Files
RGC-ADOA/ref/mitocarta3.0/MitoPathways.gmt
T

150 lines
34 KiB
Plaintext

Mitochondrial central dogma MitoCarta3.0 2810006K23Rik Aars2 Alkbh1 Angel2 Apex1 Atad3a Aurkaip1 Cars2 Cdk5rap1 Chchd1 Coa3 Cox14 Dap3 Dars2 Ddx28 Dhx30 Dna2 Dus2 Ears2 Elac2 Endog Eral1 Exd2 Exog Fars2 Fastk Fastkd1 Fastkd2 Fastkd3 Fastkd5 Gadd45gip1 Gars Gatb Gatc Gfm1 Gfm2 Grsf1 Gtpbp10 Gtpbp3 Guf1 Hars2 Hemk1 Hsd17b10 Iars2 Kars Lactb2 Lars2 Lig3 Lrpprc Malsu1 Mars2 Metap1d Mettl15 Mettl17 Mettl4 Mettl5 Mettl8 Mgme1 Mief1 Mpv17l2 Mrm1 Mrm2 Mrm3 Mrpl1 Mrpl10 Mrpl11 Mrpl12 Mrpl13 Mrpl14 Mrpl15 Mrpl16 Mrpl17 Mrpl18 Mrpl19 Mrpl2 Mrpl20 Mrpl21 Mrpl22 Mrpl23 Mrpl24 Mrpl27 Mrpl28 Mrpl3 Mrpl30 Mrpl32 Mrpl33 Mrpl34 Mrpl35 Mrpl36 Mrpl37 Mrpl38 Mrpl39 Mrpl4 Mrpl40 Mrpl41 Mrpl42 Mrpl43 Mrpl44 Mrpl45 Mrpl46 Mrpl47 Mrpl48 Mrpl49 Mrpl50 Mrpl51 Mrpl52 Mrpl53 Mrpl54 Mrpl55 Mrpl57 Mrpl58 Mrpl9 Mrps10 Mrps11 Mrps12 Mrps14 Mrps15 Mrps16 Mrps17 Mrps18a Mrps18b Mrps18c Mrps2 Mrps21 Mrps22 Mrps23 Mrps24 Mrps25 Mrps26 Mrps27 Mrps28 Mrps30 Mrps31 Mrps33 Mrps34 Mrps35 Mrps36 Mrps5 Mrps6 Mrps7 Mrps9 Mrrf Mterf1a Mterf1b Mterf2 Mterf3 Mterf4 Mtfmt Mtg1 Mtg2 Mtif2 Mtif3 Mto1 Mtpap Mtres1 Mtrf1 Mtrf1l Mutyh Myg1 Nars2 Ngrn Noa1 Nsun2 Nsun3 Nsun4 Ogg1 Osgepl1 Oxa1l Pars2 Pde12 Pdf Pif1 Pnpt1 Polb Poldip2 Polg Polg2 Polq Polrmt Ppa2 Primpol Prorp Ptcd1 Ptcd2 Ptcd3 Pus1 Pusl1 Qrsl1 Qtrt1 Rars2 Rbfa Rcc1l Recql4 Rexo2 Rmnd1 Rnaseh1 Rpusd3 Rpusd4 Sars2 Slirp Ssbp1 Supv3l1 Taco1 Tars2 Tbrg4 Tefm Tfam Tfb1m Tfb2m Thg1l Timm21 Top1mt Top3a Trit1 Trmt1 Trmt10c Trmt2b Trmt5 Trmu Trnt1 Trub2 Tsfm Tufm Twnk Ung Vars2 Wars2 Yars2 Ybey Yrdc
Mitochondrial central dogma > mtDNA maintenance MitoCarta3.0 Apex1 Atad3a Dna2 Endog Exog Lig3 Mettl4 Mgme1 Mterf1a Mterf1b Mterf2 Mutyh Ogg1 Pif1 Polb Poldip2 Polg Polg2 Polq Polrmt Ppa2 Primpol Recql4 Rnaseh1 Ssbp1 Tfam Tfb2m Top1mt Top3a Twnk Ung
Mitochondrial central dogma > mtDNA maintenance > mtDNA replication MitoCarta3.0 Dna2 Exog Lig3 Mgme1 Polg Polg2 Polrmt Rnaseh1 Ssbp1 Tfam Tfb2m Top1mt Top3a Twnk
Mitochondrial central dogma > mtDNA maintenance > mtDNA nucleoid MitoCarta3.0 Atad3a Mterf1a Mterf1b Mterf2 Poldip2 Polg Polg2 Polrmt Ssbp1 Tfam Twnk
Mitochondrial central dogma > mtDNA maintenance > mtDNA repair MitoCarta3.0 Apex1 Exog Lig3 Ogg1 Polb Polg Primpol Recql4 Ung
Mitochondrial central dogma > mtDNA maintenance > mtDNA modifications MitoCarta3.0 Mettl4
Mitochondrial central dogma > mtDNA maintenance > mtDNA stability and decay MitoCarta3.0 Endog Exog Mgme1
Mitochondrial central dogma > mtRNA metabolism MitoCarta3.0 Alkbh1 Angel2 Cdk5rap1 Ddx28 Dhx30 Dus2 Elac2 Endog Eral1 Fastk Fastkd1 Fastkd2 Fastkd3 Fastkd5 Grsf1 Gtpbp3 Hsd17b10 Lactb2 Lrpprc Mettl15 Mettl17 Mettl5 Mettl8 Mrm1 Mrm2 Mrm3 Mrpl12 Mrpl47 Mrps7 Mrps9 Mterf1a Mterf1b Mto1 Mtpap Mtres1 Myg1 Ngrn Noa1 Nsun2 Nsun3 Nsun4 Osgepl1 Pde12 Pnpt1 Polrmt Ppa2 Prorp Ptcd1 Ptcd2 Pus1 Qtrt1 Rcc1l Rexo2 Rmnd1 Rnaseh1 Rpusd3 Rpusd4 Slirp Supv3l1 Tbrg4 Tefm Tfam Tfb1m Tfb2m Thg1l Top1mt Trit1 Trmt1 Trmt10c Trmt2b Trmt5 Trmu Trnt1 Trub2 Ybey Yrdc
Mitochondrial central dogma > mtRNA metabolism > Transcription MitoCarta3.0 Mrpl12 Mterf1a Mterf1b Mtres1 Polrmt Tefm Tfam Tfb2m Top1mt
Mitochondrial central dogma > mtRNA metabolism > mtRNA granules MitoCarta3.0 Alkbh1 Ddx28 Dhx30 Eral1 Fastk Fastkd1 Fastkd2 Fastkd5 Grsf1 Hsd17b10 Mrm1 Mrm2 Mrpl47 Mrps7 Mrps9 Mtpap Noa1 Prorp Ptcd1 Ptcd2 Pus1 Rmnd1 Rpusd3 Rpusd4 Supv3l1 Tfb1m Trmt10c Trub2
Mitochondrial central dogma > mtRNA metabolism > Polycistronic mtRNA processing MitoCarta3.0 Elac2 Fastk Fastkd1 Fastkd2 Fastkd3 Fastkd5 Grsf1 Hsd17b10 Prorp Ptcd2 Tbrg4 Trmt10c Ybey
Mitochondrial central dogma > mtRNA metabolism > mt-tRNA modifications MitoCarta3.0 Alkbh1 Cdk5rap1 Dus2 Gtpbp3 Hsd17b10 Mto1 Nsun2 Nsun3 Osgepl1 Pus1 Qtrt1 Rpusd4 Thg1l Trit1 Trmt1 Trmt10c Trmt2b Trmt5 Trmu Trnt1 Yrdc
Mitochondrial central dogma > mtRNA metabolism > mt-rRNA modifications MitoCarta3.0 Mettl15 Mettl17 Mettl5 Mrm1 Mrm2 Mrm3 Mtpap Myg1 Ngrn Nsun4 Rcc1l Rpusd3 Rpusd4 Tfb1m Trit1 Trmt2b Trub2
Mitochondrial central dogma > mtRNA metabolism > mt-mRNA modifications MitoCarta3.0 Angel2 Mtpap Myg1 Pde12
Mitochondrial central dogma > mtRNA metabolism > mtRNA stability and decay MitoCarta3.0 Endog Fastk Fastkd1 Fastkd2 Fastkd3 Fastkd5 Grsf1 Lactb2 Lrpprc Mtpap Pde12 Pnpt1 Rexo2 Rnaseh1 Slirp Supv3l1 Tbrg4
Mitochondrial central dogma > Translation MitoCarta3.0 2810006K23Rik Aars2 Aurkaip1 Cars2 Chchd1 Coa3 Cox14 Dap3 Dars2 Ddx28 Dhx30 Ears2 Eral1 Exd2 Fars2 Fastkd2 Gadd45gip1 Gars Gatb Gatc Gfm1 Gfm2 Grsf1 Gtpbp10 Guf1 Hars2 Hemk1 Iars2 Kars Lars2 Lrpprc Malsu1 Mars2 Metap1d Mettl17 Mief1 Mpv17l2 Mrm2 Mrm3 Mrpl1 Mrpl10 Mrpl11 Mrpl12 Mrpl13 Mrpl14 Mrpl15 Mrpl16 Mrpl17 Mrpl18 Mrpl19 Mrpl2 Mrpl20 Mrpl21 Mrpl22 Mrpl23 Mrpl24 Mrpl27 Mrpl28 Mrpl3 Mrpl30 Mrpl32 Mrpl33 Mrpl34 Mrpl35 Mrpl36 Mrpl37 Mrpl38 Mrpl39 Mrpl4 Mrpl40 Mrpl41 Mrpl42 Mrpl43 Mrpl44 Mrpl45 Mrpl46 Mrpl47 Mrpl48 Mrpl49 Mrpl50 Mrpl51 Mrpl52 Mrpl53 Mrpl54 Mrpl55 Mrpl57 Mrpl58 Mrpl9 Mrps10 Mrps11 Mrps12 Mrps14 Mrps15 Mrps16 Mrps17 Mrps18a Mrps18b Mrps18c Mrps2 Mrps21 Mrps22 Mrps23 Mrps24 Mrps25 Mrps26 Mrps27 Mrps28 Mrps30 Mrps31 Mrps33 Mrps34 Mrps35 Mrps36 Mrps5 Mrps6 Mrps7 Mrps9 Mrrf Mterf1a Mterf3 Mterf4 Mtfmt Mtg1 Mtg2 Mtif2 Mtif3 Mtres1 Mtrf1 Mtrf1l Nars2 Ngrn Noa1 Nsun4 Oxa1l Pars2 Pdf Ppa2 Ptcd3 Pusl1 Qrsl1 Rars2 Rbfa Rmnd1 Sars2 Slirp Taco1 Tars2 Tfb1m Timm21 Tsfm Tufm Vars2 Wars2 Yars2 Ybey
Mitochondrial central dogma > Translation > Mitochondrial ribosome MitoCarta3.0 Aurkaip1 Chchd1 Dap3 Gadd45gip1 Mrpl1 Mrpl10 Mrpl11 Mrpl12 Mrpl13 Mrpl14 Mrpl15 Mrpl16 Mrpl17 Mrpl18 Mrpl19 Mrpl2 Mrpl20 Mrpl21 Mrpl22 Mrpl23 Mrpl24 Mrpl27 Mrpl28 Mrpl3 Mrpl30 Mrpl32 Mrpl33 Mrpl34 Mrpl35 Mrpl36 Mrpl37 Mrpl38 Mrpl39 Mrpl4 Mrpl40 Mrpl41 Mrpl42 Mrpl43 Mrpl44 Mrpl45 Mrpl46 Mrpl47 Mrpl48 Mrpl49 Mrpl50 Mrpl51 Mrpl52 Mrpl53 Mrpl54 Mrpl55 Mrpl57 Mrpl58 Mrpl9 Mrps10 Mrps11 Mrps12 Mrps14 Mrps15 Mrps16 Mrps17 Mrps18a Mrps18b Mrps18c Mrps2 Mrps21 Mrps22 Mrps23 Mrps24 Mrps25 Mrps26 Mrps27 Mrps28 Mrps30 Mrps31 Mrps33 Mrps34 Mrps35 Mrps36 Mrps5 Mrps6 Mrps7 Mrps9 Ptcd3
Mitochondrial central dogma > Translation > Mitochondrial ribosome assembly MitoCarta3.0 Ddx28 Dhx30 Eral1 Fastkd2 Grsf1 Gtpbp10 Malsu1 Mettl17 Mief1 Mpv17l2 Mrm2 Mrm3 Mterf1a Mterf3 Mterf4 Mtg1 Mtg2 Ngrn Noa1 Nsun4 Ptcd3 Rbfa Tfb1m Ybey
Mitochondrial central dogma > Translation > Translation factors MitoCarta3.0 2810006K23Rik Coa3 Cox14 Gfm1 Gfm2 Hemk1 Mrpl58 Mrrf Mtif2 Mtif3 Mtrf1 Mtrf1l Taco1 Timm21 Tsfm Tufm
Mitochondrial central dogma > Translation > mt-tRNA synthetases MitoCarta3.0 Aars2 Cars2 Dars2 Ears2 Fars2 Gars Gatb Gatc Hars2 Iars2 Kars Lars2 Mars2 Nars2 Pars2 Qrsl1 Rars2 Sars2 Tars2 Vars2 Wars2 Yars2
Mitochondrial central dogma > Translation > fMet processing MitoCarta3.0 Metap1d Mtfmt Pdf
Protein import, sorting and homeostasis MitoCarta3.0 Afg1l Afg3l1 Afg3l2 Agk Aifm1 Atad1 Atp23 Casp3 Casp8 Casp9 Chchd4 Clpb Clpp Clpx Dnaja3 Dnajc11 Dnajc15 Dnajc19 Dnajc4 Dnlz Fkbp10 Gfer Grpel1 Grpel2 Hspd1 Hspe1 Htra2 Ide Immp1l Immp2l Lactb Lap3 Lonp1 Maip1 Metap1d Mipep Mtx1 Mtx2 Mul1 Nln Nrd1 Oma1 Oxa1l Pam16 Park7 Parl Pdf Phb Phb2 Pitrm1 Pmpca Pmpcb Prss35 Romo1 Samm50 Spg7 Stoml2 Timm10 Timm10b Timm13 Timm17a Timm17b Timm21 Timm22 Timm23 Timm29 Timm44 Timm50 Timm8a1 Timm8a2 Timm8b Timm9 Tomm20 Tomm20l Tomm22 Tomm34 Tomm40 Tomm40l Tomm5 Tomm6 Tomm7 Tomm70a Trap1 Uqcrc1 Uqcrc2 Usp30 Xpnpep3 Yme1l1
Protein import, sorting and homeostasis > Protein import and sorting MitoCarta3.0 Agk Aifm1 Chchd4 Dnajc11 Dnajc15 Dnajc19 Gfer Grpel1 Grpel2 Immp1l Immp2l Mipep Mtx1 Mtx2 Nrd1 Oxa1l Pam16 Pmpca Pmpcb Romo1 Samm50 Timm10 Timm10b Timm13 Timm17a Timm17b Timm21 Timm22 Timm23 Timm29 Timm44 Timm50 Timm8a1 Timm8a2 Timm8b Timm9 Tomm20 Tomm20l Tomm22 Tomm34 Tomm40 Tomm40l Tomm5 Tomm6 Tomm7 Tomm70a Uqcrc1 Uqcrc2 Xpnpep3
Protein import, sorting and homeostasis > Protein import and sorting > TOM MitoCarta3.0 Tomm20 Tomm22 Tomm34 Tomm40 Tomm40l Tomm5 Tomm6 Tomm7 Tomm70a
Protein import, sorting and homeostasis > Protein import and sorting > SAM MitoCarta3.0 Mtx1 Mtx2 Samm50
Protein import, sorting and homeostasis > Protein import and sorting > MIA40 MitoCarta3.0 Aifm1 Chchd4 Gfer
Protein import, sorting and homeostasis > Protein import and sorting > TIM22 carrier pathway MitoCarta3.0 Agk Timm22 Timm29
Protein import, sorting and homeostasis > Protein import and sorting > TIM23 presequence pathway MitoCarta3.0 Romo1 Timm17a Timm17b Timm21 Timm23 Timm50
Protein import, sorting and homeostasis > Protein import and sorting > Import motor MitoCarta3.0 Dnajc15 Dnajc19 Grpel1 Grpel2 Pam16 Timm44
Protein import, sorting and homeostasis > Protein import and sorting > OXA MitoCarta3.0 Oxa1l
Protein import, sorting and homeostasis > Protein import and sorting > Preprotein cleavage MitoCarta3.0 Immp1l Immp2l Mipep Pmpca Pmpcb Uqcrc1 Uqcrc2 Xpnpep3
Protein import, sorting and homeostasis > Protein homeostasis MitoCarta3.0 Afg1l Afg3l1 Afg3l2 Atad1 Atp23 Casp3 Casp8 Casp9 Clpb Clpp Clpx Dnaja3 Dnajc4 Dnlz Fkbp10 Hspd1 Hspe1 Htra2 Ide Immp1l Immp2l Lactb Lap3 Lonp1 Maip1 Metap1d Mipep Mul1 Nln Nrd1 Oma1 Park7 Parl Pdf Phb Phb2 Pitrm1 Pmpca Pmpcb Prss35 Spg7 Stoml2 Timm10 Timm10b Timm13 Timm8a1 Timm8a2 Timm8b Timm9 Trap1 Usp30 Xpnpep3 Yme1l1
Protein import, sorting and homeostasis > Protein homeostasis > Proteases MitoCarta3.0 Afg1l Afg3l1 Afg3l2 Atad1 Atp23 Casp3 Casp9 Clpb Clpp Clpx Htra2 Ide Immp1l Immp2l Lactb Lap3 Lonp1 Metap1d Mipep Nln Oma1 Parl Pitrm1 Pmpca Pmpcb Spg7 Usp30 Xpnpep3 Yme1l1
Protein import, sorting and homeostasis > Protein homeostasis > Chaperones MitoCarta3.0 Dnaja3 Dnlz Fkbp10 Hspd1 Hspe1 Maip1 Nrd1 Phb Phb2 Timm10 Timm10b Timm13 Timm8a1 Timm8a2 Timm8b Timm9 Trap1
OXPHOS MitoCarta3.0 Acad9 Aifm1 Atp5a1 Atp5b Atp5c1 Atp5d Atp5e Atp5g1 Atp5g2 Atp5g3 Atp5h Atp5j Atp5j2 Atp5k Atp5l Atp5md Atp5mpl Atp5o Atp5pb Atpaf1 Atpaf2 Atpif1 Atpsckmt Bcs1l Cep89 Cmc1 Cmc2 Coa3 Coa4 Coa5 Coa6 Coa7 Coa8 Cox10 Cox11 Cox14 Cox15 Cox16 Cox17 Cox18 Cox19 Cox20 Cox4i1 Cox4i2 Cox5a Cox5b Cox6a1 Cox6a2 Cox6b1 Cox6b2 Cox6c Cox7a1 Cox7a2 Cox7a2l Cox7b Cox7c Cox8a Cox8b Cox8c Cyc1 Cycs Cyct Dmac1 Dmac2 Dmac2l Ecsit Fmc1 Foxred1 Hccs Higd1a Higd2a Lyrm2 Lyrm7 Ndufa1 Ndufa10 Ndufa11 Ndufa12 Ndufa13 Ndufa2 Ndufa3 Ndufa4 Ndufa5 Ndufa6 Ndufa7 Ndufa8 Ndufa9 Ndufab1 Ndufaf1 Ndufaf2 Ndufaf3 Ndufaf4 Ndufaf5 Ndufaf6 Ndufaf7 Ndufaf8 Ndufb10 Ndufb11 Ndufb2 Ndufb3 Ndufb4 Ndufb5 Ndufb6 Ndufb7 Ndufb8 Ndufb9 Ndufc1 Ndufc2 Ndufs1 Ndufs2 Ndufs3 Ndufs4 Ndufs5 Ndufs6 Ndufs7 Ndufs8 Ndufv1 Ndufv2 Ndufv3 Nubpl Pet100 Pet117 Pnkd Rab5if Sco1 Sco2 Sdha Sdhaf1 Sdhaf2 Sdhaf3 Sdhaf4 Sdhb Sdhc Sdhd Smim20 Surf1 Taco1 Timm21 Timmdc1 Tmem126a Tmem126b Tmem177 Tmem186 Tmem70 Ttc19 Uqcc1 Uqcc2 Uqcc3 Uqcr10 Uqcr11 Uqcrb Uqcrc1 Uqcrc2 Uqcrfs1 Uqcrh Uqcrq mt-Atp6 mt-Atp8 mt-Co1 mt-Co2 mt-Co3 mt-Cytb mt-Nd1 mt-Nd2 mt-Nd3 mt-Nd4 mt-Nd4l mt-Nd5 mt-Nd6
OXPHOS > OXPHOS subunits MitoCarta3.0 Atp5a1 Atp5b Atp5c1 Atp5d Atp5e Atp5g1 Atp5g2 Atp5g3 Atp5h Atp5j Atp5j2 Atp5k Atp5l Atp5md Atp5mpl Atp5o Atp5pb Atpif1 Cox4i1 Cox4i2 Cox5a Cox5b Cox6a1 Cox6a2 Cox6b1 Cox6b2 Cox6c Cox7a1 Cox7a2 Cox7a2l Cox7b Cox7c Cox8a Cox8b Cox8c Cyc1 Cycs Cyct Dmac2l Hccs Ndufa1 Ndufa10 Ndufa11 Ndufa12 Ndufa13 Ndufa2 Ndufa3 Ndufa4 Ndufa5 Ndufa6 Ndufa7 Ndufa8 Ndufa9 Ndufab1 Ndufb10 Ndufb11 Ndufb2 Ndufb3 Ndufb4 Ndufb5 Ndufb6 Ndufb7 Ndufb8 Ndufb9 Ndufc1 Ndufc2 Ndufs1 Ndufs2 Ndufs3 Ndufs4 Ndufs5 Ndufs6 Ndufs7 Ndufs8 Ndufv1 Ndufv2 Ndufv3 Sdha Sdhb Sdhc Sdhd Uqcr10 Uqcr11 Uqcrb Uqcrc1 Uqcrc2 Uqcrfs1 Uqcrh Uqcrq mt-Atp6 mt-Atp8 mt-Co1 mt-Co2 mt-Co3 mt-Cytb mt-Nd1 mt-Nd2 mt-Nd3 mt-Nd4 mt-Nd4l mt-Nd5 mt-Nd6
OXPHOS > OXPHOS assembly factors MitoCarta3.0 Acad9 Aifm1 Atpaf1 Atpaf2 Atpsckmt Bcs1l Cep89 Cmc1 Cmc2 Coa3 Coa4 Coa5 Coa6 Coa7 Coa8 Cox10 Cox11 Cox14 Cox15 Cox16 Cox17 Cox18 Cox19 Cox20 Cox7a2l Dmac1 Dmac2 Ecsit Fmc1 Foxred1 Higd1a Higd2a Lyrm2 Lyrm7 Ndufaf1 Ndufaf2 Ndufaf3 Ndufaf4 Ndufaf5 Ndufaf6 Ndufaf7 Ndufaf8 Nubpl Pet100 Pet117 Pnkd Rab5if Sco1 Sco2 Sdhaf1 Sdhaf2 Sdhaf3 Sdhaf4 Smim20 Surf1 Taco1 Timm21 Timmdc1 Tmem126a Tmem126b Tmem177 Tmem186 Tmem70 Ttc19 Uqcc1 Uqcc2 Uqcc3
OXPHOS > Complex I MitoCarta3.0 Acad9 Aifm1 Dmac1 Dmac2 Ecsit Foxred1 Lyrm2 Ndufa1 Ndufa10 Ndufa11 Ndufa12 Ndufa13 Ndufa2 Ndufa3 Ndufa5 Ndufa6 Ndufa7 Ndufa8 Ndufa9 Ndufab1 Ndufaf1 Ndufaf2 Ndufaf3 Ndufaf4 Ndufaf5 Ndufaf6 Ndufaf7 Ndufaf8 Ndufb10 Ndufb11 Ndufb2 Ndufb3 Ndufb4 Ndufb5 Ndufb6 Ndufb7 Ndufb8 Ndufb9 Ndufc1 Ndufc2 Ndufs1 Ndufs2 Ndufs3 Ndufs4 Ndufs5 Ndufs6 Ndufs7 Ndufs8 Ndufv1 Ndufv2 Ndufv3 Nubpl Timmdc1 Tmem126a Tmem126b Tmem186 Tmem70 mt-Nd1 mt-Nd2 mt-Nd3 mt-Nd4 mt-Nd4l mt-Nd5 mt-Nd6
OXPHOS > Complex I > CI subunits MitoCarta3.0 Ndufa1 Ndufa10 Ndufa11 Ndufa12 Ndufa13 Ndufa2 Ndufa3 Ndufa5 Ndufa6 Ndufa7 Ndufa8 Ndufa9 Ndufab1 Ndufb10 Ndufb11 Ndufb2 Ndufb3 Ndufb4 Ndufb5 Ndufb6 Ndufb7 Ndufb8 Ndufb9 Ndufc1 Ndufc2 Ndufs1 Ndufs2 Ndufs3 Ndufs4 Ndufs5 Ndufs6 Ndufs7 Ndufs8 Ndufv1 Ndufv2 Ndufv3 mt-Nd1 mt-Nd2 mt-Nd3 mt-Nd4 mt-Nd4l mt-Nd5 mt-Nd6
OXPHOS > Complex I > CI assembly factors MitoCarta3.0 Acad9 Aifm1 Dmac1 Dmac2 Ecsit Foxred1 Lyrm2 Ndufaf1 Ndufaf2 Ndufaf3 Ndufaf4 Ndufaf5 Ndufaf6 Ndufaf7 Ndufaf8 Nubpl Timmdc1 Tmem126a Tmem126b Tmem186 Tmem70
OXPHOS > Complex II MitoCarta3.0 Sdha Sdhaf1 Sdhaf2 Sdhaf3 Sdhaf4 Sdhb Sdhc Sdhd
OXPHOS > Complex II > CII subunits MitoCarta3.0 Sdha Sdhb Sdhc Sdhd
OXPHOS > Complex II > CII assembly factors MitoCarta3.0 Sdhaf1 Sdhaf2 Sdhaf3 Sdhaf4
OXPHOS > Complex III MitoCarta3.0 Bcs1l Cyc1 Lyrm7 Ttc19 Uqcc1 Uqcc2 Uqcc3 Uqcr10 Uqcr11 Uqcrb Uqcrc1 Uqcrc2 Uqcrfs1 Uqcrh Uqcrq mt-Cytb
OXPHOS > Complex III > CIII subunits MitoCarta3.0 Cyc1 Uqcr10 Uqcr11 Uqcrb Uqcrc1 Uqcrc2 Uqcrfs1 Uqcrh Uqcrq mt-Cytb
OXPHOS > Complex III > CIII assembly factors MitoCarta3.0 Bcs1l Lyrm7 Ttc19 Uqcc1 Uqcc2 Uqcc3
OXPHOS > Complex IV MitoCarta3.0 Cep89 Cmc1 Cmc2 Coa3 Coa4 Coa5 Coa6 Coa7 Coa8 Cox10 Cox11 Cox14 Cox15 Cox16 Cox17 Cox18 Cox19 Cox20 Cox4i1 Cox4i2 Cox5a Cox5b Cox6a1 Cox6a2 Cox6b1 Cox6b2 Cox6c Cox7a1 Cox7a2 Cox7a2l Cox7b Cox7c Cox8a Cox8b Cox8c Higd1a Ndufa4 Pet100 Pet117 Pnkd Sco1 Sco2 Smim20 Surf1 Taco1 Timm21 Tmem177 mt-Co1 mt-Co2 mt-Co3
OXPHOS > Complex IV > CIV subunits MitoCarta3.0 Cox4i1 Cox4i2 Cox5a Cox5b Cox6a1 Cox6a2 Cox6b1 Cox6b2 Cox6c Cox7a1 Cox7a2 Cox7a2l Cox7b Cox7c Cox8a Cox8b Cox8c Ndufa4 mt-Co1 mt-Co2 mt-Co3
OXPHOS > Complex IV > CIV assembly factors MitoCarta3.0 Cep89 Cmc1 Cmc2 Coa3 Coa4 Coa5 Coa6 Coa7 Coa8 Cox10 Cox11 Cox14 Cox15 Cox16 Cox17 Cox18 Cox19 Cox20 Higd1a Pet100 Pet117 Pnkd Sco1 Sco2 Smim20 Surf1 Taco1 Timm21 Tmem177
OXPHOS > Complex V MitoCarta3.0 Atp5a1 Atp5b Atp5c1 Atp5d Atp5e Atp5g1 Atp5g2 Atp5g3 Atp5h Atp5j Atp5j2 Atp5k Atp5l Atp5md Atp5mpl Atp5o Atp5pb Atpaf1 Atpaf2 Atpif1 Atpsckmt Dmac2l Fmc1 Tmem70 mt-Atp6 mt-Atp8
OXPHOS > Complex V > CV subunits MitoCarta3.0 Atp5a1 Atp5b Atp5c1 Atp5d Atp5e Atp5g1 Atp5g2 Atp5g3 Atp5h Atp5j Atp5j2 Atp5k Atp5l Atp5md Atp5mpl Atp5o Atp5pb Atpif1 Dmac2l mt-Atp6 mt-Atp8
OXPHOS > Complex V > CV assembly factors MitoCarta3.0 Atpaf1 Atpaf2 Atpsckmt Fmc1 Tmem70
OXPHOS > Respirasome assembly MitoCarta3.0 Cox7a2l Higd1a Higd2a Rab5if
OXPHOS > Cytochrome C MitoCarta3.0 Cycs Cyct Hccs
Metabolism MitoCarta3.0 Aadat Aass Abat Abcb10 Abcb6 Abcb7 Abhd10 Abhd11 Acaa1a Acaa1b Acaa2 Acaca Acacb Acad10 Acad11 Acad12 Acad8 Acadl Acadm Acads Acadsb Acadvl Acat1 Acly Aco2 Acod1 Acot10 Acot11 Acot13 Acot2 Acot7 Acot9 Acp6 Acsf2 Acsf3 Acsl1 Acsl6 Acsm1 Acsm2 Acsm3 Acsm4 Acsm5 Acss1 Acss3 Adhfe1 Agk Agmat Agpat4 Agpat5 Agxt Agxt2 Aifm2 Aifm3 Ak2 Ak3 Ak4 Akr1b10 Akr1b7 Akr7a5 Alas1 Alas2 Aldh18a1 Aldh1b1 Aldh1l1 Aldh1l2 Aldh2 Aldh3a2 Aldh4a1 Aldh5a1 Aldh6a1 Aldh7a1 Aldh9a1 Amacr Amt Antkmt Arg2 Auh Bcat2 Bckdha Bckdhb Bckdk Bco2 Bdh1 Bola1 Bola3 Bphl Car5a Car5b Cat Cbr2 Cbr3 Cbr4 Chchd7 Chdh Chpt1 Cisd1 Cisd3 Ckmt1 Ckmt2 Clybl Cmpk2 Coasy Comt Coq10a Coq10b Coq2 Coq3 Coq4 Coq5 Coq6 Coq7 Coq8a Coq8b Coq9 Cox10 Cox11 Cox15 Cox17 Cox19 Cpox Cps1 Cpt1a Cpt1b Cpt1c Cpt2 Crat Crls1 Crot Cs Cyb5b Cyb5r3 Cyc1 Cycs Cyct Cyp11a1 Cyp11b1 Cyp11b2 Cyp24a1 Cyp27a1 Cyp27b1 D2hgdh Dbi Dbt Dcxr Decr1 Dglucy Dguok Dhodh Dhrs1 Dhrs2 Dhrs4 Dhtkd1 Dlat Dld Dlst Dmgdh Dna2 Dut Ech1 Echdc1 Echs1 Eci1 Eci2 Ehhadh Ephx2 Etfa Etfb Etfbkmt Etfdh Etfrf1 Ethe1 Fabp1 Fahd1 Fam210b Fasn Fdps Fdx1 Fdx2 Fdxr Fech Fh1 Fhit Flad1 Fpgs Fth1 Ftmt Fxn Gatm Gcat Gcdh Gcsh Gldc Glrx2 Glrx5 Gls Gls2 Glud1 Glyat Glyctk Gm4952 Gm4984 Got2 Gpam Gpat2 Gpd2 Gpt2 Gpx1 Gpx4 Grhpr Grpel1 Grpel2 Gsr Gstk1 Gstz1 Gtpbp3 Guk1 H2-Ke6 Hadh Hadha Hadhb Hagh Hao2 Hccs Hibadh Hibch Hint1 Hint2 Hmgcl Hmgcs2 Hoga1 Hscb Hsd17b10 Hsd17b4 Hspa9 Htd2 Iba57 Idh2 Idh3a Idh3b Idh3g Idi1 Isca1 Isca2 Iscu Ivd Kmo Kyat3 L2hgdh Lactb Ldhal6b Ldhb Ldhd Lias Lipt1 Lipt2 Lypla1 Lyplal1 Lyrm4 Maoa Maob Mcat Mccc1 Mccc2 Mcee Mdh2 Me2 Me3 Mecr Mgst1 Mgst3 Mlycd Mmaa Mmab Mmadhc Mmut Mocs1 Mpc1 Mpc2 Mpst Mrps36 Msra Msrb2 Msrb3 Mtarc1 Mtarc2 Mtfmt Mthfd1l Mthfd2 Mthfd2l Mthfs Mthfsl Mto1 Nadk2 Nags Nat8l Naxd Naxe Ndufab1 Ndufs1 Ndufs2 Ndufs7 Ndufs8 Ndufv1 Ndufv2 Neu4 Nfs1 Nfu1 Nit1 Nit2 Nme3 Nme4 Nme6 Nmnat3 Nnt Noct Nt5dc2 Nt5m Nthl1 Nubpl Nudt13 Nudt19 Nudt2 Nudt5 Nudt8 Nudt9 Oat Ogdh Ogdhl Osbpl1a Otc Oxct1 Oxct2a Oxr1 Oxsm Paics Pank2 Pcbd2 Pcca Pccb Pck2 Pcx Pdha1 Pdha2 Pdhb Pdhx Pdk1 Pdk2 Pdk3 Pdk4 Pdp1 Pdp2 Pdpr Pdss1 Pdss2 Pgs1 Phyh Pisd Pld6 Plpbp Plscr3 Pnpla8 Pnpo Ppa2 Ppm1k Ppox Prdx2 Prdx3 Prdx4 Prdx5 Prdx6 Prelid1 Prelid3a Prelid3b Prodh Prodh2 Prxl2a Ptges2 Ptpmt1 Pycr1 Pycr2 Qdpr Rdh13 Rdh14 Rfk Rpia Rsad1 Sardh Sco1 Sco2 Scp2 Sdha Sdhb Sdhc Sdhd Sdsl Selenoo Serac1 Sfxn1 Sfxn3 Sfxn5 Shmt2 Sirt3 Sirt4 Sirt5 Slc25a1 Slc25a10 Slc25a11 Slc25a12 Slc25a13 Slc25a14 Slc25a15 Slc25a19 Slc25a2 Slc25a20 Slc25a21 Slc25a23 Slc25a24 Slc25a25 Slc25a28 Slc25a29 Slc25a3 Slc25a30 Slc25a31 Slc25a32 Slc25a33 Slc25a36 Slc25a37 Slc25a38 Slc25a4 Slc25a41 Slc25a42 Slc25a44 Slc25a5 Slc25a51 Sod1 Sod2 Sphk2 Spr Sptlc2 Sqor Star Stard7 Sucla2 Suclg1 Suclg2 Sugct Suox Tamm41 Taz Them4 Them5 Tk2 Tmlhe Triap1 Tspo Tst Tstd1 Txn2 Txnrd1 Txnrd2 Uqcrfs1 Zadh2 mt-Co1 mt-Cytb
Metabolism > Carbohydrate metabolism MitoCarta3.0 Abhd11 Acaa2 Acat1 Acly Aco2 Acod1 Auh Bdh1 Clybl Cs D2hgdh Dcxr Dlat Dld Dlst Fahd1 Fh1 Glyctk Gm4984 Got2 Gpd2 Hadhb Hmgcl Hmgcs2 Idh2 Idh3a Idh3b Idh3g L2hgdh Ldhal6b Ldhd Mcee Mdh2 Me2 Me3 Mmut Mpc1 Mpc2 Mrps36 Neu4 Ogdh Ogdhl Oxct1 Oxct2a Pcca Pccb Pck2 Pcx Pdha1 Pdha2 Pdhb Pdhx Pdk1 Pdk2 Pdk3 Pdk4 Pdp1 Pdp2 Pdpr Rpia Sdha Sdhb Sdhc Sdhd Sfxn5 Slc25a1 Slc25a10 Slc25a11 Slc25a12 Slc25a13 Sucla2 Suclg1 Suclg2
Metabolism > Carbohydrate metabolism > Gluconeogenesis MitoCarta3.0 Gm4984 Mdh2 Mpc1 Mpc2 Pck2 Pcx Slc25a1 Slc25a10 Slc25a11
Metabolism > Carbohydrate metabolism > Malate-aspartate shuttle MitoCarta3.0 Got2 Mdh2 Slc25a10 Slc25a11 Slc25a12 Slc25a13
Metabolism > Carbohydrate metabolism > Glycerol phosphate shuttle MitoCarta3.0 Gpd2
Metabolism > Carbohydrate metabolism > Pyruvate metabolism MitoCarta3.0 Dlat Dld Gm4984 Mpc1 Mpc2 Pdha1 Pdha2 Pdhb Pdhx Pdk1 Pdk2 Pdk3 Pdk4 Pdp1 Pdp2 Pdpr
Metabolism > Carbohydrate metabolism > TCA cycle MitoCarta3.0 Aco2 Cs Dld Dlst Fh1 Idh2 Idh3a Idh3b Idh3g Mdh2 Mrps36 Ogdh Ogdhl Sdha Sdhb Sdhc Sdhd Sucla2 Suclg1 Suclg2
Metabolism > Carbohydrate metabolism > TCA-associated MitoCarta3.0 Abhd11 Acly D2hgdh Fahd1 Gm4984 L2hgdh Me2 Me3 Mpc1 Mpc2 Pck2 Pcx Sfxn5 Slc25a1 Slc25a11
Metabolism > Carbohydrate metabolism > Itaconate metabolism MitoCarta3.0 Acod1 Auh Clybl Sucla2 Suclg1 Suclg2
Metabolism > Carbohydrate metabolism > Ketone metabolism MitoCarta3.0 Acaa2 Acat1 Bdh1 Hadhb Hmgcl Hmgcs2 Oxct1 Oxct2a
Metabolism > Carbohydrate metabolism > Propanoate metabolism MitoCarta3.0 Mcee Mmut Pcca Pccb
Metabolism > Lipid metabolism MitoCarta3.0 Acaa1a Acaa1b Acaa2 Acaca Acacb Acad10 Acad11 Acad12 Acadl Acadm Acads Acadsb Acadvl Acat1 Acot10 Acot11 Acot13 Acot2 Acot7 Acot9 Acp6 Acsf2 Acsf3 Acsl1 Acsl6 Acsm1 Acsm2 Acsm3 Acsm4 Acsm5 Acss1 Acss3 Agk Agpat4 Agpat5 Akr1b7 Amacr Cbr4 Chpt1 Cpt1a Cpt1b Cpt1c Cpt2 Crat Crls1 Crot Cyb5r3 Cyp11a1 Cyp11b1 Cyp11b2 Cyp27a1 Dbi Decr1 Dhrs1 Ech1 Echdc1 Echs1 Eci1 Eci2 Ehhadh Ephx2 Etfa Etfb Etfdh Fabp1 Fasn Fdps Fdx1 Fdxr Gcsh Gpam Gpat2 H2-Ke6 Hadh Hadha Hadhb Hao2 Hint2 Hsd17b10 Hsd17b4 Htd2 Idi1 Lactb Lias Lipt1 Lipt2 Lypla1 Lyplal1 Mcat Mcee Mecr Mgst3 Mlycd Mmut Ndufab1 Osbpl1a Oxsm Pcca Pccb Pgs1 Phyh Pisd Pld6 Plscr3 Pnpla8 Prdx6 Prelid1 Prelid3a Prelid3b Ptges2 Ptpmt1 Scp2 Serac1 Slc25a1 Slc25a20 Sphk2 Sptlc2 Star Stard7 Tamm41 Taz Them4 Them5 Triap1 Tspo Zadh2
Metabolism > Lipid metabolism > Fatty acid oxidation MitoCarta3.0 Acaa1a Acaa2 Acacb Acad10 Acad11 Acad12 Acadl Acadm Acads Acadsb Acadvl Acat1 Acot11 Acsf2 Acsl1 Acsl6 Acsm1 Acsm2 Acsm3 Acsm4 Acsm5 Acss1 Amacr Cpt1a Cpt1b Cpt1c Cpt2 Crat Crot Decr1 Echs1 Eci1 Eci2 Etfa Etfb Etfdh Hadh Hadha Hadhb Hsd17b10 Mcee Mmut Pcca Pccb Slc25a20
Metabolism > Lipid metabolism > Type II fatty acid synthesis MitoCarta3.0 Acaca Acsf3 Cbr4 H2-Ke6 Htd2 Mcat Mecr Ndufab1 Oxsm
Metabolism > Lipid metabolism > Lipoate insertion MitoCarta3.0 Gcsh Lias Lipt1 Lipt2
Metabolism > Lipid metabolism > Cardiolipin synthesis MitoCarta3.0 Agpat4 Agpat5 Crls1 Gpam Gpat2 Hadha Pgs1 Pld6 Plscr3 Pnpla8 Prelid1 Prelid3a Ptpmt1 Tamm41 Taz Triap1
Metabolism > Lipid metabolism > Cholesterol, bile acid, steroid synthesis MitoCarta3.0 Cyp11a1 Cyp11b1 Cyp11b2 Cyp27a1 Dhrs1 Fdx1 Fdxr H2-Ke6 Hint2 Hsd17b10 Osbpl1a Scp2 Star Tspo
Metabolism > Lipid metabolism > Cholesterol-associated MitoCarta3.0 Fdps Idi1
Metabolism > Lipid metabolism > Phospholipid metabolism MitoCarta3.0 Acp6 Agk Agpat4 Agpat5 Akr1b7 Chpt1 Gpam Gpat2 Lactb Osbpl1a Pgs1 Pisd Pnpla8 Prdx6 Prelid1 Prelid3a Prelid3b Ptpmt1 Serac1 Sphk2 Sptlc2 Stard7 Tamm41 Triap1
Metabolism > Lipid metabolism > Eicosanoid metabolism MitoCarta3.0 Mgst3 Ptges2 Zadh2
Metabolism > Amino acid metabolism MitoCarta3.0 Aadat Aass Abat Acaa2 Acad8 Acadsb Acat1 Adhfe1 Agmat Agxt Agxt2 Akr7a5 Aldh18a1 Aldh4a1 Aldh5a1 Aldh6a1 Aldh7a1 Aldh9a1 Amt Arg2 Auh Bcat2 Bckdha Bckdhb Bckdk Car5a Car5b Chdh Comt Cps1 Dbt Dglucy Dhtkd1 Dld Dlst Dmgdh Echs1 Etfa Etfb Etfdh Gcat Gcdh Gcsh Gldc Gls Gls2 Glud1 Glyat Got2 Gpt2 Grhpr Hadh Hadha Hadhb Hibadh Hibch Hmgcl Hoga1 Hsd17b10 Ivd Kmo Kyat3 Ldhb Maoa Maob Mccc1 Mccc2 Nags Nat8l Oat Otc Ppm1k Prodh Prodh2 Pycr1 Pycr2 Sardh Sdsl Sfxn1 Sfxn3 Shmt2 Slc25a12 Slc25a13 Slc25a15 Slc25a2 Slc25a21 Slc25a29 Slc25a38 Slc25a44 Sugct
Metabolism > Amino acid metabolism > Branched-chain amino acid metabolism MitoCarta3.0 Acad8 Acadsb Acat1 Aldh6a1 Auh Bcat2 Bckdha Bckdhb Bckdk Dbt Dld Echs1 Etfa Etfb Etfdh Hadha Hibadh Hibch Hmgcl Hsd17b10 Ivd Mccc1 Mccc2 Ppm1k Slc25a44
Metabolism > Amino acid metabolism > Branched-chain amino acid dehydrogenase complex MitoCarta3.0 Bckdha Bckdhb Bckdk Dbt Dld Ppm1k
Metabolism > Amino acid metabolism > Lysine metabolism MitoCarta3.0 Aadat Aass Acaa2 Acat1 Aldh7a1 Dhtkd1 Dld Dlst Echs1 Etfa Etfb Etfdh Gcdh Hadh Hadhb Slc25a29
Metabolism > Amino acid metabolism > Serine metabolism MitoCarta3.0 Agxt Sdsl Sfxn1 Sfxn3 Shmt2
Metabolism > Amino acid metabolism > Glycine metabolism MitoCarta3.0 Aldh7a1 Amt Chdh Dld Dmgdh Etfa Etfb Etfdh Gcat Gcsh Gldc Glyat Sardh Shmt2 Slc25a38
Metabolism > Amino acid metabolism > Glycine cleavage system MitoCarta3.0 Amt Dld Gcsh Gldc
Metabolism > Amino acid metabolism > Glutamate metabolism MitoCarta3.0 Gls Gls2 Glud1 Got2 Gpt2 Nat8l Slc25a12
Metabolism > Amino acid metabolism > Proline metabolism MitoCarta3.0 Aldh18a1 Aldh4a1 Oat Prodh Pycr1 Pycr2
Metabolism > Amino acid metabolism > Glyoxylate metabolism MitoCarta3.0 Agxt Agxt2 Aldh4a1 Got2 Grhpr Hoga1 Ldhb Prodh2
Metabolism > Amino acid metabolism > GABA metabolism MitoCarta3.0 Abat Adhfe1 Akr7a5 Aldh5a1 Aldh9a1 Glud1
Metabolism > Amino acid metabolism > Catechol metabolism MitoCarta3.0 Comt Maoa Maob
Metabolism > Amino acid metabolism > Kynurenine metabolism MitoCarta3.0 Got2 Kmo Kyat3
Metabolism > Amino acid metabolism > Urea cycle MitoCarta3.0 Car5a Car5b Cps1 Nags Otc Slc25a13 Slc25a15 Slc25a2
Metabolism > Nucleotide metabolism MitoCarta3.0 Ak2 Ak3 Ak4 Antkmt Ckmt1 Ckmt2 Cmpk2 Dguok Dhodh Dut Fhit Gatm Guk1 Hint1 Nme3 Nme4 Nme6 Nt5dc2 Nt5m Nudt2 Nudt5 Nudt9 Paics Ppa2 Slc25a23 Slc25a24 Slc25a25 Slc25a31 Slc25a33 Slc25a36 Slc25a4 Slc25a41 Slc25a5 Sucla2 Suclg1 Tk2
Metabolism > Nucleotide metabolism > Nucleotide import MitoCarta3.0 Slc25a23 Slc25a24 Slc25a25 Slc25a31 Slc25a33 Slc25a36 Slc25a4 Slc25a41 Slc25a5
Metabolism > Nucleotide metabolism > Nucleotide synthesis and processing MitoCarta3.0 Ak2 Ak3 Ak4 Cmpk2 Dguok Dhodh Dut Fhit Guk1 Hint1 Nme3 Nme4 Nme6 Nt5dc2 Nt5m Nudt2 Nudt5 Nudt9 Paics Sucla2 Suclg1 Tk2
Metabolism > Nucleotide metabolism > Creatine metabolism MitoCarta3.0 Ckmt1 Ckmt2 Gatm
Metabolism > Metals and cofactors MitoCarta3.0 Abat Abcb10 Abcb6 Abcb7 Aco2 Aifm3 Alas1 Alas2 Bola1 Bola3 Chchd7 Cisd1 Cisd3 Coasy Coq10a Coq10b Coq2 Coq3 Coq4 Coq5 Coq6 Coq7 Coq8a Coq8b Coq9 Cox10 Cox11 Cox15 Cox17 Cox19 Cpox Cpt1a Cpt1b Cpt1c Cpt2 Cyb5b Cyc1 Cycs Cyp11a1 Cyp11b2 Cyp24a1 Cyp27a1 Cyp27b1 Dna2 Etfdh Fabp1 Fam210b Fdx1 Fdx2 Fdxr Fech Fth1 Ftmt Fxn Glrx2 Glrx5 Grpel1 Grpel2 Hccs Hscb Hspa9 Iba57 Isca1 Isca2 Iscu Kmo Kyat3 Lias Lyrm4 Mocs1 Mtarc1 Mtarc2 Nadk2 Naxd Naxe Ndufab1 Ndufs1 Ndufs2 Ndufs7 Ndufs8 Ndufv1 Ndufv2 Nfs1 Nfu1 Nmnat3 Nnt Noct Nthl1 Nubpl Nudt13 Nudt19 Nudt8 Pank2 Pcbd2 Pdss1 Pdss2 Ppox Qdpr Rsad1 Sco1 Sco2 Sdhb Sdhc Sdhd Sirt3 Sirt4 Sirt5 Slc25a20 Slc25a28 Slc25a3 Slc25a37 Slc25a38 Slc25a42 Slc25a51 Spr Suox Tmlhe Uqcrfs1 mt-Co1 mt-Cytb
Metabolism > Metals and cofactors > Carnitine synthesis and transport MitoCarta3.0 Cpt1a Cpt1b Cpt1c Cpt2 Slc25a20 Tmlhe
Metabolism > Metals and cofactors > Carnitine shuttle MitoCarta3.0 Cpt1a Cpt1b Cpt1c Cpt2 Slc25a20
Metabolism > Metals and cofactors > Coenzyme A metabolism MitoCarta3.0 Coasy Nudt19 Nudt8 Pank2 Slc25a42
Metabolism > Metals and cofactors > Coenzyme Q metabolism MitoCarta3.0 Coq10a Coq10b Coq2 Coq3 Coq4 Coq5 Coq6 Coq7 Coq8a Coq8b Coq9 Pdss1 Pdss2
Metabolism > Metals and cofactors > Copper metabolism MitoCarta3.0 Chchd7 Cox11 Cox17 Cox19 Sco1 Sco2 Slc25a3
Metabolism > Metals and cofactors > Iron homeostasis MitoCarta3.0 Fam210b Fth1 Ftmt Slc25a28 Slc25a37
Metabolism > Metals and cofactors > Heme synthesis and processing MitoCarta3.0 Abcb10 Abcb6 Abcb7 Alas1 Alas2 Cox10 Cox15 Cpox Fabp1 Fdx1 Fdx2 Fdxr Fech Hccs Ppox Slc25a38
Metabolism > Metals and cofactors > Fe-S cluster biosynthesis MitoCarta3.0 Abcb7 Bola1 Bola3 Cisd1 Cisd3 Fdx1 Fdx2 Fdxr Fxn Glrx5 Grpel1 Grpel2 Hscb Hspa9 Iba57 Isca1 Isca2 Iscu Lyrm4 Ndufab1 Nfs1 Nfu1 Nubpl
Metabolism > Metals and cofactors > Molybdenum cofactor synthesis and proteins MitoCarta3.0 Abcb7 Mocs1 Mtarc1 Mtarc2 Suox
Metabolism > Metals and cofactors > NAD biosynthesis and metabolism MitoCarta3.0 Kmo Kyat3 Nadk2 Naxd Naxe Nmnat3 Nnt Noct Nudt13 Sirt3 Sirt4 Sirt5 Slc25a51
Metabolism > Metals and cofactors > Tetrahydrobiopterin synthesis MitoCarta3.0 Pcbd2 Qdpr Spr
Metabolism > Metals and cofactors > Fe-S-containing proteins MitoCarta3.0 Abat Aco2 Aifm3 Bola1 Bola3 Cisd1 Cisd3 Dna2 Etfdh Fdx1 Fdx2 Fech Glrx2 Glrx5 Isca1 Isca2 Iscu Lias Ndufs1 Ndufs2 Ndufs7 Ndufs8 Ndufv1 Ndufv2 Nfs1 Nfu1 Nthl1 Nubpl Rsad1 Sdhb Uqcrfs1
Metabolism > Metals and cofactors > Heme-containing proteins MitoCarta3.0 Cyb5b Cyc1 Cycs Cyp11a1 Cyp11b2 Cyp24a1 Cyp27a1 Cyp27b1 Sdhc Sdhd mt-Co1 mt-Cytb
Metabolism > Vitamin metabolism MitoCarta3.0 Acaca Acacb Akr1b10 Aldh1l1 Aldh1l2 Aldh7a1 Amt Bco2 Chdh Cyp24a1 Cyp27b1 Dhrs4 Dmgdh Etfa Etfb Etfdh Fdx1 Fdxr Flad1 Fpgs Glrx2 Gtpbp3 Mccc1 Mmaa Mmab Mmadhc Mmut Mtfmt Mthfd1l Mthfd2 Mthfd2l Mthfs Mthfsl Mto1 Pcca Pcx Plpbp Pnpo Qdpr Rdh13 Rdh14 Rfk Sardh Sfxn1 Sfxn3 Shmt2 Slc25a19 Slc25a32 Slc25a38 Txn2
Metabolism > Vitamin metabolism > Choline and betaine metabolism MitoCarta3.0 Aldh7a1 Chdh Dmgdh Etfa Etfb Etfdh Sardh
Metabolism > Vitamin metabolism > Biotin utilizing proteins MitoCarta3.0 Acaca Acacb Mccc1 Pcca Pcx
Metabolism > Vitamin metabolism > Vitamin A metabolism MitoCarta3.0 Akr1b10 Bco2 Dhrs4 Rdh13 Rdh14
Metabolism > Vitamin metabolism > Vitamin B1 metabolism MitoCarta3.0 Slc25a19
Metabolism > Vitamin metabolism > Vitamin B2 metabolism MitoCarta3.0 Flad1 Rfk Slc25a32
Metabolism > Vitamin metabolism > Vitamin B6 metabolism MitoCarta3.0 Plpbp Pnpo
Metabolism > Vitamin metabolism > Vitamin B12 metabolism MitoCarta3.0 Mmaa Mmab Mmadhc Mmut
Metabolism > Vitamin metabolism > Vitamin C metabolism MitoCarta3.0 Glrx2 Txn2
Metabolism > Vitamin metabolism > Vitamin D metabolism MitoCarta3.0 Cyp24a1 Cyp27b1 Fdx1 Fdxr
Metabolism > Vitamin metabolism > Folate and 1-C metabolism MitoCarta3.0 Aldh1l1 Aldh1l2 Aldh7a1 Amt Chdh Dmgdh Fpgs Gtpbp3 Mtfmt Mthfd1l Mthfd2 Mthfd2l Mthfs Mthfsl Mto1 Qdpr Sardh Sfxn1 Sfxn3 Shmt2 Slc25a32 Slc25a38
Metabolism > Detoxification MitoCarta3.0 Abhd10 Acsm2 Acsm5 Aifm2 Akr1b10 Akr7a5 Aldh1b1 Aldh2 Aldh3a2 Aldh7a1 Aldh9a1 Bphl Cat Cbr3 Cyb5b Cyb5r3 Dhrs2 Ephx2 Glrx2 Glyat Gpx1 Gpx4 Gsr Gstk1 Gstz1 Hagh Maoa Maob Mgst1 Mpst Msra Msrb2 Msrb3 Mtarc1 Mtarc2 Nit1 Nit2 Oxr1 Prdx2 Prdx3 Prdx4 Prdx5 Prdx6 Prxl2a Selenoo Sod1 Sod2 Tst Txn2 Txnrd1 Txnrd2
Metabolism > Detoxification > Xenobiotic metabolism MitoCarta3.0 Abhd10 Acsm2 Acsm5 Akr1b10 Akr7a5 Aldh1b1 Aldh2 Bphl Cbr3 Cyb5b Cyb5r3 Dhrs2 Ephx2 Glyat Gstk1 Gstz1 Maoa Maob Mgst1 Mpst Mtarc1 Mtarc2 Tst
Metabolism > Detoxification > ROS and glutathione metabolism MitoCarta3.0 Aifm2 Aldh3a2 Aldh7a1 Aldh9a1 Cat Glrx2 Gpx1 Gpx4 Gsr Hagh Mgst1 Msra Msrb2 Msrb3 Nit1 Oxr1 Prdx2 Prdx3 Prdx4 Prdx5 Prdx6 Prxl2a Sod1 Sod2 Txn2 Txnrd1 Txnrd2
Metabolism > Detoxification > Amidoxime reducing complex MitoCarta3.0 Cyb5b Cyb5r3 Mtarc1 Mtarc2
Metabolism > Detoxification > Selenoproteins MitoCarta3.0 Gpx1 Gpx4 Selenoo Txnrd1 Txnrd2
Metabolism > Electron carriers MitoCarta3.0 Chdh Cyb5b Cyc1 Cycs Cyct Dhodh Etfa Etfb Etfbkmt Etfdh Etfrf1 Gpd2 Prodh Prodh2 Sqor mt-Cytb
Metabolism > Electron carriers > Cytochromes MitoCarta3.0 Cyb5b Cyc1 Cycs Cyct mt-Cytb
Metabolism > Electron carriers > Q-linked reactions, other MitoCarta3.0 Chdh Dhodh Etfa Etfb Etfbkmt Etfdh Etfrf1 Gpd2 Prodh Prodh2 Sqor
Metabolism > Sulfur metabolism MitoCarta3.0 Ethe1 Got2 Mpst Msra Msrb2 Slc25a14 Slc25a30 Sqor Suox Tst Tstd1
Small molecule transport MitoCarta3.0 Abca9 Abcb10 Abcb6 Abcb7 Abcb8 Abcd1 Abcd2 Abcd3 Ccdc51 Gm4984 Letmd1 Mcu Mcub Micu1 Micu2 Micu3 Mpc1 Mpc2 Mpv17 Mpv17l Mrs2 Mtch1 Mtch2 Romo1 Sfxn1 Sfxn2 Sfxn3 Sfxn4 Sfxn5 Slc25a1 Slc25a10 Slc25a11 Slc25a12 Slc25a13 Slc25a14 Slc25a15 Slc25a16 Slc25a18 Slc25a19 Slc25a2 Slc25a20 Slc25a21 Slc25a22 Slc25a23 Slc25a24 Slc25a25 Slc25a26 Slc25a27 Slc25a28 Slc25a29 Slc25a3 Slc25a30 Slc25a31 Slc25a32 Slc25a33 Slc25a34 Slc25a35 Slc25a36 Slc25a37 Slc25a38 Slc25a39 Slc25a4 Slc25a40 Slc25a41 Slc25a42 Slc25a43 Slc25a44 Slc25a45 Slc25a46 Slc25a47 Slc25a48 Slc25a5 Slc25a51 Slc25a53 Slc25a54 Slc30a9 Slc8b1 Smdt1 Stard7 Ucp1 Ucp2 Ucp3 Vdac1 Vdac2 Vdac3
Small molecule transport > SLC25A family MitoCarta3.0 Mtch1 Mtch2 Slc25a1 Slc25a10 Slc25a11 Slc25a12 Slc25a13 Slc25a14 Slc25a15 Slc25a16 Slc25a18 Slc25a19 Slc25a2 Slc25a20 Slc25a21 Slc25a22 Slc25a23 Slc25a24 Slc25a25 Slc25a26 Slc25a27 Slc25a28 Slc25a29 Slc25a3 Slc25a30 Slc25a31 Slc25a32 Slc25a33 Slc25a34 Slc25a35 Slc25a36 Slc25a37 Slc25a38 Slc25a39 Slc25a4 Slc25a40 Slc25a41 Slc25a42 Slc25a43 Slc25a44 Slc25a45 Slc25a46 Slc25a47 Slc25a48 Slc25a5 Slc25a51 Slc25a53 Slc25a54 Ucp1 Ucp2 Ucp3
Small molecule transport > ABC transporters MitoCarta3.0 Abca9 Abcb10 Abcb6 Abcb7 Abcb8 Abcd1 Abcd2 Abcd3
Small molecule transport > Sideroflexins MitoCarta3.0 Sfxn1 Sfxn2 Sfxn3 Sfxn4 Sfxn5
Signaling MitoCarta3.0 Acod1 Adcy10 Akap1 Akap10 Bloc1s1 C1qbp Cstad Dele1 Efhd1 Fundc2 Ifi27 Letm1 Lypla1 Macrod1 Mavs Mcrip2 Mcu Mcub Micu1 Micu2 Micu3 Mrs2 Mul1 Nlrx1 Ociad2 Pde2a Pink1 Ppif Pptc7 Prkaca Rhot1 Rhot2 Sirt3 Slc25a12 Slc25a13 Slc25a23 Slc25a24 Slc25a25 Slc25a3 Slc25a31 Slc25a4 Slc25a5 Slc8b1 Smdt1 Sphkap Vdac1 Vdac3
Signaling > Calcium homeostasis MitoCarta3.0 Efhd1 Letm1 Mcu Mcub Micu1 Micu2 Micu3 Ppif Rhot1 Rhot2 Slc25a12 Slc25a13 Slc25a23 Slc25a24 Slc25a25 Slc25a3 Slc25a31 Slc25a4 Slc25a5 Slc8b1 Smdt1 Vdac1 Vdac3
Small molecule transport > Calcium uniporter MitoCarta3.0 Mcu Mcub Micu1 Micu2 Micu3 Smdt1
Signaling > Calcium homeostasis > Calcium cycle MitoCarta3.0 Letm1 Mcu Mcub Micu1 Micu2 Micu3 Slc25a3 Slc8b1 Smdt1
Signaling > Calcium homeostasis > Mitochondrial permeability transition pore MitoCarta3.0 Ppif Slc25a31 Slc25a4 Slc25a5 Vdac1 Vdac3
Signaling > Calcium homeostasis > EF hand proteins MitoCarta3.0 Efhd1 Micu1 Micu2 Micu3 Rhot1 Rhot2 Slc25a12 Slc25a13 Slc25a23 Slc25a24 Slc25a25
Signaling > Immune response MitoCarta3.0 Acod1 C1qbp Cstad Ifi27 Mavs Nlrx1
Signaling > cAMP-PKA signaling MitoCarta3.0 Adcy10 Akap1 Akap10 Pde2a Prkaca Sphkap
Mitochondrial dynamics and surveillance MitoCarta3.0 Ahcyl1 Aifm1 Aifm2 Aifm3 Apoo Apool Arl2 Armc10 Armcx1 Armcx3 Atad3a Atp5k Atp5l Atp5md Bad Bak1 Bax Bbc3 Bcl2 Bcl2a1d Bcl2l1 Bcl2l10 Bcl2l11 Bcl2l13 Bcl2l2 Bid Bik Bnip3 Bnip3l Bok Casp3 Casp8 Casp9 Chchd2 Chchd3 Chchd6 Cycs Diablo Dnajc11 Dnm1l Endog Fis1 Fkbp8 Fundc1 Fundc2 Ghitm Htra2 Ifi27 Immt Marchf5 Mcl1 Mff Mfn1 Mfn2 Mgarp Micos10 Micos13 Mief1 Mief2 Miga1 Miga2 Mtch2 Mtfp1 Mtfr1 Mtfr2 Mtx1 Mtx2 Mtx3 Mul1 Myo19 Nbr1 Nipsnap1 Nipsnap2 Oma1 Opa1 Park7 Parl Pgam5 Pigbos1 Pink1 Pld6 Pmaip1 Prkn Rab24 Rhot1 Rhot2 Rmdn3 Samm50 Septin4 Slc25a46 Snap29 Sphk2 Spire1 Stx17 Styxl1 Synj2bp Tmem11 Tomm20 Tomm7 Usp30 Vdac1 Vps13d
Mitochondrial dynamics and surveillance > Fusion MitoCarta3.0 Arl2 Mfn1 Mfn2 Miga1 Miga2 Mtch2 Oma1 Opa1 Pld6
Mitochondrial dynamics and surveillance > Fission MitoCarta3.0 Armc10 Dnm1l Fis1 Mff Mief1 Mief2 Mtfp1 Mtfr1 Mtfr2 Mul1 Oma1 Rab24 Slc25a46 Spire1 Stx17
Mitochondrial dynamics and surveillance > Organelle contact sites MitoCarta3.0 Ahcyl1 Atad3a Fkbp8 Fundc2 Mfn1 Mfn2 Miga2 Pigbos1 Rmdn3 Spire1 Stx17 Synj2bp Vdac1
Mitochondrial dynamics and surveillance > Intramitochondrial membrane interactions MitoCarta3.0 Atad3a Chchd3 Dnajc11 Mtx1 Mtx2 Mtx3 Samm50 Slc25a46
Mitochondrial dynamics and surveillance > Trafficking MitoCarta3.0 Armc10 Armcx1 Armcx3 Mgarp Myo19 Rhot1 Rhot2
Mitochondrial dynamics and surveillance > Mitophagy MitoCarta3.0 Bcl2l13 Fkbp8 Fundc1 Marchf5 Nipsnap1 Nipsnap2 Park7 Parl Pgam5 Pink1 Prkn Tomm7 Usp30 Vps13d
Mitochondrial dynamics and surveillance > Autophagy MitoCarta3.0 Bcl2l13 Fkbp8 Fundc1 Marchf5 Nbr1 Nipsnap1 Nipsnap2 Park7 Parl Pgam5 Pink1 Prkn Rab24 Snap29 Stx17 Tomm7 Usp30 Vps13d
Mitochondrial dynamics and surveillance > Apoptosis MitoCarta3.0 Aifm1 Aifm2 Aifm3 Bad Bak1 Bax Bbc3 Bcl2 Bcl2a1d Bcl2l1 Bcl2l10 Bcl2l11 Bcl2l13 Bcl2l2 Bid Bik Bnip3 Bnip3l Bok Casp3 Casp8 Casp9 Chchd2 Cycs Diablo Endog Ghitm Htra2 Ifi27 Mcl1 Pmaip1 Septin4 Sphk2 Styxl1
Mitochondrial dynamics and surveillance > Cristae formation MitoCarta3.0 Apoo Apool Atp5k Atp5l Atp5md Chchd3 Chchd6 Immt Micos10 Micos13 Opa1
Mitochondrial dynamics and surveillance > Cristae formation > MICOS complex MitoCarta3.0 Apoo Apool Chchd3 Chchd6 Immt Micos10 Micos13