Tmem65157378.0transmembrane protein 65literature, APEX_matrix, targetP signal, coexpression, MS/MS++MIM0
65928185Tomm70a9868.0translocase of outer mitochondrial membrane 70Aliterature, yeast mito homolog+, mito protein domain, induction, coexpressionMOMProtein import, sorting and homeostasis > Protein import and sorting > TOM
66014198Fhit2272.0fragile histidine triad genetargetP signal, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
66172085Osgepl164172.0O-sialoglycoprotein endopeptidase-like 1APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
66266586Crls154675.0cardiolipin synthase 1literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMIMMetabolism > Lipid metabolism > Cardiolipin synthesis
66356738Mocs14337.0molybdenum cofactor synthesis 1APEX_matrix, targetP signal, mito protein domain+, MS/MS+MatrixMetabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteins
664107747Aldh1l110840.0aldehyde dehydrogenase 1 family, member L1APEX_matrix, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, coexpression, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolism
66554391Rfk55312.0riboflavin kinasetargetP signal, yeast mito homolog++, MS/MSMatrixMetabolism > Vitamin metabolism > Vitamin B2 metabolism
66652585Dhrs1115817.0dehydrogenase/reductase (SDR family) member 1targetP signal, Rickettsial homolog, mito protein domain, MS/MS++MIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis
66718975Polg5428.0polymerase (DNA directed), gammaliterature, APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, MS/MSMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication | Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid | Mitochondrial central dogma > mtDNA maintenance > mtDNA repair
668225655Prelid3a10650.0PRELI domain containing 3Ayeast mito homolog+, mito protein domain+, MS/MSIMSMetabolism > Lipid metabolism > Cardiolipin synthesis | Metabolism > Lipid metabolism > Phospholipid metabolism
669223262Timm8a2translocase of inner mitochondrial membrane 8A2literature, yeast mito homolog+, mito protein domain+, MS/MSIMSProtein import, sorting and homeostasis > Protein homeostasis > Chaperones | Protein import, sorting and homeostasis > Protein import and sorting
67020523Slc25a149016.0solute carrier family 25 (mitochondrial carrier, brain), member 14literature, yeast mito homolog+, mito protein domain+, MS/MSMIMMetabolism > Sulfur metabolism | Small molecule transport > SLC25A family
67159040Rhot155288.0ras homolog family member T1literature, targetP signal, yeast mito homolog, mito protein domain+, MS/MS+MOMSignaling > Calcium homeostasis > EF hand proteins | Mitochondrial dynamics and surveillance > Trafficking
67214775Gpx12876.0glutathione peroxidase 1literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Detoxification > ROS and glutathione metabolism | Metabolism > Detoxification > Selenoproteins
67367453Slc25a4691137.0solute carrier family 25, member 46yeast mito homolog+, mito protein domain+, inductionMOMSmall molecule transport > SLC25A family | Mitochondrial dynamics and surveillance > Fission | Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
67417721mt-Nd54540.0NADH dehydrogenase subunit 5literature, APEX_IMS, APEX_matrix, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
67517719mt-Nd44538.0NADH dehydrogenase subunit 4literature, APEX_IMS, APEX_matrix, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
67617717mt-Nd24536.0NADH dehydrogenase subunit 2literature, Rickettsial homolog, mito protein domain+, MS/MS+MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
67766494Prelid127166.0PRELI domain containing 1literature, APEX_IMS, GFP, targetP signal, yeast mito homolog++, mito protein domain+IMSMetabolism > Lipid metabolism > Cardiolipin synthesis | Metabolism > Lipid metabolism > Phospholipid metabolism
67877032Tstd3100130890.0thiosulfate sulfurtransferase (rhodanese)-like domain containing 3targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, induction, MS/MSunknown0
67969906Slc25a3281034.0solute carrier family 25, member 32literature, targetP signal, yeast mito homolog+, mito protein domain+MIMMetabolism > Vitamin metabolism > Vitamin B2 metabolism | Metabolism > Vitamin metabolism > Folate and 1-C metabolism | Small molecule transport > SLC25A family
680215999Mcu90550.0mitochondrial calcium uniporterliterature, GFP, targetP signal, mito protein domain+, MS/MS++MIMSignaling > Calcium homeostasis > Calcium cycle | Small molecule transport > Calcium uniporter
68118082Nipsnap18508.0nipsnap homolog 1APEX_matrix, targetP signal+, coexpression, MS/MS++MatrixMitochondrial dynamics and surveillance > Mitophagy | Mitochondrial dynamics and surveillance > Autophagy
68256361Pus180324.0pseudouridine synthase 1APEX_matrix, targetP signal, yeast mito homolog++, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
683382051Pdp257546.0pyruvate dehyrogenase phosphatase catalytic subunit 2APEX_matrix, targetP signal, yeast mito homolog+, mito protein domain, coexpressionMatrixMetabolism > Carbohydrate metabolism > Pyruvate metabolism
68418777Lypla110434.0lysophospholipase 1Rickettsial homolog, mito protein domain, coexpression, MS/MS++unknownMetabolism > Lipid metabolism | Signaling
685665563Mthfd2l441024.0methylenetetrahydrofolate dehydrogenase (NADP+ dependent) 2-likeliterature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolism
686211253Mtrf19617.0mitochondrial translational release factor 1literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translation > Translation factors
68776889Coq8b79934.0coenzyme Q8BAPEX_matrix, GFP, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMIMMetabolism > Metals and cofactors > Coenzyme Q metabolism
68869536Hemk151409.0HemK methyltransferase family member 1GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain+MatrixMitochondrial central dogma > Translation > Translation factors
689110198Akr7a58574.0aldo-keto reductase family 7, member A5 (aflatoxin aldehyde reductase)APEX_matrix, targetP signal+, coexpression, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolism | Metabolism > Detoxification > Xenobiotic metabolism
690104086Cyp27a11593.0cytochrome P450, family 27, subfamily a, polypeptide 1literature, targetP signal+, mito protein domain, MS/MS++MIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis | Metabolism > Metals and cofactors > Heme-containing proteins
69164059Oxct2a3-oxoacid CoA transferase 2AtargetP signal+, mito protein domain, MS/MS++MatrixMetabolism > Carbohydrate metabolism > Ketone metabolism
69268836Mrpl52122704.0mitochondrial ribosomal protein L52literature, APEX_matrix, targetP signal+, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
69366437Fis151024.0fission, mitochondrial 1literature, yeast mito homolog++, mito protein domain+MOMMitochondrial dynamics and surveillance > Fission
694434437Amt275.0aminomethyltransferasetargetP signal, yeast mito homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Glycine metabolism | Metabolism > Amino acid metabolism > Glycine cleavage system | Metabolism > Vitamin metabolism > Folate and 1-C metabolism
695208194Exog9941.0endo/exonuclease (5'-3'), endonuclease G-likeAPEX_IMS, targetP signal, yeast mito homolog, mito protein domain, MS/MS++MIMMitochondrial central dogma > mtDNA maintenance > mtDNA replication | Mitochondrial central dogma > mtDNA maintenance > mtDNA repair | Mitochondrial central dogma > mtDNA maintenance > mtDNA stability and decay
696246221Mpst4357.0mercaptopyruvate sulfurtransferaseAPEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++MIMMetabolism > Detoxification > Xenobiotic metabolism | Metabolism > Sulfur metabolism
697103711Pnpo55163.0pyridoxine 5'-phosphate oxidaseAPEX_matrix, targetP signal, yeast mito homolog++, coexpression, MS/MSMatrixMetabolism > Vitamin metabolism > Vitamin B6 metabolism
698234384Mpv17l284769.0MPV17 mitochondrial membrane protein-like 2GFP, targetP signal, yeast mito homolog+, mito protein domain, coexpressionMIMMitochondrial central dogma > Translation > Mitochondrial ribosome assembly
69967391Fundc265991.0FUN14 domain containing 2mito protein domain+, MS/MS++MOMMitochondrial dynamics and surveillance > Organelle contact sites | Signaling
70067681Mrpl1829074.0mitochondrial ribosomal protein L18literature, APEX_matrix, targetP signal, Rickettsial homolog, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
70167942Atp5g2517.0ATP synthase, H+ transporting, mitochondrial F0 complex, subunit C2 (subunit 9)literature, targetP signal+, yeast mito homolog+, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
70275422Mettl529081.0methyltransferase like 5Rickettsial homolog, mito protein domain+, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
703208638Slc25a3854977.0solute carrier family 25, member 38yeast mito homolog++, mito protein domain+, coexpressionMIMMetabolism > Amino acid metabolism > Glycine metabolism | Metabolism > Metals and cofactors > Heme synthesis and processing | Metabolism > Vitamin metabolism > Folate and 1-C metabolism | Small molecule transport > SLC25A family
704192287Slc25a3655186.0solute carrier family 25, member 36GFP, yeast mito homolog+, mito protein domain+, coexpressionMIMMetabolism > Nucleotide metabolism > Nucleotide import | Small molecule transport > SLC25A family
705215201Trmt2b79979.0TRM2 tRNA methyltransferase 2BGFP, targetP signal, mito protein domain+, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications | Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
706268860Abat18.04-aminobutyrate aminotransferaseliterature, APEX_matrix, targetP signal, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolism | Metabolism > Metals and cofactors > Fe-S-containing proteins
707214579Aldh5a17915.0aldhehyde dehydrogenase family 5, subfamily A1APEX_matrix, targetP signal, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > GABA metabolism
70814719Got22806.0glutamatic-oxaloacetic transaminase 2, mitochondrialliterature, APEX_IMS, APEX_matrix, targetP signal, mito protein domain, MS/MS++MIMMetabolism > Carbohydrate metabolism > Malate-aspartate shuttle | Metabolism > Amino acid metabolism > Glutamate metabolism | Metabolism > Amino acid metabolism > Glyoxylate metabolism | Metabolism > Amino acid metabolism > Kynurenine metabolism | Metabolism > Sulfur metabolism
70912716Ckmt1548596.0creatine kinase, mitochondrial 1, ubiquitousliterature, targetP signal, mito protein domain, MS/MS++MIMMetabolism > Nucleotide metabolism > Creatine metabolism
71070359Gtpbp384705.0GTP binding protein 3literature, APEX_matrix, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications | Metabolism > Vitamin metabolism > Folate and 1-C metabolism
71164384Sirt323410.0sirtuin 3literature, APEX_matrix, mito protein domain, induction, coexpression, MS/MS+MatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolism | Signaling
71277422C330018D20Rik401207.0RIKEN cDNA C330018D20 genetargetP signal, coexpression+, MS/MSMatrix0
713381038Parl55486.0presenilin associated, rhomboid-likeliterature, targetP signal, yeast mito homolog++, mito protein domain, MS/MSMIMProtein import, sorting and homeostasis > Protein homeostasis > Proteases | Mitochondrial dynamics and surveillance > Mitophagy | Mitochondrial dynamics and surveillance > Autophagy
71414533Bloc1s12647.0biogenesis of lysosomal organelles complex-1, subunit 1mito protein domain, coexpression++, MS/MSunknownSignaling
71575483Cox8c341947.0cytochrome c oxidase subunit 8Cliterature, targetP signal, mito protein domain+, MS/MSMIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
716104112Acly47.0ATP citrate lyaseAPEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionMatrixMetabolism > Carbohydrate metabolism > TCA-associated
71794282Sfxn594097.0sideroflexin 5literature, yeast mito homolog, mito protein domain+, MS/MS++MIMMetabolism > Carbohydrate metabolism > TCA-associated | Small molecule transport > Sideroflexins
718319653Slc25a4055972.0solute carrier family 25, member 40literature, yeast mito homolog+, mito protein domain+, MS/MSMIMSmall molecule transport > SLC25A family
71974011Slc25a279481.0solute carrier family 25, member 27literature, yeast mito homolog+, mito protein domain+, MS/MSMIMSmall molecule transport > SLC25A family
72066972Slc25a2379085.0solute carrier family 25 (mitochondrial carrier; phosphate carrier), member 23literature, yeast mito homolog+, mito protein domain+, MS/MSMIMMetabolism > Nucleotide metabolism > Nucleotide import | Signaling > Calcium homeostasis > EF hand proteins | Small molecule transport > SLC25A family
72122229Ucp37352.0uncoupling protein 3 (mitochondrial, proton carrier)literature, yeast mito homolog+, mito protein domain+, MS/MSMIMSmall molecule transport > SLC25A family
72264704Htra227429.0HtrA serine peptidase 2literature, APEX_IMS, targetP signal, Rickettsial homolog, mito protein domain, MS/MS+MIMProtein import, sorting and homeostasis > Protein homeostasis > Proteases | Mitochondrial dynamics and surveillance > Apoptosis
72368646Nadk2133686.0NAD kinase 2, mitochondrialAPEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolism
72417711mt-Cytb4519.0cytochrome bliterature, yeast mito homolog++, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex III > CIII subunits | Metabolism > Metals and cofactors > Heme-containing proteins | Metabolism > Electron carriers > Cytochromes | OXPHOS > OXPHOS subunits
72566170Chchd584269.0coiled-coil-helix-coiled-coil-helix domain containing 5APEX_IMS, yeast mito homolog++, coexpression, MS/MSIMS0
72657312Mrps3110240.0mitochondrial ribosomal protein S31literature, APEX_matrix, targetP signal, induction, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
72754405Ndufa14694.0NADH:ubiquinone oxidoreductase subunit A1literature, coexpression+, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
72867432Hoga1112817.04-hydroxy-2-oxoglutarate aldolase 1GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMetabolism > Amino acid metabolism > Glyoxylate metabolism
72911671Aldh3a2224.0aldehyde dehydrogenase family 3, subfamily A2targetP signal+, yeast mito homolog, mito protein domain, coexpressionMembraneMetabolism > Detoxification > ROS and glutathione metabolism
73066449Pam1651025.0presequence translocase-asssociated motor 16 homolog (S. cerevisiae)literature, APEX_matrix, targetP signal, yeast mito homolog, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Import motor
73168512Tomm5401505.0translocase of outer mitochondrial membrane 5literature, mito protein domain+, MS/MS++MOMProtein import, sorting and homeostasis > Protein import and sorting > TOM
73268194Ndufb44710.0NADH:ubiquinone oxidoreductase subunit B4literature, mito protein domain+, MS/MS++MIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
73366488Fam136a84908.0family with sequence similarity 136, member AAPEX_IMS, mito protein domain+, MS/MS++IMS0
73493734Mpv17l255027.0Mpv17 transgene, kidney disease mutant-likeyeast mito homolog+, mito protein domain, MS/MS++MIMSmall molecule transport
73514625Gykl1glycerol kinase-like 1yeast mito homolog+, mito protein domain, MS/MS++Membrane0
73612895Cpt1b1375.0carnitine palmitoyltransferase 1b, muscleliterature, yeast mito homolog+, mito protein domain, MS/MS++MOMMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Metals and cofactors > Carnitine synthesis and transport | Metabolism > Metals and cofactors > Carnitine shuttle
73767861Akr1b1057016.0aldo-keto reductase family 1, member B10 (aldose reductase)induction, coexpression, MS/MS++unknownMetabolism > Vitamin metabolism > Vitamin A metabolism | Metabolism > Detoxification > Xenobiotic metabolism
73883885Slc25a2solute carrier family 25 (mitochondrial carrier, ornithine transporter) member 2literature, yeast mito homolog++, mito protein domain+MIMMetabolism > Amino acid metabolism > Urea cycle | Small molecule transport > SLC25A family
73967062Slc25a53401612.0solute carrier family 25, member 53yeast mito homolog++, mito protein domain+MIMSmall molecule transport > SLC25A family
740403187Opa380207.0optic atrophy 3literature, targetP signal, coexpression, MS/MS++MOM0
74168636Fahd181889.0fumarylacetoacetate hydrolase domain containing 1literature, APEX_matrix, yeast mito homolog, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Carbohydrate metabolism > TCA-associated
74259038Pxmp411264.0peroxisomal membrane protein 4targetP signal, mito protein domain+, coexpressionunknown0
74365102Nif3l160491.0Ngg1 interacting factor 3-like 1 (S. pombe)APEX_matrix, targetP signal, yeast mito homolog, coexpression, MS/MS+Matrix0
744231413Grsf12926.0G-rich RNA sequence binding factor 1APEX_matrix, targetP signal, mito protein domain, induction, coexpression, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing | Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
745107227Macrod128992.0mono-ADP ribosylhydrolase 1APEX_matrix, targetP signal, coexpression, MS/MS++MatrixSignaling
746217149Cisd3284106.0CDGSH iron sulfur domain 3APEX_matrix, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Metals and cofactors > Fe-S-containing proteins
74774080Nmnat3349565.0nicotinamide nucleotide adenylyltransferase 3literature, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolism
74866387Nudt8254552.0nudix (nucleoside diphosphate linked moiety X)-type motif 8APEX_matrix, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Coenzyme A metabolism
74912359Cat847.0catalaseyeast mito homolog++, mito protein domain, coexpressionIMSMetabolism > Detoxification > ROS and glutathione metabolism
75067713Dnajc19131118.0DnaJ heat shock protein family (Hsp40) member C19literature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, MS/MS++MIMProtein import, sorting and homeostasis > Protein import and sorting > Import motor
75168626Elac260528.0elaC ribonuclease Z 2APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing
752192136Sugct79783.0succinyl-CoA glutarate-CoA transferaseAPEX_matrix, targetP signal, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Amino acid metabolism
75366847Hint3135114.0histidine triad nucleotide binding protein 3Rickettsial homolog, mito protein domain, induction, coexpression+unknown0
75485305Kars3735.0lysyl-tRNA synthetaseliterature, GFP, targetP signal+, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
755246738Dnajc2854943.0DnaJ heat shock protein family (Hsp40) member C28targetP signal, Rickettsial homolog, mito protein domain, coexpression+unknown0
75666427Cyb5b80777.0cytochrome b5 type Bliterature, mito protein domain, coexpression, MS/MS++MOMMetabolism > Metals and cofactors > Heme-containing proteins | Metabolism > Detoxification > Xenobiotic metabolism | Metabolism > Detoxification > Amidoxime reducing complex | Metabolism > Electron carriers > Cytochromes
75766401Nudt2318.0nudix (nucleoside diphosphate linked moiety X)-type motif 2mito protein domain, coexpression, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
75816922Phyh5264.0phytanoyl-CoA hydroxylasetargetP signal, induction, MS/MS++MatrixMetabolism > Lipid metabolism
75914923Guk12987.0guanylate kinase 1APEX_matrix, targetP signal, Rickettsial homolog, induction, coexpression, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
760110959Nudt19390916.0nudix (nucleoside diphosphate linked moiety X)-type motif 19APEX_matrix, targetP signal+, mito protein domain, inductionMatrixMetabolism > Metals and cofactors > Coenzyme A metabolism
76117710mt-Co34514.0cytochrome c oxidase subunit IIIliterature, yeast mito homolog++, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits
76267270Mrpl4228977.0mitochondrial ribosomal protein L42APEX_matrix, GFP, mito protein domain+, induction, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
763216820Dhrs7b25979.0dehydrogenase/reductase (SDR family) member 7BRickettsial homolog, mito protein domain, induction, coexpressionMembrane0
764103850Nt5m56953.05',3'-nucleotidase, mitochondrialliterature, targetP signal, mito protein domain, induction, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
765100039707Mthfsl10588.05, 10-methenyltetrahydrofolate synthetase-liketargetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolism
766107885Mthfs5, 10-methenyltetrahydrofolate synthetasetargetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolism
76756520Nme44833.0NME/NM23 nucleoside diphosphate kinase 4APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMIMMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
76867013Oma1115209.0OMA1 zinc metallopeptidaseAPEX_IMS, GFP, targetP signal, yeast mito homolog++, coexpressionMIMProtein import, sorting and homeostasis > Protein homeostasis > Proteases | Mitochondrial dynamics and surveillance > Fusion | Mitochondrial dynamics and surveillance > Fission
769216739Acsl623305.0acyl-CoA synthetase long-chain family member 6yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MOMMetabolism > Lipid metabolism > Fatty acid oxidation
770101122Rpusd3285367.0RNA pseudouridylate synthase domain containing 3APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
77168738Acss184532.0acyl-CoA synthetase short-chain family member 1literature, APEX_matrix, targetP signal, mito protein domain, MS/MS++MIMMetabolism > Lipid metabolism > Fatty acid oxidation
77227369Dguok1716.0deoxyguanosine kinaseliterature, APEX_matrix, targetP signal, mito protein domain, MS/MS++MatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
773230577Pars225973.0prolyl-tRNA synthetase (mitochondrial)(putative)APEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
77453415Htatip210553.0HIV-1 Tat interactive protein 2yeast mito homolog, mito protein domain+, MS/MSMembrane0
77576563Qrsl155278.0glutaminyl-tRNA synthase (glutamine-hydrolyzing)-like 1literature, APEX_matrix, GFP, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
77669225Naxd55739.0NAD(P)HX dehydrataseGFP, targetP signal, mito protein domain, MS/MS++MIMMetabolism > Metals and cofactors > NAD biosynthesis and metabolism
77766098Chchd684303.0coiled-coil-helix-coiled-coil-helix domain containing 6literature, APEX_IMS, APEX_matrix, yeast mito homolog, coexpression, MS/MS++MIMMitochondrial dynamics and surveillance > Cristae formation > MICOS complex
77872562Pcbd284105.0pterin 4 alpha carbinolamine dehydratase/dimerization cofactor of hepatocyte nuclear factor 1 alpha (TCF1) 2targetP signal+, yeast mito homolog, induction, MS/MSunknownMetabolism > Metals and cofactors > Tetrahydrobiopterin synthesis
77975986Agmat79814.0agmatine ureohydrolase (agmatinase)literature, targetP signal+, mito protein domain, MS/MS+MatrixMetabolism > Amino acid metabolism
78068514Micu2221154.0mitochondrial calcium uptake 2literature, APEX_IMS, GFP, targetP signal+, mito protein domain, MS/MS+MIMSignaling > Calcium homeostasis > Calcium cycle | Signaling > Calcium homeostasis > EF hand proteins | Small molecule transport > Calcium uniporter
78111997Akr1b7aldo-keto reductase family 1, member B7induction, coexpression, MS/MS++unknownMetabolism > Lipid metabolism > Phospholipid metabolism
78220280Scp26342.0sterol carrier protein 2, livertargetP signal, Rickettsial homolog, mito protein domain+MIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis
78319336Rab2453917.0RAB24, member RAS oncogene familyyeast mito homolog, mito protein domain, induction, coexpression, MS/MSMOMMitochondrial dynamics and surveillance > Fission | Mitochondrial dynamics and surveillance > Autophagy
78466815Mcub55013.0mitochondrial calcium uniporter dominant negative beta subunitliterature, targetP signal+, mito protein domain+MIMSignaling > Calcium homeostasis > Calcium cycle | Small molecule transport > Calcium uniporter
785226791Lyplal1127018.0lysophospholipase-like 1targetP signal, mito protein domain, MS/MS++unknownMetabolism > Lipid metabolism
78675469Spata19219938.0spermatogenesis associated 19mito protein domain+, MS/MS++unknown0
78717706mt-Atp84509.0ATP synthase F0 subunit 8literature, mito protein domain+, MS/MS++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
788106557Ldhal6b92483.0lactate dehydrogenase A-like 6BtargetP signal, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Carbohydrate metabolism
78926358Aldh1a7aldehyde dehydrogenase family 1, subfamily A7yeast mito homolog+, mito protein domain, coexpression, MS/MSunknown0
790229905Kyat356267.0kynurenine aminotransferase 3APEX_matrix, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Kynurenine metabolism | Metabolism > Metals and cofactors > NAD biosynthesis and metabolism
79171147Oxsm54995.03-oxoacyl-ACP synthase, mitochondrialliterature, APEX_matrix, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS++MatrixMetabolism > Lipid metabolism > Type II fatty acid synthesis
79217718mt-Nd34537.0NADH dehydrogenase subunit 3literature, Rickettsial homolog, mito protein domain+, MS/MSMIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
79372113Adck157143.0aarF domain containing kinase 1yeast mito homolog+, Rickettsial homolog, mito protein domain, MS/MSunknown0
79470556Slc25a3384275.0solute carrier family 25, member 33literature, yeast mito homolog+, mito protein domain+MIMMetabolism > Nucleotide metabolism > Nucleotide import | Small molecule transport > SLC25A family
79556615Mgst14257.0microsomal glutathione S-transferase 1mito protein domain, coexpression, MS/MS++MembraneMetabolism > Detoxification > Xenobiotic metabolism | Metabolism > Detoxification > ROS and glutathione metabolism
79622256Ung7374.0uracil DNA glycosylaseliterature, targetP signal, yeast mito homolog, mito protein domain, inductionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repair
79772181Nsun4387338.0NOL1/NOP2/Sun domain family, member 4APEX_matrix, targetP signal, mito protein domain, induction, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
798235043Tmem205374882.0transmembrane protein 205yeast mito homolog, mito protein domain+, coexpressionMembrane0
79913167Dbi1622.0diazepam binding inhibitortargetP signal, mito protein domain, induction, coexpressionunknownMetabolism > Lipid metabolism
80071743Coasy80347.0Coenzyme A synthaseAPEX_matrix, mito protein domain, coexpression, MS/MS++MatrixMetabolism > Metals and cofactors > Coenzyme A metabolism
80199138Stard756910.0START domain containing 7APEX_IMS, targetP signal, mito protein domain, induction, coexpression+IMSMetabolism > Lipid metabolism > Phospholipid metabolism | Small molecule transport
802270035Letm2137994.0leucine zipper-EF-hand containing transmembrane protein 2targetP signal, yeast mito homolog+, mito protein domain+MIM0
80371799Ptcd126024.0pentatricopeptide repeat domain 1targetP signal, mito protein domain+, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules
80467900Mtfp151537.0mitochondrial fission process 1literature, induction, coexpression, MS/MS+MembraneMitochondrial dynamics and surveillance > Fission
80568185Coa451287.0cytochrome c oxidase assembly factor 4yeast mito homolog++, mito protein domain, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
80613850Ephx22053.0epoxide hydrolase 2, cytoplasmicRickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Detoxification > Xenobiotic metabolism | Metabolism > Lipid metabolism
807230598Nrd14898.0nardilysin, N-arginine dibasic convertase, NRD convertase 1targetP signal, Rickettsial homolog, mito protein domain+MatrixProtein import, sorting and homeostasis > Protein homeostasis > Chaperones | Protein import, sorting and homeostasis > Protein import and sorting
808100705Acacb32.0acetyl-Coenzyme A carboxylase betayeast mito homolog, Rickettsial homolog, mito protein domain, coexpression+MOMMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Vitamin metabolism > Biotin utilizing proteins
809228607Mavs57506.0mitochondrial antiviral signaling proteinliterature, induction, coexpression+, MS/MSMOMSignaling > Immune response
81070209Tmem14355260.0transmembrane protein 143targetP signal, coexpression+, MS/MSMIM0
81167440Mtpap55149.0mitochondrial poly(A) polymeraseliterature, APEX_matrix, targetP signal+, mito protein domain, inductionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications | Mitochondrial central dogma > mtRNA metabolism > mt-mRNA modifications | Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
812257635Sdsl113675.0serine dehydratase-likeyeast mito homolog+, Rickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Amino acid metabolism > Serine metabolism
81322169Cmpk2129607.0cytidine monophosphate (UMP-CMP) kinase 2, mitochondrialliterature, targetP signal+, Rickettsial homolog, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
814235582Glyctk132158.0glycerate kinasetargetP signal, coexpression, MS/MS+MatrixMetabolism > Carbohydrate metabolism
81571989Rpusd484881.0RNA pseudouridylate synthase domain containing 4APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications | Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
81666278Smim20389203.0small integral membrane protein 20literature,targetP signal, coexpression, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
81769821Mterf4130916.0mitochondrial transcription termination factor 4APEX_matrix, targetP signal, mito protein domain+, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assembly
81872960Top1mt116447.0DNA topoisomerase 1, mitochondrialliterature, APEX_matrix, targetP signal+, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication | Mitochondrial central dogma > mtRNA metabolism > Transcription
81911847Arg2384.0arginase type IIliterature, APEX_matrix, targetP signal+, mito protein domain, MS/MSMatrixMetabolism > Amino acid metabolism
820217057Ptrh251651.0peptidyl-tRNA hydrolase 2literature, yeast mito homolog, mito protein domain, MS/MS++MOM0
82173919Lyrm157149.0LYR motif containing 1GFP, yeast mito homolog, mito protein domain+, MS/MSunknown0
822224805Aars257505.0alanyl-tRNA synthetase 2, mitochondrialliterature, APEX_matrix, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > mt-tRNA synthetases
82314081Acsl12180.0acyl-CoA synthetase long-chain family member 1yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMOMMetabolism > Lipid metabolism > Fatty acid oxidation
82466114Dnajc3084277.0DnaJ heat shock protein family (Hsp40) member C30APEX_matrix, GFP, targetP signal, Rickettsial homolog, mito protein domain, MS/MSMIM0
825192289Tmlhe55217.0trimethyllysine hydroxylase, epsilonliterature, APEX_matrix, targetP signal, yeast mito homolog, mito protein domain, MS/MSMatrixMetabolism > Metals and cofactors > Carnitine synthesis and transport
82612028Bax581.0BCL2-associated X proteinliterature, mito protein domain, coexpression, MS/MS++MOMMitochondrial dynamics and surveillance > Apoptosis
827226527Cryzl2crystallin zeta like 2targetP signal, mito protein domain, MS/MS++Matrix0
82874006Dnm1l10059.0dynamin 1-likeliterature, yeast mito homolog+, mito protein domain, inductionMOMMitochondrial dynamics and surveillance > Fission
82919301Pxmp25827.0peroxisomal membrane protein 2GFP, yeast mito homolog+, mito protein domain, inductionMIM0
83066359Cox20116228.0cytochrome c oxidase assembly protein 20literature, APEX_IMS, GFP, yeast mito homolog++, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
83166343Tmem17780775.0transmembrane protein 177targetP signal, coexpression, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
83257813Tk27084.0thymidine kinase 2, mitochondrialliterature, targetP signal+, mito protein domain, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
83372018Fundc1139341.0FUN14 domain containing 1yeast mito homolog, mito protein domain+, MS/MSMOMMitochondrial dynamics and surveillance > Mitophagy | Mitochondrial dynamics and surveillance > Autophagy
83474451Pgs19489.0phosphatidylglycerophosphate synthase 1targetP signal, yeast mito homolog++MIMMetabolism > Lipid metabolism > Cardiolipin synthesis | Metabolism > Lipid metabolism > Phospholipid metabolism
83514104Fasn2194.0fatty acid synthaseyeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionIMSMetabolism > Lipid metabolism
83612409Cbr2carbonyl reductase 2targetP signal, Rickettsial homolog, mito protein domain, MS/MS+MatrixMetabolism
837212862Chpt156994.0choline phosphotransferase 1targetP signal, mito protein domain, induction, coexpression+MIMMetabolism > Lipid metabolism > Phospholipid metabolism
83811951Atp5g1516.0ATP synthase, H+ transporting, mitochondrial F0 complex, subunit C1 (subunit 9)literature, targetP signal, yeast mito homolog+, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
83967017Fam210b116151.0family with sequence similarity 210, member BtargetP signal, yeast mito homolog, coexpression, MS/MSMIMMetabolism > Metals and cofactors > Iron homeostasis
84094279Sfxn2118980.0sideroflexin 2yeast mito homolog, mito protein domain+, coexpressionMIMSmall molecule transport > Sideroflexins
841109129Mmadhc27249.0methylmalonic aciduria (cobalamin deficiency) cblD type, with homocystinuriaAPEX_matrix, targetP signal, induction, coexpressionMatrixMetabolism > Vitamin metabolism > Vitamin B12 metabolism
84218416Otc5009.0ornithine transcarbamylaseliterature, targetP signal, mito protein domain, MS/MS+MatrixMetabolism > Amino acid metabolism > Urea cycle
84350493Txnrd17296.0thioredoxin reductase 1GFP, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpression, MS/MSunknownMetabolism > Detoxification > ROS and glutathione metabolism | Metabolism > Detoxification > Selenoproteins
84411844Arf5381.0ADP-ribosylation factor 5targetP signal, mito protein domain, coexpression, MS/MSunknown0
84514287Fpgs2356.0folylpolyglutamyl synthetaseAPEX_matrix, GFP, targetP signal, yeast mito homolog, Rickettsial homologMatrixMetabolism > Vitamin metabolism > Folate and 1-C metabolism
84652575Trmt10c54931.0tRNA methyltransferase 10C, mitochondrial RNase P subunitliterature, APEX_matrix, GFP, targetP signal+, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing | Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
84774088Them7thioesterase superfamily member 7targetP signal, mito protein domain, MS/MS+Matrix0
848212442Lactb251110.0lactamase, beta 2mito protein domain, induction, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
849228715Smim26small integral membrane protein 26induction, coexpression, MS/MSMembrane0
85072542Pgam5192111.0phosphoglycerate mutase family member 5APEX_IMS, mito protein domain, coexpression, MS/MS++MOMMitochondrial dynamics and surveillance > Mitophagy | Mitochondrial dynamics and surveillance > Autophagy
85166461Ptpmt1114971.0protein tyrosine phosphatase, mitochondrial 1literature, APEX_matrix, mito protein domain, coexpression, MS/MS++MIMMetabolism > Lipid metabolism > Cardiolipin synthesis | Metabolism > Lipid metabolism > Phospholipid metabolism
85215199Hebp150865.0heme binding protein 1APEX_IMS, mito protein domain, coexpression, MS/MS++IMS0
85311666Abcd1215.0ATP-binding cassette, sub-family D (ALD), member 1targetP signal, Rickettsial homolog, mito protein domain, inductionMembraneSmall molecule transport > ABC transporters
85472552Hsdl183693.0hydroxysteroid dehydrogenase like 1GFP, Rickettsial homolog, mito protein domain, MS/MS++unknown0
855109857Cbr3874.0carbonyl reductase 3targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MSMatrixMetabolism > Detoxification > Xenobiotic metabolism
85611758Prdx69588.0peroxiredoxin 6yeast mito homolog+, Rickettsial homolog, mito protein domainunknownMetabolism > Lipid metabolism > Phospholipid metabolism | Metabolism > Detoxification > ROS and glutathione metabolism
85757431Dnajc43338.0DnaJ heat shock protein family (Hsp40) member C4GFP, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMembraneProtein import, sorting and homeostasis > Protein homeostasis
85868554CebpzosCCAAT/enhancer binding protein (C/EBP), zeta, opposite strandcoexpression+, MS/MS+unknown0
859235169Foxred155572.0FAD-dependent oxidoreductase domain containing 1literature, targetP signal, mito protein domain, coexpression+MIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
860140546Eri379033.0exoribonuclease 3targetP signal+, mito protein domain, MS/MSMatrix0
86172831Dhx3022907.0DEAH (Asp-Glu-Ala-His) box polypeptide 30literature, targetP signal+, yeast mito homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
86294044Bcl2l1323786.0BCL2-like 13 (apoptosis facilitator)literature, mito protein domain, coexpression, MS/MS+MOMMitochondrial dynamics and surveillance > Mitophagy | Mitochondrial dynamics and surveillance > Autophagy | Mitochondrial dynamics and surveillance > Apoptosis
86366659Acp651205.0acid phosphatase 6, lysophosphatidicliterature, APEX_IMS, targetP signal, mito protein domain, MS/MS++IMSMetabolism > Lipid metabolism > Phospholipid metabolism
86420463Cox7a2l9167.0cytochrome c oxidase subunit 7A2 likeliterature, APEX_IMS, APEX_matrix, mito protein domain+, MS/MS+MIMOXPHOS > Complex IV > CIV subunits | OXPHOS > OXPHOS subunits | OXPHOS > OXPHOS assembly factors | OXPHOS > Respirasome assembly
865226654Tstd1100131187.0thiosulfate sulfurtransferase (rhodanese)-like domain containing 1targetP signal, yeast mito homolog, mito protein domain, MS/MSunknownMetabolism > Sulfur metabolism
866110391Qdpr5860.0quinoid dihydropteridine reductaseAPEX_matrix, targetP signal, mito protein domain, inductionMatrixMetabolism > Metals and cofactors > Tetrahydrobiopterin synthesis | Metabolism > Vitamin metabolism > Folate and 1-C metabolism
867233799Acsm2123876.0acyl-CoA synthetase medium-chain family member 2yeast mito homolog, Rickettsial homolog, mito protein domain, MS/MS+MatrixMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Detoxification > Xenobiotic metabolism
86857869Adck290956.0aarF domain containing kinase 2GFP, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domainMIM0
86964291Osbpl1a114876.0oxysterol binding protein-like 1ARickettsial homolog, mito protein domain, induction, MS/MSunknownMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis | Metabolism > Lipid metabolism > Phospholipid metabolism
870212528Trmt155621.0tRNA methyltransferase 1targetP signal+, yeast mito homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
87176366Mtif3219402.0mitochondrial translational initiation factor 3literature, APEX_matrix, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > Translation factors
872100503890Pet100100131801.0PET100 homologliterature, yeast mito homolog++, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
87367472Mtfr19650.0mitochondrial fission regulator 1literature, targetP signal, mito protein domain+, coexpressionMembraneMitochondrial dynamics and surveillance > Fission
874224481Tfb1m51106.0transcription factor B1, mitochondrialliterature, APEX_matrix, Rickettsial homolog, mito protein domain, MS/MS+MatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
87514319Fth12495.0ferritin heavy polypeptide 1mito protein domain, MS/MS++unknownMetabolism > Metals and cofactors > Iron homeostasis
87612257Tspo706.0translocator proteinliterature, mito protein domain, MS/MS++MOMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis
877107146Glyat10249.0glycine-N-acyltransferaseliterature, mito protein domain, coexpression, MS/MS+MatrixMetabolism > Amino acid metabolism > Glycine metabolism | Metabolism > Detoxification > Xenobiotic metabolism
87868731Rbfa79863.0ribosome binding factor AAPEX_matrix, targetP signal, Rickettsial homolog, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assembly
87919819Rnaseh1246243.0ribonuclease H1literature, APEX_matrix, targetP signal, Rickettsial homolog, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication | Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
88066690Tmem18625880.0transmembrane protein 186targetP signal, coexpression, MS/MSMIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
88118632Pex11b8799.0peroxisomal biogenesis factor 11 betatargetP signal, coexpression, MS/MSMembrane0
88253893Nudt511164.0nudix (nucleoside diphosphate linked moiety X)-type motif 5yeast mito homolog++, mito protein domain, coexpressionunknownMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
88320655Sod16647.0superoxide dismutase 1, solubleliterature, yeast mito homolog, mito protein domain, induction, coexpressionIMSMetabolism > Detoxification > ROS and glutathione metabolism
88420845Star6770.0steroidogenic acute regulatory proteinliterature, targetP signal, mito protein domain, coexpression, MS/MSMOM | IMSMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis
885207704Gtpbp1085865.0GTP-binding protein 10 (putative)APEX_matrix, yeast mito homolog+, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assembly
886380660Acss379611.0acyl-CoA synthetase short-chain family member 3targetP signal, yeast mito homolog, mito protein domain, MS/MSMatrixMetabolism > Lipid metabolism
88766658Ccdc5179714.0coiled-coil domain containing 51APEX_matrix, targetP signal, MS/MS++MIMSmall molecule transport
88856360Acot923597.0acyl-CoA thioesterase 9literature, targetP signal, MS/MS++MIMMetabolism > Lipid metabolism
88966706Ndufaf325915.0NADH:ubiquinone oxidoreductase complex assembly factor 3literature, targetP signal, mito protein domain, MS/MSMIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
890319945Flad180308.0flavin adenine dinucleotide synthetase 1APEX_matrix, mito protein domain, induction, coexpressionMatrixMetabolism > Vitamin metabolism > Vitamin B2 metabolism
891107476Acaca31.0acetyl-Coenzyme A carboxylase alphayeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMatrixMetabolism > Lipid metabolism > Type II fatty acid synthesis | Metabolism > Vitamin metabolism > Biotin utilizing proteins
89298256Kmo8564.0kynurenine 3-monooxygenase (kynurenine 3-hydroxylase)yeast mito homolog, mito protein domain, MS/MS++MOMMetabolism > Amino acid metabolism > Kynurenine metabolism | Metabolism > Metals and cofactors > NAD biosynthesis and metabolism
89366410Mterf351001.0mitochondrial transcription termination factor 3literature, APEX_matrix, GFP, targetP signal, mito protein domain+, coexpressionMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assembly
894170719Oxr155074.0oxidation resistance 1literature, yeast mito homolog+, mito protein domain, MS/MSMOMMetabolism > Detoxification > ROS and glutathione metabolism
89574167Nudt953343.0nudix (nucleoside diphosphate linked moiety X)-type motif 9APEX_matrix, targetP signal, mito protein domain, coexpression, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
896208967Thnsl179896.0threonine synthase-like 1 (bacterial)APEX_matrix, mito protein domain, MS/MS++Matrix0
89769051Pycr229920.0pyrroline-5-carboxylate reductase family, member 2APEX_matrix, mito protein domain, MS/MS++MatrixMetabolism > Amino acid metabolism > Proline metabolism
89815254Hint13094.0histidine triad nucleotide binding protein 1Rickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
899384071Slc25a34284723.0solute carrier family 25, member 34yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A family
900328258Slc25a48153328.0solute carrier family 25, member 48yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A family
901246696Slc25a2881894.0solute carrier family 25, member 28literature, yeast mito homolog+, mito protein domain+MIMMetabolism > Metals and cofactors > Iron homeostasis | Small molecule transport > SLC25A family
902194744Slc25a43203427.0solute carrier family 25, member 43yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A family
903104910Slc25a47283600.0solute carrier family 25, member 47literature, yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A family
904103775Slc25a41284427.0solute carrier family 25, member 41yeast mito homolog+, mito protein domain+MIMMetabolism > Nucleotide metabolism > Nucleotide import | Small molecule transport > SLC25A family
90574686Slc25a54solute carrier family 25, member 54yeast mito homolog+, mito protein domain+MembraneSmall molecule transport > SLC25A family
90667712Slc25a3751312.0solute carrier family 25, member 37literature, yeast mito homolog+, mito protein domain+MIMMetabolism > Metals and cofactors > Iron homeostasis | Small molecule transport > SLC25A family
90722228Ucp27351.0uncoupling protein 2 (mitochondrial, proton carrier)literature, yeast mito homolog+, mito protein domain+MIMSmall molecule transport > SLC25A family
908216119Ybey54059.0ybeY metallopeptidaseAPEX_matrix, targetP signal, Rickettsial homolog, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
90918294Ogg14968.08-oxoguanine DNA-glycosylase 1literature, targetP signal+, yeast mito homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repair
910240549Gm4952predicted gene 4952mito protein domain, MS/MS++unknownMetabolism
91114080Fabp12168.0fatty acid binding protein 1, livermito protein domain, MS/MS++unknownMetabolism > Metals and cofactors > Heme synthesis and processing | Metabolism > Lipid metabolism
91276894Mettl15196074.0methyltransferase like 15APEX_matrix, targetP signal, Rickettsial homolog, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
91366559Metap1d254042.0methionyl aminopeptidase type 1D (mitochondrial)literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > Translation > fMet processing | Protein import, sorting and homeostasis > Protein homeostasis > Proteases
91416832Ldhb3945.0lactate dehydrogenase BRickettsial homolog, mito protein domain, inductionunknownMetabolism > Amino acid metabolism > Glyoxylate metabolism
91566274Lyrm9201229.0LYR motif containing 9mito protein domain+, MS/MSunknown0
91666112Mtarc164757.0mitochondrial amidoxime reducing component 1mito protein domain+, MS/MSMOMMetabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteins | Metabolism > Detoxification > Xenobiotic metabolism | Metabolism > Detoxification > Amidoxime reducing complex
91779456Recql49401.0RecQ protein-like 4targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repair
918114863Plpbp11212.0pyridoxal phosphate binding proteinAPEX_matrix, targetP signal, coexpression, MS/MS++MatrixMetabolism > Vitamin metabolism > Vitamin B6 metabolism
91968350Mul179594.0mitochondrial ubiquitin ligase activator of NFKB 1literature, mito protein domain+, inductionMOMProtein import, sorting and homeostasis > Protein homeostasis | Mitochondrial dynamics and surveillance > Fission | Signaling
920229228Nudt611162.0nudix (nucleoside diphosphate linked moiety X)-type motif 6APEX_matrix, targetP signal, mito protein domain, coexpressionMatrix0
92168943Pink165018.0PTEN induced putative kinase 1literature, targetP signal, mito protein domain, coexpressionMOMMitochondrial dynamics and surveillance > Mitophagy | Mitochondrial dynamics and surveillance > Autophagy | Signaling
922230895Vps13d55187.0vacuolar protein sorting 13Dmanual, yeast mito homolog, mito protein domain, induction, coexpressionMOMMitochondrial dynamics and surveillance > Mitophagy | Mitochondrial dynamics and surveillance > Autophagy
92366349Dmac255101.0distal membrane arm assembly complex 2APEX_matrix, GFP, targetP signal, induction, MS/MSMIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
924216001Micu110367.0mitochondrial calcium uptake 1literature, APEX_IMS, GFP, targetP signal, mito protein domain, MS/MS+MIMSignaling > Calcium homeostasis > Calcium cycle | Signaling > Calcium homeostasis > EF hand proteins | Small molecule transport > Calcium uniporter
925103466Nt5dc351559.05'-nucleotidase domain containing 3APEX_matrix, targetP signal, MS/MS++Matrix0
92673398Nipsnap3a25934.0nipsnap homolog 3AAPEX_matrix, targetP signal, MS/MS++Matrix0
92721975Top3a7156.0topoisomerase (DNA) III alphaAPEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication
92817117Amacr23600.0alpha-methylacyl-CoA racemaseliterature, mito protein domain, coexpression, MS/MSMatrixMetabolism > Lipid metabolism > Fatty acid oxidation
92976357Trmt557570.0TRM5 tRNA methyltransferase 5literature,targetP signal, yeast mito homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
93078506Micu3286097.0mitochondrial calcium uptake family, member 3manual, targetP signal, mito protein domain, MS/MSMIMSignaling > Calcium homeostasis > Calcium cycle | Signaling > Calcium homeostasis > EF hand proteins | Small molecule transport > Calcium uniporter
93156695Pnkd25953.0paroxysmal nonkinesiogenic dyskinesialiterature,targetP signal, mito protein domain, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
93212352Car5a763.0carbonic anhydrase 5a, mitochondrialliterature, targetP signal, mito protein domain, MS/MSMatrixMetabolism > Amino acid metabolism > Urea cycle
93318207Nthl14913.0nth (endonuclease III)-like 1 (E.coli)literature, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domainunknownMetabolism > Metals and cofactors > Fe-S-containing proteins
93456327Arl2402.0ADP-ribosylation factor-like 2literature, mito protein domain, coexpression, MS/MS+IMSMitochondrial dynamics and surveillance > Fusion
93524071Synj2bp55333.0synaptojanin 2 binding proteinAPEX_IMS, mito protein domain, coexpression, MS/MS+MOMMitochondrial dynamics and surveillance > Organelle contact sites
936228019Mettl879828.0methyltransferase like 8APEX_matrix, targetP signal, mito protein domain+MatrixMitochondrial central dogma > mtRNA metabolism
937208595Mterf1b7978.0mitochondrial transcription termination factor 1bliterature, APEX_matrix, targetP signal, mito protein domain+MatrixMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid | Mitochondrial central dogma > mtRNA metabolism > Transcription
938237926Rsad155316.0radical S-adenosyl methionine domain containing 1APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMIMMetabolism > Metals and cofactors > Fe-S-containing proteins
939110196Fdps2224.0farnesyl diphosphate synthetaseRickettsial homolog, mito protein domain, MS/MS+MIMMetabolism > Lipid metabolism > Cholesterol-associated
94068095Ociad154940.0OCIA domain containing 1APEX_IMS, GFP, MS/MS++MOM0
94166587Fastk10922.0Fas-activated serine/threonine kinaseGFP, targetP signal, induction, coexpressionMIMMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing | Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
942233801Acsm4341392.0acyl-CoA synthetase medium-chain family member 4manual, targetP signal, yeast mito homolog, Rickettsial homolog, mito protein domainMatrixMetabolism > Lipid metabolism > Fatty acid oxidation
94354369Nme610201.0NME/NM23 nucleoside diphosphate kinase 6literature, APEX_matrix, GFP, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
944229709Ahcyl110768.0S-adenosylhomocysteine hydrolase-like 1mito protein domain+, inductionMOMMitochondrial dynamics and surveillance > Organelle contact sites
94566291Smim857150.0small integral membrane protein 8manual, induction, coexpression, MS/MSMOM0
946319554Idi13422.0isopentenyl-diphosphate delta isomerasetargetP signal, mito protein domain, MS/MS+MatrixMetabolism > Lipid metabolism > Cholesterol-associated
947382793Mtx3345778.0metaxin 3manual, mito protein domain+, MS/MSMOMMitochondrial dynamics and surveillance > Intramitochondrial membrane interactions
94868472Tmem126b55863.0transmembrane protein 126Bmito protein domain+, MS/MSMIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
94912176Bnip3664.0BCL2/adenovirus E1B interacting protein 3literature, mito protein domain+, MS/MSMOMMitochondrial dynamics and surveillance > Apoptosis
95014232Fkbp823770.0FK506 binding protein 8literature, yeast mito homolog, mito protein domain, coexpression, MS/MSMOMMitochondrial dynamics and surveillance > Organelle contact sites | Mitochondrial dynamics and surveillance > Mitophagy | Mitochondrial dynamics and surveillance > Autophagy
95168241Mcrip284331.0MAPK regulated corepressor interacting protein 2induction, coexpression+unknownSignaling
95278653Bola3388962.0bolA-like 3 (E. coli)targetP signal, mito protein domain, MS/MSMatrixMetabolism > Metals and cofactors > Fe-S cluster biosynthesis | Metabolism > Metals and cofactors > Fe-S-containing proteins
95371701Pnpt187178.0polyribonucleotide nucleotidyltransferase 1literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrix|IMSMitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
954211948Pde12201626.0phosphodiesterase 12APEX_matrix, targetP signal+, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-mRNA modifications | Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
955100756Usp3084749.0ubiquitin specific peptidase 30literature,targetP signal+, mito protein domainMOMProtein import, sorting and homeostasis > Protein homeostasis > Proteases | Mitochondrial dynamics and surveillance > Mitophagy | Mitochondrial dynamics and surveillance > Autophagy
95615278Tfb2m64216.0transcription factor B2, mitochondrialliterature, APEX_matrix, targetP signal+, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication | Mitochondrial central dogma > mtRNA metabolism > Transcription
95766973Mrps18b28973.0mitochondrial ribosomal protein S18Bliterature, APEX_matrix, Rickettsial homolog, mito protein domain, MS/MSMatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
958109731Maob4129.0monoamine oxidase Bliterature, mito protein domain, MS/MS++MOMMetabolism > Amino acid metabolism > Catechol metabolism | Metabolism > Detoxification > Xenobiotic metabolism
95970564Prxl2a84293.0peroxiredoxin like 2AGFP, mito protein domain, MS/MS++MembraneMetabolism > Detoxification > ROS and glutathione metabolism
96066447Mgst34259.0microsomal glutathione S-transferase 3APEX_IMS, mito protein domain, MS/MS++MOMMetabolism > Lipid metabolism > Eicosanoid metabolism
96156749Dhodh1723.0dihydroorotate dehydrogenaseliterature, mito protein domain, MS/MS++MIMMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing | Metabolism > Electron carriers > Q-linked reactions, other
96252443Mrpl4851642.0mitochondrial ribosomal protein L48literature, APEX_matrix, mito protein domain, MS/MS++MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome
96314545Gdap154332.0ganglioside-induced differentiation-associated-protein 1APEX_IMS, mito protein domain, MS/MS++MOM0
96412018Bak1578.0BCL2-antagonist/killer 1literature, mito protein domain, MS/MS++MOMMitochondrial dynamics and surveillance > Apoptosis
96517716mt-Nd14535.0NADH dehydrogenase subunit 1literature, Rickettsial homolog, mito protein domain, MS/MSMIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
966433904Ociad2132299.0OCIA domain containing 2MS/MS++unknownSignaling
96766826Taz6901.0tafazzinliterature,yeast mito homolog++, mito protein domainIMSMetabolism > Lipid metabolism > Cardiolipin synthesis
96867880Dcxr51181.0dicarbonyl L-xylulose reductaseAPEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrixMetabolism > Carbohydrate metabolism
96958801Pmaip15366.0phorbol-12-myristate-13-acetate-induced protein 1literature, targetP signal, mito protein domain+MOMMitochondrial dynamics and surveillance > Apoptosis
97066536Nipsnap3b55335.0nipsnap homolog 3BGFP, targetP signal, MS/MS+Matrix0
971109136Mmaa166785.0methylmalonic aciduria (cobalamin deficiency) type Amanual, targetP signal, coexpression+MatrixMetabolism > Vitamin metabolism > Vitamin B12 metabolism
97213070Cyp11a11583.0cytochrome P450, family 11, subfamily a, polypeptide 1literature, mito protein domain, MS/MS+MIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis | Metabolism > Metals and cofactors > Heme-containing proteins
97371361Aifm284883.0apoptosis-inducing factor, mitochondrion-associated 2literature, yeast mito homolog, Rickettsial homolog, mito protein domain, coexpressionMembraneMetabolism > Detoxification > ROS and glutathione metabolism | Mitochondrial dynamics and surveillance > Apoptosis
97469104Marchf554708.0membrane associated ring-CH-type finger 5literature, mito protein domain, coexpression, MS/MSMOMMitochondrial dynamics and surveillance > Mitophagy | Mitochondrial dynamics and surveillance > Autophagy
97521672Prdx27001.0peroxiredoxin 2GFP, Rickettsial homolog, mito protein domain, coexpressionunknownMetabolism > Detoxification > ROS and glutathione metabolism
97694281Sfxn4119559.0sideroflexin 4literature, yeast mito homolog, mito protein domain+MIMSmall molecule transport > Sideroflexins
97752668Ifi273429.0interferon, alpha-inducible protein 27literature, targetP signal, induction, coexpressionMembraneSignaling > Immune response | Mitochondrial dynamics and surveillance > Apoptosis
978217262Abca910350.0ATP-binding cassette, sub-family A (ABC1), member 9GFP, targetP signal, Rickettsial homolog, mito protein domainMembraneSmall molecule transport > ABC transporters
97971986Ddx2855794.0DEAD box helicase 28literature, APEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
98070025Acot711332.0acyl-CoA thioesterase 7targetP signal, mito protein domain, inductionMatrixMetabolism > Lipid metabolism
981320183Msrb3253827.0methionine sulfoxide reductase B3yeast mito homolog+, mito protein domainunknownMetabolism > Detoxification > ROS and glutathione metabolism
982694782300009A05Rik145853.0RIKEN cDNA 2300009A05 geneAPEX_matrix, targetP signal, MS/MSMatrix0
98352123Agpat555326.01-acylglycerol-3-phosphate O-acyltransferase 5 (lysophosphatidic acid acyltransferase, epsilon)literature, mito protein domain, induction, MS/MSMOMMetabolism > Lipid metabolism > Cardiolipin synthesis | Metabolism > Lipid metabolism > Phospholipid metabolism
98416365Acod1730249.0aconitate decarboxylase 1literature,yeast mito homolog, mito protein domain+MatrixMetabolism > Carbohydrate metabolism > Itaconate metabolism | Signaling > Immune response
985269514Fbxl426235.0F-box and leucine-rich repeat protein 4literature, mito protein domain, coexpressionIMS0
98667634Ftmt94033.0ferritin mitochondrialliterature, targetP signal, mito protein domain, MS/MSMatrixMetabolism > Metals and cofactors > Iron homeostasis
98714732Gpam57678.0glycerol-3-phosphate acyltransferase, mitochondrialliterature, mito protein domain, coexpressionMembraneMetabolism > Lipid metabolism > Cardiolipin synthesis | Metabolism > Lipid metabolism > Phospholipid metabolism
98860507Qtrt181890.0queuine tRNA-ribosyltransferase catalytic subunit 1APEX_matrix, targetP signal, Rickettsial homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
989242642Hpdl84842.04-hydroxyphenylpyruvate dioxygenase-likemanual, targetP signal, inductionunknown0
990664994Isoc2a79763.0isochorismatase domain containing 2aAPEX_matrix, MS/MS++Matrix0
991110115Cyp11b1cytochrome P450, family 11, subfamily b, polypeptide 1literature, targetP signal, mito protein domain, coexpressionMIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis
99213072Cyp11b21585.0cytochrome P450, family 11, subfamily b, polypeptide 2literature, targetP signal, mito protein domain, coexpressionMIMMetabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis | Metabolism > Metals and cofactors > Heme-containing proteins
993100048644Pet117100303755.0PET117 homologliterature, yeast mito homolog, MS/MSMIMOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
99471412Dhrs210202.0dehydrogenase/reductase member 2literature,targetP signal, Rickettsial homolog, mito protein domainMatrixMetabolism > Detoxification > Xenobiotic metabolism
99566971Cdk5rap151654.0CDK5 regulatory subunit associated protein 1literature,targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
99656463Snd127044.0staphylococcal nuclease and tudor domain containing 1GFP, yeast mito homolog, mito protein domainunknown0
997109754Cyb5r31727.0cytochrome b5 reductase 3literature, mito protein domain, MS/MS+MOMMetabolism > Detoxification > Xenobiotic metabolism | Metabolism > Detoxification > Amidoxime reducing complex | Metabolism > Lipid metabolism
99817161Maoa4128.0monoamine oxidase Aliterature, mito protein domain, MS/MS+MOMMetabolism > Amino acid metabolism > Catechol metabolism | Metabolism > Detoxification > Xenobiotic metabolism
99975734Mff56947.0mitochondrial fission factorliterature, induction, MS/MSMOMMitochondrial dynamics and surveillance > Fission
1000270151Nlrx179671.0NLR family member X1APEX_matrix, targetP signal, MS/MSMatrixSignaling > Immune response
1001330050Fam185a222234.0family with sequence similarity 185, member AAPEX_matrix, targetP signal, coexpressionMatrix0
1002239555Mief154471.0mitochondrial elongation factor 1literature, mito protein domain, induction, coexpressionMOM | MatrixMitochondrial central dogma > Translation > Mitochondrial ribosome assembly | Mitochondrial dynamics and surveillance > Fission
100369893Coa765260.0cytochrome c oxidase assembly factor 7literature, APEX_IMS, mito protein domain, coexpression, MS/MSIMSOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
1004329910Acot1126027.0acyl-CoA thioesterase 11literature,targetP signal, mito protein domain, coexpressionMatrixMetabolism > Lipid metabolism > Fatty acid oxidation
1005433813Pusl1126789.0pseudouridylate synthase-like 1APEX_matrix, targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > Translation
100677782Polq10721.0polymerase (DNA directed), thetaliterature,targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance
100768055Dmac2l27109.0distal membrane arm assembly complex 2 likeliterature, APEX_matrix, MS/MS++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits
100867809Rmdn355177.0regulator of microtubule dynamics 3literature, APEX_IMS, GFP, MS/MS++MOMMitochondrial dynamics and surveillance > Organelle contact sites
100966477Atp5md84833.0ATP synthase membrane subunit DAPITGFP, MS/MS++MIMOXPHOS > Complex V > CV subunits | OXPHOS > OXPHOS subunits | Mitochondrial dynamics and surveillance > Cristae formation
101067952Tomm209804.0translocase of outer mitochondrial membrane 20literature, yeast mito homolog+MOMProtein import, sorting and homeostasis > Protein import and sorting > TOM | Mitochondrial dynamics and surveillance
101112177Bnip3l665.0BCL2/adenovirus E1B interacting protein 3-likeliterature, mito protein domain+, coexpressionMOMMitochondrial dynamics and surveillance > Apoptosis
101272168Aifm3150209.0apoptosis-inducing factor, mitochondrion-associated 3literature, Rickettsial homolog, mito protein domain+MIMMetabolism > Metals and cofactors > Fe-S-containing proteins | Mitochondrial dynamics and surveillance > Apoptosis
101369773Timm2990580.0translocase of inner mitochondrial membrane 29coexpression, MS/MSMIMProtein import, sorting and homeostasis > Protein import and sorting > TIM22 carrier pathway
1014243382Ppm1k152926.0protein phosphatase 1K (PP2C domain containing)literature, targetP signal, mito protein domainMatrixMetabolism > Amino acid metabolism > Branched-chain amino acid metabolism | Metabolism > Amino acid metabolism > Branched-chain amino acid dehydrogenase complex
101575387Sirt423409.0sirtuin 4literature, targetP signal, mito protein domainMatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolism
101657320Park711315.0Parkinson disease (autosomal recessive, early onset) 7literature, mito protein domain, coexpressionMOMProtein import, sorting and homeostasis > Protein homeostasis | Mitochondrial dynamics and surveillance > Mitophagy | Mitochondrial dynamics and surveillance > Autophagy
1017545725Mterf1amitochondrial transcription termination factor 1aliterature, APEX_matrix, targetP signal, mito protein domain+MatrixMitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid | Mitochondrial central dogma > mtRNA metabolism > Transcription | Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly
101817720mt-Nd4l4539.0NADH dehydrogenase subunit 4Lliterature, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
1019433470AA46719784419.0expressed sequence AA467197GFP, mito protein domain, MS/MS+Membrane0
102067267Uqcc284300.0ubiquinol-cytochrome c reductase complex assembly factor 2APEX_matrix, GFP, coexpression, MS/MSMIMOXPHOS > Complex III > CIII assembly factors | OXPHOS > OXPHOS assembly factors
102179059Nme34832.0NME/NM23 nucleoside diphosphate kinase 3GFP, yeast mito homolog, Rickettsial homolog, mito protein domainMOMMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
1022107999Gtpbp68225.0GTP binding protein 6 (putative)APEX_matrix, targetP signal+, mito protein domainMatrix0
102366198Them5284486.0thioesterase superfamily member 5literature,targetP signal+, mito protein domainMatrixMetabolism > Lipid metabolism
102418747Prkaca5566.0protein kinase, cAMP dependent, catalytic, alphaliterature,mito protein domain, coexpressionMIMSignaling > cAMP-PKA signaling
1025108958Miga284895.0mitoguardin 2literature,coexpressionMOMMitochondrial dynamics and surveillance > Fusion | Mitochondrial dynamics and surveillance > Organelle contact sites
102667749Mgarp84709.0mitochondria localized glutamic acid rich proteinliterature, APEX_IMS, targetP signal, yeast mito homolog, coexpressionMembraneMitochondrial dynamics and surveillance > Trafficking
102717210Mcl14170.0myeloid cell leukemia sequence 1manual, targetP signal, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosis
102860315Myg160314.0melanocyte proliferating gene 1literature, targetP signal, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications | Mitochondrial central dogma > mtRNA metabolism > mt-mRNA modifications
1029320204Etfbkmt254013.0electron transfer flavoprotein beta subunit lysine methyltransferaseliterature,mito protein domain+MatrixMetabolism > Electron carriers > Q-linked reactions, other
103070603Mutyh4595.0mutY DNA glycosylaseGFP, targetP signal, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance
1031380601Fastkd560493.0FAST kinase domains 5APEX_matrix, targetP signal, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing | Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
103267054Paics10606.0phosphoribosylaminoimidazole carboxylase, phosphoribosylaminoribosylaminoimidazole, succinocarboxamide synthetaseAPEX_matrix, Rickettsial homolog, coexpressionMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
103378070Cpt1c126129.0carnitine palmitoyltransferase 1cliterature, yeast mito homolog+, mito protein domainMOMMetabolism > Lipid metabolism > Fatty acid oxidation | Metabolism > Metals and cofactors > Carnitine synthesis and transport | Metabolism > Metals and cofactors > Carnitine shuttle
103494254Rcc1l81554.0reculator of chromosome condensation 1 likeliterature, APEX_matrix, targetP signal, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
1035214917Antkmt65990.0adenine nucleotide translocase lysine methyltransferaseliterature,coexpression, MS/MSMIMMetabolism > Nucleotide metabolism
1036107197Uqcc3790955.0ubiquinol-cytochrome c reductase complex assembly factor 3literature,coexpression, MS/MSMIMOXPHOS > Complex III > CIII assembly factors | OXPHOS > OXPHOS assembly factors
103753381Prdx410549.0peroxiredoxin 4APEX_IMS, Rickettsial homolog, mito protein domainIMSMetabolism > Detoxification > ROS and glutathione metabolism
1038209027Pycr15831.0pyrroline-5-carboxylate reductase 1literature, mito protein domain, MS/MSMatrixMetabolism > Amino acid metabolism > Proline metabolism
103912972Cryz1429.0crystallin, zetaAPEX_matrix, mito protein domain, MS/MSMatrix0
104052477Angel290806.0angel homolog 2APEX_matrix, mito protein domain, MS/MSMatrixMitochondrial central dogma > mtRNA metabolism > mt-mRNA modifications
104174528Mgme192667.0mitochondrial genome maintenance exonuclease 1literature, APEX_matrix, GFP, targetP signalMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication | Mitochondrial central dogma > mtDNA maintenance > mtDNA stability and decay
104268262Agpat456895.01-acylglycerol-3-phosphate O-acyltransferase 4 (lysophosphatidic acid acyltransferase, delta)literature,mito protein domain, inductionMOMMetabolism > Lipid metabolism > Cardiolipin synthesis | Metabolism > Lipid metabolism > Phospholipid metabolism
104369156Comtd1118881.0catechol-O-methyltransferase domain containing 1GFP, MS/MS++Membrane0
1044241159Neu4129807.0sialidase 4GFP, targetP signal+MOMMetabolism > Carbohydrate metabolism
104513115Cyp27b11594.0cytochrome P450, family 27, subfamily b, polypeptide 1literature, targetP signal, mito protein domainMIMMetabolism > Metals and cofactors > Heme-containing proteins | Metabolism > Vitamin metabolism > Vitamin D metabolism
104612457Noct25819.0nocturninliterature,targetP signal, mito protein domainMatrixMetabolism > Metals and cofactors > NAD biosynthesis and metabolism
104772748Hdhd381932.0haloacid dehalogenase-like hydrolase domain containing 3APEX_matrix, MS/MS++Matrix0
1048170756Slc8b180024.0solute carrier family 8 (sodium/lithium/calcium exchanger), member B1literature,mito protein domain, inductionMIMSignaling > Calcium homeostasis > Calcium cycle | Small molecule transport
104917722mt-Nd64541.0NADH dehydrogenase subunit 6literature, Rickettsial homolog, mito protein domainMIMOXPHOS > Complex I > CI subunits | OXPHOS > OXPHOS subunits
105066928Dmac190871.0distal membrane arm assembly complex 1literature,MS/MSMIMOXPHOS > Complex I > CI assembly factors | OXPHOS > OXPHOS assembly factors
1051170752Bco283875.0beta-carotene oxygenase 2literature,mito protein domain, MS/MSMIMMetabolism > Vitamin metabolism > Vitamin A metabolism
105272634Tdrkh11022.0tudor and KH domain containing proteinGFP, mito protein domain, MS/MSMembrane0
1053625249Gpx42879.0glutathione peroxidase 4literature, yeast mito homolog, mito protein domainMIMMetabolism > Detoxification > ROS and glutathione metabolism | Metabolism > Detoxification > Selenoproteins
105412846Comt1312.0catechol-O-methyltransferaseGFP, induction, coexpressionMembraneMetabolism > Amino acid metabolism > Catechol metabolism
105571804Mtfr2113115.0mitochondrial fission regulator 2manual, mito protein domain+MembraneMitochondrial dynamics and surveillance > Fission
105612124Bik638.0BCL2-interacting killermanual, mito protein domain+MOMMitochondrial dynamics and surveillance > Apoptosis
105716882Lig33980.0ligase III, DNA, ATP-dependentliterature,yeast mito homolog, mito protein domain, coexpressionMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication | Mitochondrial central dogma > mtDNA maintenance > mtDNA repair
105812952Cry11407.0cryptochrome 1 (photolyase-like)literature, yeast mito homolog, mito protein domain, coexpressionunknown0
1059227682Trub226995.0TruB pseudouridine (psi) synthase family member 2APEX_matrix, yeast mito homolog, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications
106075266Tomm20l387990.0translocase of outer mitochondrial membrane 20-likemanual, yeast mito homolog+MOMProtein import, sorting and homeostasis > Protein import and sorting
106167433Ccdc127133957.0coiled-coil domain containing 127APEX_IMS, MS/MSMembrane0
1062230734Yrdc79693.0yrdC domain containing (E.coli)manual, targetP signal, Rickettsial homologMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
1063213760Prepl9581.0prolyl endopeptidase-likeAPEX_matrix, targetP signal, Rickettsial homologMatrix0
106466196Myo1980179.0myosin XIXliterature,yeast mito homolog, mito protein domainMOMMitochondrial dynamics and surveillance > Trafficking
106566628Thg1l54974.0tRNA-histidine guanylyltransferase 1-like (S. cerevisiae)literature, targetP signal, coexpressionMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
1066208084Pif180119.0PIF1 5'-to-3' DNA helicaseliterature, yeast mito homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance
106767388Rab5if55969.0RAB5 interacting factorGFP, induction, coexpressionMIMOXPHOS > OXPHOS assembly factors | OXPHOS > Respirasome assembly
106872140Cep8984902.0centrosomal protein 89literature, targetP signalIMSOXPHOS > Complex IV > CIV assembly factors | OXPHOS > OXPHOS assembly factors
106964833Acot10acyl-CoA thioesterase 10literature, targetP signalMatrixMetabolism > Lipid metabolism
107098363Efhd180303.0EF hand domain containing 1literature, mito protein domain, inductionMIMSignaling > Calcium homeostasis > EF hand proteins
107112122Bid637.0BH3 interacting domain death agonistliterature, mito protein domain, coexpressionMOMMitochondrial dynamics and surveillance > Apoptosis
107268073Atpsckmt134145.0ATP synthase C subunit lysine N-methyltransferaseliterature,coexpressionMIMOXPHOS > Complex V > CV assembly factors | OXPHOS > OXPHOS assembly factors
107313081Cyp24a11591.0cytochrome P450, family 24, subfamily a, polypeptide 1literature, targetP signal, mito protein domainMIMMetabolism > Metals and cofactors > Heme-containing proteins | Metabolism > Vitamin metabolism > Vitamin D metabolism
107420773Sptlc29517.0serine palmitoyltransferase, long chain base subunit 2GFP, Rickettsial homolog, mito protein domainMembraneMetabolism > Lipid metabolism > Phospholipid metabolism
107511792Apex1328.0apurinic/apyrimidinic endonuclease 1literature,Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repair
1076329659E130311K13Rik285315.0RIKEN cDNA E130311K13 geneAPEX_matrix, MS/MSMatrix0
107769923Agk55750.0acylglycerol kinaseliterature, APEX_IMS, mito protein domainMIMProtein import, sorting and homeostasis > Protein import and sorting > TIM22 carrier pathway | Metabolism > Lipid metabolism > Phospholipid metabolism
107866369Dus254920.0dihydrouridine synthase 2GFP, Rickettsial homolog, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
107974450Pank280025.0pantothenate kinase 2literature, targetP signal, mito protein domainIMSMetabolism > Metals and cofactors > Coenzyme A metabolism
108050776Polg211232.0polymerase (DNA directed), gamma 2, accessory subunitliterature, APEX_matrix, targetP signal, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication | Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid
1081215456Gpat2150763.0glycerol-3-phosphate acyltransferase 2, mitochondrialmanual, mito protein domainMOMMetabolism > Lipid metabolism > Cardiolipin synthesis | Metabolism > Lipid metabolism > Phospholipid metabolism
108267145Tomm3410953.0translocase of outer mitochondrial membrane 34literature, mito protein domainMOMProtein import, sorting and homeostasis > Protein import and sorting > TOM
108370310Plscr357048.0phospholipid scramblase 3literature,yeast mito homolog, mito protein domainMIMMetabolism > Lipid metabolism > Cardiolipin synthesis
108414230Fkbp1060681.0FK506 binding protein 10APEX_IMS, mito protein domainIMSProtein import, sorting and homeostasis > Protein homeostasis > Chaperones
108597827Exd255218.0exonuclease 3'-5' domain containing 2literature,mito protein domainMatrixMitochondrial central dogma > Translation
108612048Bcl2l1598.0BCL2-like 1literature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosis
108766629Golph364083.0golgi phosphoprotein 3literature, targetP signal, inductionIMS0
108870021Nt5dc264943.05'-nucleotidase domain containing 2APEX_matrix, MS/MSMatrixMetabolism > Nucleotide metabolism > Nucleotide synthesis and processing
108967211Armc1083787.0armadillo repeat containing 10GFP, MS/MSMOMMitochondrial dynamics and surveillance > Fission | Mitochondrial dynamics and surveillance > Trafficking
1090211064Alkbh18846.0alkB homolog 1, histone H2A dioxygenaseliterature, APEX_matrix, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
109156697Akap1011216.0A kinase (PRKA) anchor protein 10literature, mito protein domainMOMSignaling > cAMP-PKA signaling
1092321007Serac184947.0serine active site containing 1literature, APEX_IMS, targetP signalMOMMetabolism > Lipid metabolism > Phospholipid metabolism
109318952Septin45414.0septin 4literature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosis
109469577Fastkd379072.0FAST kinase domains 3APEX_matrix, targetP signalMatrixMitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing | Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay
109512125Bcl2l1110018.0BCL2-like 11 (apoptosis facilitator)manual, targetP signalMOMMitochondrial dynamics and surveillance > Apoptosis
109617966Nbr14077.0NBR1, autophagy cargo receptorAPEX_IMS, coexpressionIMSMitochondrial dynamics and surveillance > Autophagy
109719895Rpia22934.0ribose 5-phosphate isomerase AAPEX_matrix, targetP signalMatrixMetabolism > Carbohydrate metabolism
109851800Bok666.0BCL2-related ovarian killermanual, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosis
1099215708Miga1374986.0mitoguardin 1literatureMOMMitochondrial dynamics and surveillance > Fusion
110066132Prorp9692.0protein only RNase P catalytic subunitAPEX_matrixMatrixMitochondrial central dogma > mtRNA metabolism > mtRNA granules | Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing
110167727Stx1755014.0syntaxin 17APEX_IMS, coexpressionMOMMitochondrial dynamics and surveillance > Fission | Mitochondrial dynamics and surveillance > Organelle contact sites | Mitochondrial dynamics and surveillance > Autophagy
1102408022Primpol201973.0primase and polymerase (DNA-directed)literature,mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repair
1103327762Dna21763.0DNA replication helicase/nuclease 2literature, mito protein domainMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA replication | Metabolism > Metals and cofactors > Fe-S-containing proteins
1104271639Adcy1055811.0adenylate cyclase 10literature,mito protein domainMembraneSignaling > cAMP-PKA signaling
1105244954Prss35167681.0protease, serine 35GFP, mito protein domainunknownProtein import, sorting and homeostasis > Protein homeostasis
1106237781Mief2125170.0mitochondrial elongation factor 2literature,mito protein domainMOMMitochondrial dynamics and surveillance > Fission
1107106338Nsun363899.0NOL1/NOP2/Sun domain family member 3APEX_matrix, mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
110893728Pabpc5140886.0poly(A) binding protein, cytoplasmic 5literature, mito protein domainMatrix0
110976571Styxl151657.0serine/threonine/tyrosine interacting-like 1literature,mito protein domainMatrixMitochondrial dynamics and surveillance > Apoptosis
111056632Sphk256848.0sphingosine kinase 2literature,mito protein domainMIMMetabolism > Lipid metabolism > Phospholipid metabolism | Mitochondrial dynamics and surveillance > Apoptosis
111150873Prkn5071.0parkin RBR E3 ubiquitin protein ligasemanual, mito protein domainMOMMitochondrial dynamics and surveillance > Mitophagy | Mitochondrial dynamics and surveillance > Autophagy
111228114Nsun254888.0NOL1/NOP2/Sun domain family member 2literature,mito protein domainMatrixMitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications
111318693Pick19463.0protein interacting with C kinase 1literature, mito protein domainunknown0
111413400Dmpk1760.0dystrophia myotonica-protein kinaseliterature, mito protein domainMOM0
111512371Casp9842.0caspase 9literature,mito protein domainIMSProtein import, sorting and homeostasis > Protein homeostasis > Proteases | Mitochondrial dynamics and surveillance > Apoptosis
111612370Casp8841.0caspase 8literature, mito protein domainMOMProtein import, sorting and homeostasis > Protein homeostasis | Mitochondrial dynamics and surveillance > Apoptosis
111712367Casp3836.0caspase 3literature,mito protein domainIMSProtein import, sorting and homeostasis > Protein homeostasis > Proteases | Mitochondrial dynamics and surveillance > Apoptosis
111812050Bcl2l2599.0BCL2-like 2literature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosis
111912049Bcl2l1010017.0Bcl2-like 10manual, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosis
112012047Bcl2a1d597.0B cell leukemia/lymphoma 2 related protein A1dmanual, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosis
112112043Bcl2596.0B cell leukemia/lymphoma 2literature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosis
112212015Bad572.0BCL2-associated agonist of cell deathliterature, mito protein domainMOMMitochondrial dynamics and surveillance > Apoptosis
1123207728Pde2a5138.0phosphodiesterase 2A, cGMP-stimulatedliterature,targetP signalMIMSignaling > cAMP-PKA signaling
1124217116Spata2064847.0spermatogenesis associated 20APEX_matrixMatrix0
112567759Plgrkt55848.0plasminogen receptor, C-terminal lysine transmembrane proteinGFPMembrane0
1126194908Pld6201164.0phospholipase D family, member 6literatureMOMMetabolism > Lipid metabolism > Cardiolipin synthesis | Mitochondrial dynamics and surveillance > Fusion
1127170770Bbc327113.0BCL2 binding component 3manualMOMMitochondrial dynamics and surveillance > Apoptosis
112878617CstadCSA-conditional, T cell activation-dependent proteinliteratureMOMSignaling > Immune response
1129734671700066M21Rik205327.0RIKEN cDNA 1700066M21 geneAPEX_matrixMatrix0
113068166Spire156907.0spire type actin nucleation factor 1literatureMOMMitochondrial dynamics and surveillance > Fission | Mitochondrial dynamics and surveillance > Organelle contact sites
113178248Armcx151309.0armadillo repeat containing, X-linked 1literatureMOMMitochondrial dynamics and surveillance > Trafficking
113267416Armcx29823.0armadillo repeat containing, X-linked 2literatureMembrane0
1133278097Armcx654470.0armadillo repeat containing, X-linked 6literatureMembrane0
1134269642Nat8l339983.0N-acetyltransferase 8-likeliteratureMembraneMetabolism > Amino acid metabolism > Glutamate metabolism
113577629Sphkap80309.0SPHK1 interactor, AKAP domain containingmanualMIMSignaling > cAMP-PKA signaling
113676781Mettl464863.0methyltransferase like 4literatureMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA modifications
113771703Armcx351566.0armadillo repeat containing, X-linked 3literatureMOMMitochondrial dynamics and surveillance > Trafficking
113867474Snap299342.0synaptosomal-associated protein 29APEX_IMSIMSMitochondrial dynamics and surveillance > Autophagy
113918970Polb5423.0polymerase (DNA directed), betaliteratureMatrixMitochondrial central dogma > mtDNA maintenance > mtDNA repair
1140109729085Htd2109703458.0hydroxyacyl-thioester dehydratase type 2literatureMatrixMetabolism > Lipid metabolism > Type II fatty acid synthesis
114166364Pigbos1101928527.0Pigb opposite strand 1literatureMOMMitochondrial dynamics and surveillance > Organelle contact sites